Ola kinoLapaau

ʻike makaʻole mau maka Blashko laina ma ke kanaka kino

Imperceptible i ka mea kapa ole maka i kumu hoohalike ma ke kanaka kino ana ma lalo o ka aoao o endogenous a me ka exogenous io aʻe. Hooponoponoia ia mea, ma ka pathology like laina Blashko. Melanogenesis hoike aku hypopigmentation, pili i ka pae o ka maʻi dermatoses. Hiki benign panee i ka 'epekema. Maopopo i ka loina o ke ano o kaʻeho, e mea hiki ke pale aku i ke ano o ka melanoma.

I ka moolelo o ka hoʻopaʻa 'ana o kaʻili mai

German kanaka noiʻi dermatological pilikia i loaʻa Blashko laina i ka 1901. kū no ka mea, i kekahi kumu o ka pigmentation, like i loko o nā hale a me nā mea a pau nā mea maʻi. I ka maʻi i kapaʻia ma hope o ka inoa o ke nä känaka 'epekema, nona ka inoa o Alfred.

Dermatologist hoʻokumu pilina me ka hanana o ka pathology X-chromosomes. Ma olakino ili imperceptible loli i loko o kā lākou maʻamau lehulehu. E like me ka hopena o ka chaotic Polenekia malanoblastov i ke kahua o ka hiki māhele kumu. Kūlana o ka mutated aeee mea e kaukaʻi ma ke kino o ko mākou hopohopo breakdowns. Eia naʻe, dermatological pilikia hiki ke loaʻa i loko o congenital'āina hoʻoili o ka maʻi.

Ke kumu nui no deviations o na kanaka ili

E kuhikuhi i na kēia mau kumumea Education Blashko laina ma ke kino:

  • Chimerism - pinepine haawiia i like ke kulana o kekahi kanaka kiaʻi mauʻano o ka DNA. Aʻokoʻa kauʻia o nā'ōewe triggers ke kahua o ka pigmentation ma luna o ke kino. Mau waiwai hōʻike incest me nāʻano o kēia lāhui kanaka. Kumu o ka ili pathology i ke kuʻi nukeliu o ka fertilized hua ma ka kakahiaka kahua o ka hāpai keiki.
  • Kanaka stress imbalance - he chaotic kumu ua hana.
  • Aaiaoe? - hoʻololi i loko o kanaka DNA. Ke kumu no ka helehelena o congenital pathology i nevi: depigmented, pigmented, sebaceous, laina verrucous hoʻoʻino.
  • Aaiaoe paʻipaʻiʻia ai e DNA i embryogenesis -ʻepekema lele akula 'ole o ke kanaka nā'aʻaʻa: i hoʻokahi nā hīnaʻi manu' ia paha o nā'ōewe ua malamaia. Oiai ke kumu o ka hope o ua loko mai o ka hookahi zygote.

Ke ano o ka helehelena o ka dermatosis

He mea ole ia i ike i ka manawa "Blashko laina" - He aha ka mea laina? Na pilikia pinepine i loaʻa i loko o keiki keiki, i hou aku 2% o ka a i predisposed ai i keʻano o nā pathologies. Ka 'ole o ka DNA mea initially kekahi mau' ike maʻi. Mawaho symptoms ai ka haohao ana i ka hopena o deviations Endocrinology kino.

Blashko laina wehewehe aku ma ka ekolu aeee i loko o ke kino, o ke kumu o ka maʻi.

