Ola kinoMaʻi a me nā kūlana

Myasthenia Gravis: symptoms,ʻike, lapaʻau

I kēia lā, he nui na autoimmune maʻi. I kekahi ke pakele a me ke kōkua o ka pono koho Inc, oiai na mea e ae mai i pane i ka lapaau, a me ka mea wale nō ka mea hiki ke lapaau - e ole exacerbations.

He 'atikala e olelo e pili ana i na maʻi like myasthenia gravis: symptoms,ʻike, a me ka hana o ka maʻi - i mau minute, e ho'āʻo e kūkākūkā i maopopo i hiki. Eia hou kekahi, huli mai i mea susceptible loa i illnesses, he mau aoao, e pale aku i ka pilikia ma laila.

He aha ka myasthenia gravis?

Myasthenia gravis mea he autoimmune mai i ke kumu e holumua ai Muscle nawaliwali. Kēia ia lŘlŘ like me ka hopena o ka hoʻolako 'ole i loko o neuromuscular EYI. Ma ka hapanui o na, e loli i nāʻiʻo o nā maka, nui aʻe ana a me ka maka, ma ka liʻiliʻi loa - hoʻokō i naehana kuleana pili i.

E like me ka 'ikepili helu hōʻike, myasthenia gravis pinepine e loli ai i na wahine ma waena o nā makahiki,ʻoiai i loko o nā makahiki, hoomaka ae la e e kākau i waena o ka hanauna kaikaina.

Mea Maluna o ka maʻi

ʻaneʻane i na mai hiki ke hoʻolaha ma type. Au ua i koe, a me ka myasthenia gravis. Ano o ka maʻi e hilinaʻi ma ka likeʻole aʻe, nolaila, ke nana aku ma ka loa, he pono ole ano.

Ke kaumaha ma muli o ka makahiki pae o ka hoʻomanawanui myasthenia gravis hiki e:

  • congenital;
  • nā pēpē i;
  • wa opiopio;
  • makua;
  • hope mana.

Ke kaumaha ma muli o ka lapaʻau hoailona o ka maʻi i ke kēia mau 'ano i kapaia myasthenia gravis:

  • maka shape;
  • musculoskeletal;
  • pharyngeal-maka;
  • generalized.

Symptoms o kela a me keia o naʻano o ka maʻi kūkā mai ma lalo nei.

Nā kumu o ka maʻi

Ka mole kumu o ka maʻi nō koe unexplored. Ua ua waleʻike i ka maʻi ia lŘlŘ ma muli o ka blockage o ka'ōnaehana paleʻea'ōnaehana receptors ma na nāʻiʻo. E like me ka hopena, e hiki ke pane i ka kūpono neural no lepa mea.

Ka maʻi myasthenia gravis hiki e congenital a loaa. Ka palapala mua ka nui rarer, a me kona kumu i aaiaoe mutations.

Lilo myasthenia gravis hiki hoike mai ai ia ia iho ma luna o ke kāʻei kua thymomegaly (benign prostatic hyperplasia, thymus) a me ka hikoko. Emi olelo, i ke kumu o ka maʻi hiki e ka autoimmune maʻi, e like me scleroderma paha dermatomyositis.

He nui na ka wā myasthenia gravis hoʻomohala e ku e ia i ke kāʻei kua o ka maʻi 'aʻai. Ma kekahi, e piliʻeho wahine nā loko (prostate, ovary), ma ka liʻiliʻi loa - akepaa, akemāmā, a no laila, ma luna o.

symptoms

He aha hoailona, e kōkua i ka hana i kaʻike,, "myasthenia gravis"? Symptoms paha e okoa paha hui ke kaumaha ma muli o ka palapala a me ke kahua o ka maʻi.

Ocular myasthenia gravis e loli ai:

  • hoʻopoepoe Muscle o ka maka;
  • ka maka nāʻiʻo ;
  • Muscle, i mea kuleana no ka hookiekie ana i ka luna lihilihi.

E like me ka hopena, i ka symptoms o keia palapala o ka maʻi i e like penei:

  • pilikia i hoʻomālama na maka;
  • strabismus;
  • palua hihiʻo;
  • ka impossibility no ka manawa lōʻihi, e nana ma ke kaawale mea kekahi pū He kokekau wale;
  • palupalu o ke keena lihilihi (ptosis).

Hope o ka noonoo symptoms e hoike mai ai ia ia iho wale nō i loko o ke ahiahi, a ma ke kakahiaka loa kahi e.

Front ano o ka myasthenia gravis pu ma symptoms:

  • loli i ka leo, a i ka "ihu" a me ka poe makapo;
  • pilikia me ka olelo (i ka hoʻomanawanui loaʻa luhi, a hiki ma hope o kekahi mau minuke o ke kamailio);
  • pilikia a me ka aiʻai ana (ka hoʻomanawanui ka loa paʻakikī e mama i paa ai no o ka nawaliwali o ka AYEIE Muscle).

