Ola kino, Maʻi a me nā kūlana
Amniotic constriction: mea, lalau mai, symptoms,ʻike, a me ka lapaʻau regimen
I kekahi manawa, clinically ola makuwahine hanau i keiki me ka morphological mā: nele o phalanges, lala, a hiki lākou mau poʻo. Ka makuahine ua ma ka manao, i hoopii ai ia ia iho a me na kumu ao mea i hanaia mai ai i kā lākou mau keiki. I kekahi manawa e hele mai i ka hookolokolo ana. Akā, aha maoli o ke kumu o ka mā hanau?
ka wehewehena
Amniotic constriction, ole kapaia "amniotic ulana" a me "kaula makalii Simonara" ho i dublication amnion lole i ua'ōʻia ma waena o ka uterine pa. E like me ka rula, ka mea, aole e hana ino i ka embryo a me ka malama ole oweliweli complications i loko o ka nahunahu hanau. Akā, ma ka pohihihi keia hihia, hiki ka hopena ma ka hoʻoponopono ulia pōpilikia 'hopena.
Amniotic constriction - puluniu filaments, i ala mai ma ka fetal bladder. Ka mea, e oOeEIAOO a wili ka piko pili ana i nā māhele o ke kino o ka fetus, ma o na la hanau mā (amputation o na lima, na wawae, me na manamana wawae, a me phalanges, i kekahi manawa decapitation).
kumu
Aia i mau theories ke kumu malaila amniotic constriction. Nā kumu no kēia kŰia wehewehe i ka pinepine ruptures amniotic Oe i loko o kakahiaka hāpai keiki. E like me ka chorion koe kōna, i ka make māinoino o ka haʻahaʻa o ka embryo? Acaeoey ua i ike, aka, i ka pae e ala mai no ia, mai hemo mai, noa-lana ana ma ka amniotic loli. Ka mea, hiki ke hui i ke kino o ka hua. Ma ka papa o ka hāpai keiki i ka pēpē ulu, akā, i ka pae koe ka ia me ka mea a pau, no laila, he mea mīkini'opihia o ka'aʻaʻa ischemia a me ka necrosis.
Kekahi manawa ma hope, i ka lua o kumumanaʻo, e like me ka mea mua iʻole nō paha skeptics ka poe i malama i amniotic constriction (kaula i loko o ka'ōpū o ka wahine hāpai) hōʻike ka poʻe me nā congenital malformations e like me mauae lehelehe a mauae kīleo. Mau kauka i ua? Aaei i loaʻa nāʻaukā e paʻa ai ma muli o ke vascular kāna hana a me kāna hana o fetal holo.
Kekahi mana o ka hanana mea intrauterine maʻiʻaʻai, a me ka trauma i hāpai keiki,'āno'ē genitalia (a pāpālua hoʻi o ka uterus, elua-pepeiaohao uterus , a no laila, ma luna o. D.), CIN (cervical incompetence), li nui o ka amnion, endometritis, oligohydramnios. Akā, i kekahi o kēia mau theories i ua hookupaa iho la ia conclusively.
lapaʻau '
Ma ka hapanui o hihia, lapaʻau, a keʻena hoʻokolohua 'aʻole e hōʻike amniotic constriction. Photos mai ka ultrasound ao uninformative, mai kēia mau pae paha i loa lahilahi. Kahiko o ka'āina e hiki ke kuhikuhi i hoonee aku a me ka pehu lala i mau mea o ka mīkini'opihia. Pili kēia he ākea overdiagnosis o keia pathology. Nolaila, ina he kumu ao ka mahuʻi wale i ke alo o amniotic ka poe hao wale, hapai kuhikuhi ia MRI a me 3D ultrasound.
More ma mua o ka hapalua o ka diagnosed amniotic constrictions ma hai ultrasound hiki ole ke 'akomi i no i kā lākou rupture.