  • Epidermal keratinocytes - lilo pathology pinepine malama i ka hopena o ka chimerism.
  • Pigment - aia i loko o ka haahaa papa o na epidermis.
  • Profiling palena pigment keena - hiki aku ai i ka loli ma ka ili kala like 'ole, maalo ae la oia ma ka hale ilaloʻili lahilahi i loko o ka luna, ahu iho o na dermis. Kēia moku'āina ua malamaia ma innate ano o ke kahua o ke melanoma.

mawaho hoailona

Ka 'inikua moʻokalaleo eaaaony' ike e pili ana i na laina Blashko: i ia mea he maʻi o ke kanaka nā'aʻaʻa, i hoike mai ai ia ia iho ma ka hihia o ka hoʻolako 'ole i loko o ke kino no ke ola. 'Oleʻike makaʻole kumu ma ka aoao hope kohu i ke ano o ka holoholona: zebra paha tiga. Ua hiki ke hoʻomaopopo ma ultraviolet pāhawewe.

Ke ano o ke kanaka ili hilinaʻi nui ma luna o ka waiwai o ka pigment melanin. Ua ua hana ia ma na epidermis nā'aʻaʻa, basal, ahu iho maupaʻa melanocytes. Deviations ma ke kaʻina hana o ka melanogenesis hiki aku ai i ke ano loli visually perceptible:

  • Hyperpigmentation - chaotic kumu pouli mau kiko ma luna o ka ili o, ua maopopo ike okoa mai ke kumu o malumalu poi.
  • Hypopigmentation - lilo o ke ano o ka ili keena, kūpono whitish mau kiko. Pohihihi keia pathology malama i oi aku 1% o ke keiki na kamalii uuku.

An mawaho hoike ana o ka maʻi kumu i V-hoʻokino, i loko o ka palapala o ka curls a wavy laina. Pinepine i hanaʻia ma luna o kēia mau māhele o ke kino.

  • hope;
  • ma na aoao;
  • poʻohiwi;
  • poo.

diagnosing i ka pilikia

Line unuhi aku la ia Blashko kekahi 'wā he kanaka irradiated me ultraviolet malamalama, akā, no ka mea ola o ke kākaʻikahi hele ia ninaninau. E hoʻopaʻa haʻawina o ka moku'āina o ke kino hoʻomaka mua i loko o e holumua ai kahua o ka hoʻonaʻauao o ka maʻi. I keiki na kamalii uuku, ka lilelile o hypopigmentation ma luna o ke kino pilikia e ike. Ke keiki ka loaʻa o ka loli nui o ka ili i loko o kekahi mau makahiki.

Ma ka moku'āina o na keena loli ana ma kekahi lākou o chromosomes. Inā ka mea, he nui okoa ma e pili pauku o ka ili, ka deviations malama i loko o 'ia nā pōpō fabrics. No laila, hypopigmentation eʻikea ia ma ke ka ana ma lalo nei:

  • Chaotic pūkoʻa - hoihoi ma ka 'epekema no ka mea, o ka mea haoʻa hale. Ke kiʻiʻelua i ka nānāʻana aku i luna 'kinona i loko o ka palapala o ka poe hao wale, Mū Kākela keena.
  • IIeEeAIEUIeXAIIUE - ike pono kekahi ke kina ole ma ka kekahi wahi.
  • Generalized - i ke ukali ia e na maʻi o na nā loko.

No ke aha la makou e noiʻi i nā nō ma luna o kaʻili e pono ai?

Ua hele aku io lapaau e hionapāʻili Ka Ikepili o nā'aʻaʻa ma complications hiki ma ka ili. Eia, i ka papa kuhikuhiE anakahi o ka laina Blashko, ka maʻi ua hoʻokolokolo no ka mea pololeiʻike. Kēia i nui ka wā i kēia dermatological pilikia:

  • chimerism;
  • mosaicism;
  • zoster;
  • nevus;
  • melanoma.

Complex textures i nui wale i kaʻaoʻao noiʻi, no ka mea i loko o, ia i Ka Ikepili i ole i alakai i kekahi mau hopena a e pili ana i ka maʻi. ʻepekema manao e hoike aku i ka manao o na kumu hoohalike i ke kanaka kino. Paha i ka loaʻa, e kōkua i ka hoʻopau i nā hualoaʻa o ka ke nānā ili maʻi.

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