Ola kinoMaʻi a me nā kūlana

Polycythemia oiaio. Kumu, Symptoms,ʻike, lapaʻau

Polycythemia - ia mea he maʻi a hiki ke nānā 'ia e nānā i ke kanaka i ka maka wale. A ina ua lawe aku mai PalekanaEND_LINK examinations, ke kanalua a me ka malama ole i koe. Ma ka 'inikua moʻokalaleo loaʻa nō nā inoa no keia pathology: erythremia, Vakeza maʻi. Nānā 'ole o ka makahiki, i ka maʻi poses he nui hoʻoweliweli' i kanaka ola. Ma kēia 'atikala e kamaʻilio mākou i loko o nui au mamuli o kaʻano papa hana o ka hanana, ka iniiaiie symptoms, kahua o ka hoʻonaʻauao a me nā'āpana hana e mohai aku.

kekahi mau 'ike

Ma lalo o polycythemia pili myeloproliferative koko Ka maʻi 'aʻai ma i ka iwi lolo produces ulaula koko keena ma excessive dala. I ka uuku loa 'ē'ūhū eiiiiiaiou mahuahua ua malama,ʻo ia a me nā leucocytes platelets.

Red koko aeee (RBCs i ole ia) paʻa kūhohonu loa me ka o oxygen, a pau kanaka keena, e hoopakele ia ia mai ka maʻiʻaʻai a hiki i ka nenoai o ka mea na nā loko. Ka mea, i kekahi kuleana no ka wehe 'ana o ke kalapona'okikene lua, mai na nā'aʻaʻa, a lawe aku ia i na ia maʻiʻaʻai no mahope exhalation.

Erythrocytes i hua mai la noke i loko o ka iwi lolo. He He spongiform iiiaanoaa nā'aʻaʻa IIeEeAIEUIeXAIIUE loko o ka iwi, a me ka mea kuleana i ke kaʻina hana o ka hematopoiesis.

Leukocytes - keʻokeʻo koko aeee e kōkua kaua nā mea palahēhē. Platelets i anuclear aeea hakina ma ka haunaele vascular ano hoopono. Ka mea, i ka hiki ke hoopili aku i kekahi i kekahi, a occlude i ka puka, ma ia noho i ke kahe ana ke koko.

Polycythemia oiaio ua wehewehe aku ma excessive? Iecaianoaaiiuo o ka ula koko keena.

prevalence

Kēia pathology ua ana diagnosed i loko o nā mākua, akā, hiki ke hana i loko o adolescents a me nā keiki. Ka maʻi hiki ole e manao ana no ka lōʻihi manawa, i mea asymptomatic. E like me ka haʻawina, ka awelika makahiki o ka hoʻomanawanui iki mai papa koa mai ka 60 a hiki i kahi o 79 makahiki. Young kanaka ua ikaika nui ae emi mai paha, e kiʻi maʻi, akā, i ka maʻi holo ia he nui ka paʻakikī. Na elele o ka ikaika ke keka, ina e manaoio oe i ka 'ikepili helu, oi pinepine ia kekahi mau manawa diagnosed me ka polycythemia.

pathogenesis

Ka hapa nui o ke ola kino pilikia pili i ka maʻi, ia lŘlŘ aie i ka mea ana mea ulu i loko o ka helu o ka ula koko keena. E like me ka hopena, i ke koko i excessively manoanoa.

Ma ka kekahi lima, a mahuahua nui kona (viscosity) hoʻonāukiukiʻana mai o ke kahua o clots (thrombi). Ka mea hiki ke ālai ia 'aʻe me ka maʻamau koko ma na arteries a me aa koko. Oia ke kahua o pinepine i ke kumu o ka hahau ana a me ka naau ino. Ka mea o ua mānoanoa ke koko i loko o kekahi mau manawa ke kua'āina o na moku. mai i ka naau, e hooikaika nui e hoʻoikaika ana i ka literally pahu aku ai ia ia.

Ka meheu o ke koko, aole ia i ae i ka na nā loko, e loaa i ke koi 'ia o ka nui o oxygen. Kēia entails ka hooulu ana o ka naau e loaa, headaches, angina, nawaliwali, a me ka 'ē aʻe ola pilikia, i pono ole e waiho unattended.