'ikepili helu
Ke kaumaha ma muli o ka oaoieei-ipu prenatal alapine (frequency) i a ka 'akomi i amniotic constrictions e ĸokoĸa ana nä pane mai 1: 1200 a hiki i 1:15 000 genera. Ua Ua manaoio aku i elua haneri a me ka umi tausani abortions ana no keia mea. Kanawalu pakeneka o na kaula makalii Simonara ino na manamana a me ka lima, a me kekahi he umi pakeneka - he mīkini'opihia o ka piko. I ka ho okumu ana o knots i loko o ka piko alakai i ka hypoxia a antenatal fetal make.
Mea pōmaikaʻi, ka hapanui diagnoses "amniotic koa constriction" uaʻaʻole i kākoʻo 'ia e lapaʻau a fibrous kaula makalii eʻaʻole i nui ka poino i ka fetus.
nā kūpuna mai
Ka pahiki i ka amniotic constrictions ikeia i hāpai keiki, ka'āina uuku. Kēia mea,ʻaʻole he hereditary maʻi. Nō kāu, ka genomic a chromosomal mutations ana symmetrically, a ma keia hihia, i ka pae i pili loa huikau. Inā ka mua hāpai keiki i loko o ke keiki makalii Simonara malama, ka mea, 'aʻole i manaʻo i mahope keiki e e poino. No hoi, ka mea, 'aʻole i manaʻo i na makua, ka poe i loaa ia ia ma utero amniotic bana constriction ua hanau, he keiki me malformations.
waiwai
ʻOiai amniotic constrictions - mea ole ona e pathology, i ka waiwai o ka mea i loaa ole ia loa. Aie i ka mea i ka paa ke hoohihia fetal māhele o ke kino, ulu lymph stagnation. Ua hiki aku i ka edema a me ka necrosis. Ma hope iho o ka hanau ana o ia i kekahi lala pono e amputated, a hoʻomōhala hahi-maʻi pale: na toxins mea i loaa ma ka anesthetized lala, hāʻule i loko o ka systemic holo a me nā loko, e hoʻomaka e hoomake iho i ka bebe. Ua hiki ke alakai i kona make ana. He nolaila, e pono ke wehe i ka lala, ina ia mea, ua unsustainable. A i 'āwīwī i hiki.
Eia hou, i loko o ka maʻi pale o amniotic constrictions i kaumaha lala a me nā manamana i loko o ka proximal hapa o ka lala. Pinepine i waena o kēia mau keiki ulana manamana a me phalanges o nā manamana lima a me nā manamana wāwae. I kekahi manawa, ma ka hou ana i na constrictions o ke keiki i malama 'ē aʻe stigma disembriogeneza: mauae kīleo a me ka lehelehe luna. I loa pohihihi keia hihia loaʻa nā 'aʻe' loa o ka spine a me ka lehalehu t iwi poʻo, eventration abdominal nā loko, atresia o ka piko.
Inā constriction e loli ai i pili loa mai la, wahi a hiki i kaʻili, a laila, i kēia wahi mea ua hana hemangioma. ʻeho ma hope o ka hānau pono e wehe.
Kekahi mau kānakaʻepekema loaʻa loko kaula Simonara me clubfoot. Keia mea no ka mea, i paa fetal wāwae i ka puluniu kaula makalii, no laila, ke uterus hiki oOeEIAOO i ka wāwae o ka fetus. He iwakalua pakeneka o keia pathology mea mau-kapakahi. Kekahi kamepiula, a e i ka obstetrician - Ua premature hanau. Kēia complication - He pinepine kŰia ma pregnancies e ana i ka maʻi pale amniotic constrictions.
lapaʻau
E like me ka rula, ma ka utero mea he maʻi hiki ole ke ola. I ka 'inikua hana, eia anecdotal hihia kahi i transvaginal a laparoscopicʻoki kino. Akā, ka mea, ua ka loa ana, e like me ka ae like nō nui nā loko. Akā, ia mea paʻakikī loa pohihihi amniotic constriction. Lapaʻau ua ana lawe mai ma hope o ke keiki ua hanau.
i dissected ke olona, a me amputated hapa o kekahi mau koʻo ikaika inā pono. E hoʻoikaika i ka pono o ke ola hiki ke transplanted manamana lima i lalo o kona mau lima.