Me ka make o ka pharynx he mea he pahiki kiʻekiʻe o ka wai ingress i loko o ka naehana'āpana. O ke kumu ho i ka mea i ka hoʻomanawanui mea e hiki ke lawe paa ai, a hiki i iiiaʻi, i ka hana he pinepine ana. E like me ka hopena, ia mea fraught me ka hooulu ana o ka wehena pneumonia.

Musculoskeletal ano o ka maʻi ua pu ma ka luhi ana o kekahi mau hapa o ke kino. Ma ka hapanui o na hihia, ua pili i na lala. Aia mau hihia, i ka wa o ka hoʻomanawanui hiki a hiki ole lawe i ka mau kiaha o ka wai a pii i ka anuu.

Ka noho pilikia loa o ka generalized ano o ka maʻi. Ua hoike mai ai ia i ka nawaliwali o ka ÷ naehana hanu nāʻiʻo, a hiki alakai i ka huʻi hypoxia a me ka make.

E like me 'oe ke ike, myasthenia gravis, na symptoms o i nā loa like, o ka mea nui a me ke ola-hooweliweli maʻi. Ia mea ke kumu ia meaʻano nui e nana i ka muli o ka pilikia, a no ka lawe a pau pono ana.

No laila,ʻo kēia mau 'ikamu i e e kūkākūkā i loko o ka? Aieao o ka theme like "Myasthenia Gravis", -ʻike, a me ka hana o ka maʻi.

ka lawelaweʻana mea

Myasthenia Gravis - keia mea hala loa he pohihihi keia maʻi. No laila, i ka neurologist hiki ole manawa wikiwiki e hana i ka pololeiʻike.

He aha E e hana i ka hōʻike 'inikua kāna hana e like me myasthenia gravis? ʻike, e nā:

  • he ana o ke ahonui i ka alo o ka hoopii;
  • lapaʻau ninaninau;
  • prozerinovoy e mālama nei i ho'āʻo ma;
  • Ka hoao ana me ka edrophonium;
  • electromyographic like;
  • hoomaopopo ana i ka nui o nā mea'aʻaʻa e acetylcholine receptors i loko o ka lāʻau lapaʻau;
  • maka hōʻike;
  • Me tomography o ka pahu;
  • MRI;
  • ka huli akemāmā kuleana pili i.

Iloko o ke ao, ia mea nui, e hoʻopau hiki maʻi a pau, na symptoms o ka i ai i kekahi mau loa i like me na symptoms o myasthenia gravis. No ka laʻana, ka mea, i e bulbar maʻi pale, hoʻoʻino maʻi (meningitis, encephalitis),ʻeho ho okumu ia ma o ka lolo kumu (hemangioblastoma, glioma), neuro-muscular maʻi (myopathy, Guillain maʻi pale, ALS, etc.), cerebrovascular maʻi (ischemic instult ) a no laila, ma luna o.

Lāʻau lapaʻau o myasthenia gravis

Ke kaumaha ma muli o ka symptoms, a me ke kahua o ka maʻi ke ĸokoĸa ana nä pane, a me ka makemake 'ano o ka Inc.

Keʻano hana mua pono ai 'i ka hoʻoikaika' ana impulse EYI ma neuromuscular hookui ana. Loa pinepine hoʻohana 'ia no keia mea e like pharmacological konohiki me "oksazil", "Neostigmine" "Pyridostigmine" a no laila, ma luna o. ka mea, a pau i ka like 'ano o ka hana a me ka hoomahuahua i ka lehulehu o ka acetylcholine. Mau ai 'i loa mana ma ka noho pakele o ka maʻi i loko o nā kahua o ka hoʻonaʻauao kakahiaka o kona ulu ana, e like me ka manawa o ka hoouka kaua ana o crises.

ʻO kekahi mea e pono ai, e hana ai - i ka pono, e hoʻomaʻa i ka wai a me ka electrolyte koena i loko o ke kino. Kēia e pono e kūponoʻai ana i B nā wikamina a me potasiuma e hōʻoia 'maʻamau pūnao.

Holomua o ka maʻi komo ai i ka hookamaia o oiʻano pākīkē lapaau ana. Ka mea, he poe i? Eaia o immunosuppressive hormones. I loko nō o ka mea i mau ai 'i poorly tolerated ma ke kino, i ka pono o ko lākou hoʻohana mea nui i oi aku Loaʻaʻiaʻaoʻao waiwai, o ka oi aku i ka wa e hele ai i ka malama ana i wale ola, akā, i ke ola.

E lohe!

Aia nō kekahi ai 'i pololei i papaia e e e i kaʻike, "myasthenia gravis". Mau nā Hoʻokolohua-blockers, makanekiuma paʻakai, kalipuna hakaka, antibiotics, aminoglycosides, thyroid hormones, tranquilizers, Morphine, quinine nā mea loaʻa, antipsychotics, barbiturates, a me ka hapanui hypnotics a me kiaha dala.

Eia hou kekahi, ua pono ole poina e hiki ke lawe i kekahi mea lāʻau lapaʻau lāʻau ma hope o ka kauka o ka manawa i oleloia ai wale, e lawe i ka mooolelo a pau na ano kanaka o ka meaola.