Outlook
Ke prognosis no ke ola a me ka ola, Ua nui maikaʻi. Children ma ka hapanui o na hihia e ulu, a ulu e like me kona mau makahiki. Kela a me keia makahiki i ka lala hou, no laila, i ka lilo ana o forearm, lima, haʻahaʻa wāwae a wāwae mea hiki ke hoala mai i kaʻimi hoʻopunipuni ae pani. Children i hooluoluia mai ai e hoʻololi i ka dentures i ko lakou ulu ana mua. Inā ka constriction, kena ae la nīnūnē ooieoeiiaeuiiai kina, mea hoʻonani kina hiki ke eliminated e hoolilo manamana a me kā lākou mau phalanges.
Ma poʻe me ka maʻi pale amniotic constrictions hiki e hanau pono ola na keiki, e like me keia maʻi ua i ili.
Kaulana a ka mea i loaʻa iā ia i paa ai Simonara
It Ka Ua he manawa ia kanaka me ka lala amputation i pee ana ma ko lakou mau home, a ostracized ma ke kaiāulu. Ano, ka mea hiki ke noho me kaʻaneʻane ole kapu, e hoopaa nui lehulehu nā kūlana hana, hoʻokō, hōʻike ma kīwī, a komo i loko o ka nani hoopapa.
Kekahi kaulana kanaka e hilahila no i hanau me ka congenital amputation, akā, ina paha i ka mea ku pono i ka amniotic constriction - he ninau hamama.
- Nohealani Bornell - mea hana keaka, ka mea i hānauʻia me ka forearm pono. Ua hana ma luna o nā keiki a ka kīwī Kanal. Ua kena ae la i kekahi poʻe'ē he naoh i waena opiopio Mea Nānā a me kā lākou mau mākua, a ua haawi mai impetus i ka muli o ka moʻo o nā papahana e pili ana pehea e haʻi aku i nā keiki e pili ana i kīnā o ke kino a me ka kūikawā hiʻona o ke ola o kēia kanaka.
- Dzhim Ebbot mea kama'āina i nā mea a pau kânaka o ka pôhili. He He He kaʻao bakeke, oa eʻai, me ka palaki akau. He hoi aku, mai ka sport ma ka pau ana o ka iwakalua kenekulia, akā, i kona laʻana mau e hoopiha i na kanaka me ke kino kīnā, a Paralympians.
- Teresa yukata - he nani Miss Amerika, i hānauʻia me ka lima hema. Ma Competition, au i i komo i ka prosthesis, e hōʻike anaʻoe hiki e nani, a me kaʻimi hoʻopunipuni māhele.
- Kelli Noks - luna kumu hoʻohālike me ka forearm hema. I ka 2008, ua lanakila 'o ia i ka ike maopopo hōʻike ma ka BBC Kanal 3. Ma waho aʻeo ia ia i loko o kēia Competition komo ehiku mau wahine a me nā kino kīnā.
- Nikolas Makkarti - kaulana pianist, ka mea i hānauʻia me ka lima akau.
- Nikolas Vuychich -'Aukekulelia Christian mea nana e hai. Famous no ka i hanau ole i kekahi lala. He publishes i kona mau buke, a hele i ka semināʻo nā mea a pau ma luna o ka honua me oukou i kumu hana, i oe e ole e haawi mai a hiki i ka loa pilikia wahi, i hiki.
- Mark Goffeni - guitarist, hanau me amputated lima. He aʻo e pāʻani me kona mau wawae.
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