Lapaʻau me kaʻoki kino

Uluwehi O Inc Aʻole i mau lawe mai i ka makemake hopena, a pakele o ka pilikia. Nolaila, ia mea pinepine pono iʻoki lāʻau lapaʻau 'uao. Ia, ma ka huli, e komo e paa ana i kekahi a me kekahi mau hana:

  • mechanical e hoʻokomo ea ma ka hihia o ka impossibility o ka noho'na makaainana i ulu hanu;
  • plasmapheresis koko me ka hoomaemae ana o'āno'ē nā mea'aʻaʻa, kahi i ke kaʻina hana e halihaliia oia iwaho mau i mauʻanuʻu;
  • keʻenaʻoihana Inc a me ka physiotherapy - kēia mau kaʻina hana mau mai i kiʻi pohaku uinihepa, o ka maʻi, akā, hiki ke kōkua i ka hoʻomanawanui, e Makuakane me fluctuations ma Muscle ikaika.

Eia hou kekahi, ka mea i e pono ke wehe i ka thymus gland maʻoki kino.

Anei i aeea Inc

Kēiaʻano o ka noho pakele o ka pilikia i ole i loaa ia ia ākea hiʻona, akā, no ka mea, o ke kumukuai o ka hoomanao ana a me ka pili ana ia ia.

Lapaʻau me anei i keena loko mai adipose'aʻaʻa, ua hōʻike kiʻekiʻe nui ka hoʻokōʻana i loko o ke kaua ana i ka maʻi. Ka mea, he hoʻonui i ka i kā mākou hoʻopaneʻe o ka wā o ke kala. Healthy anei i keena kōkua? Aiiio keʻano o ka hanaʻana o ka hanu a me ka moni 'ia. Eia hou, ka mea, he hoʻonui i ka hoʻopau o ka ptosis i loko o ka shortest hiki manawa.

I ka papa o ka lapaau a me ka alapine (frequency) o ka hooponopono ana o anei i aeee i loko o ke kino hiki wale hāʻawi aku i ka hoao ana hoʻomalu!

Ei i ka wā e hiki mai

E like ma ka hope kenekulia, i kaʻike, o "Myasthenia" ke ano o imminent make. Akā manawa hele, a me ka lapaʻau 'aʻole e ku malie. I ka manawa, ua nui keʻano o ka kūikawā huahana e kōkua hoola ola, a hoʻonui loa i ka wā o ke kala.

I ka Ia manawa, ua pono ole poina ia myasthenia gravis mea he maʻi maʻi. Kēia 'o ia hoʻi i nā mea maʻi e i ka manawa a pau e ia ma ka iapaau ana (a me ka ikaika holo' awelika) e mālama ola. Ia mea,ʻaʻole paʻakikī, e koho i ka pono o ke ola i loko o keia hihia e me ka nui loa koʻu hoomanawanui ana'ku ia.

No ia mea, ia mea pono e reiterate ia wale nō ka 'eleuʻike, no ka maʻi hiki ana kona Holomua i loko o ka' eleu kūpono a me ka pale aku complications.

relapse Kāohi

Mākou kamailio e pili ana i keia pathology like myasthenia gravis. He aha ka mea, i ka pu ma symptoms o ka maʻi, a ina paha he mea he pono ka lapaau ana i ka maʻi, ua kūkākūkā pū. Mahope au makemake makemake e noho ma luna o nā kiʻina hana o relapse Kāohiʻana, e like me ka hoʻomanawanuiʻana, i kēia kumuhana ka loa pili.

Mua, ka nui hoakaka ma ka mooolelo no ka neurologist. Ma keia hihia, ma kekahi hihia hiki ole e hala ka? Oaony i kūpono, akā, i loko o ka hanana o symptoms e leka uila i kekahi kauka kaua,ʻaʻole e kali ana no ka mea e hiki mai ana makaikai.

Ka lua, ka mea i pono, e nānā i, a, ina he pono, hoʻomaʻa i kou maʻamau ola. Nā mea maʻi me ka myasthenia ole kekahi kumu e loaʻa e physical luhi, no laila ia mea kupono e koho i kekahi 'oihana, ka hoʻolako' noʻonoʻo hana. Inā hiki, oe e kali i ka lōʻihi like 'ole o ka huakaʻi, pela me ka pili ana i ka lehulehu amo.

Mākou e mai poina i kekahi maʻi, a hiki SARS, ke kumu i ke kino stress a me ka hoʻohuikau o ka'ōnaehana paleʻea nenoaiu. He nolaila, nui no ka pono kanaka hoʻoponopono i ka moku'āina o ko lākou ola, e pale aku hypothermia a me ka ole, e noho ma wahi me ka nui nā hoʻohui like o ka poʻe i loko o ka wā o ka mau prevalence o infectious ka maʻi.

Ma ke alo o ka myasthenia gravis loaa ana i kekahi lapaau e like me kou kauka, no ka mea, ua nui kūikawā contraindications (kekahi hoʻomanaʻo mai luna ia).

Hana ole pakiko-lapaʻau, a e ola!

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