Mea Maluna o ka maʻi

  • I. ka loiloi mua ke kahua.
  1. Ua mau no ka 5 makahiki a oi.
  2. Ke spleen o maʻamau nui.
  3. Koko ho'āʻo ma hōʻike i ka lōpū mahuahua ma ka helu o ka ula koko keena.
  4. Complications kākaʻikahi diagnosed.
  • II A. polycythemic mua.
  1. Duration mai ka 5 a hiki i kahi o 15 makahiki.
  2. Aia ka he hua o kekahi nā loko (spleen, ake), kahe ana ke koko a me ka thrombosis.
  3. Mau mea o kaʻeho ma ka spleen iho hana ole.
  4. Kahe ana ke koko hiki hoʻonāukiuki hao deficiency i loko o ke kino.
  5. Ma ke Ka Ikepili o ke koko, he mea he paakiki mahuahua ma kaʻulaʻula koko keena, keʻokeʻo aeee ke koko a me ka platelets.
  • II ka anu u B. polycythemic me myeloid metaplasia spleen.
  1. Kālailai hōʻike i mahuahua ka maʻiʻo o nā mea a pau i ke koko keena, koe lymphocytes.
  2. Aia He He neoplastic kaʻina hana i loko o ka spleen.
  3. Ka lapaʻau kiʻi o ka depletion akaka, thrombosis, kahe ana ke koko.
  4. Ka iwi ka lolo mea he gradual ho okumu ana o scars.
  • III. Anemic ke kahua.
  1. Ma ke koko, aia no he hoopaapaa emi i loko o erythrocytes, platelets a me leukocytes.
  2. Aia He He haʻi mahuahua i loko o ka nui o ka spleen a me ka akepaʻa.
  3. Kēia pae 'ana e hoʻomōhala ana i loko o 20 makahiki ma hope o hōʻoiaʻiʻo nō o kaʻike,.
  4. Ka maʻi hiki ke iho i loko o ka huʻi paha maʻi leukemia.

Nā kumu o ka maʻi

Eia naʻe, e ka poe akamai i hiki ole ke olelo mea kumumea alakai i ka ulu ana o na maʻi like polycythemiaʻoiaʻiʻo.

Loa hoʻi i hāliu mai i ka mea hoʻomaʻi-aaiaoe kumumanaʻo. E like me ia, ua wahahee kūikawā nā mea hoʻomaʻi (aia nō ma kahi o 15'āpana) i loko o ka kanaka kino, a ma lalo o ka aoao o kekahi kumumea i he kūlana maikaʻiʻole i ka'ōnaehana paleʻea pale aku ia lakou, komo i loko o ka iwi lolo a me ka lymph aka wahi. laila, na keena, ua kahi o ke oo ana hoʻomaka koke hoʻomaka e puunaue me ka mahuahua, ho okumu i ka hou koena ai.

Ma ka kekahi lima, polycythemia kumu i e pee ana ma ka hereditary predisposition. ʻepekema, ua maopopo i keia maʻi e oi prone e pani mau pilikana o ka poe mai kanaka, a me ka poʻe me ka hoʻopōʻino 'ole o chromosomes.

Predisposing i ka maʻi kumumea

  • X-Ray irradiation, ionizing pāhawewe.
  • Intestinal nā mea palahēhē.
  • Nā mea hoʻomaʻi.
  • Tuberculosis.
  • ʻoki kino.
  • Pinepine stress.
  • Lōʻihi-makahiki hoʻohana o kekahi pūʻulu o ka ai '.

lapaʻau kiʻi

E hoʻomaka ana, mai ka lua o ke kahua o ka maʻi, i loko o ka pathological kaʻina e holo anaʻaneʻane a pau nenoai o na nā loko. Aia ma lalo iho nō i ka pilikino aloha o ka hoʻomanawanui.

  • Nawaliwali, a me ka haunting ano o ka luhi.
  • Mahuahua sweating.
  • Ke hana keaka emi ma ka hana.
  • Loa headaches.
  • iaiyoe hoʻopilikia.

Polycythemiaʻoiaʻiʻo hiki e pu no hoi ma ka hahai ana symptoms. I kēlā me kēia hihia lākou oolea loli aʻe.

  • Aa koko a me ka hoʻololi i ka hue o ka ili. Nā mea maʻi e hoailona oukou i ka alo o ka pono i ho'ākāka 'aa koko. Ma keia maʻi wehewehe aku ma ka lepaʻano-Wai kamako iki i ka ili, ka mea i oi loa kekahi 'ma o ka paku ole ia māhele o ke kino (alelo, lima, maka). Mau lehelehe i uliuli, i kona mau maka ua bloodshot. He loli ka helehelena mea ku pono i ka hoʻohālana o kaʻilikai ipu koko, a me ka ia slowdown i loko o kona paipai '.
  • Itchy ili. Kēia symptom ia lŘlŘ i loko o 40% o ka hihia.
  • Rodonalgia (transient ahiʻeha ma nā manaʻo kōkua o na manamana a me nā manamana wāwae, a i pu ma redness o ka ili). Ka muli o keia symptom ua pili i hoonuiia pae ana o ke koko platelets a me ke kahua o mikrotrombov.
  • Mahuahua i ka nui o ka spleen.
  • Keʻano o nā ulcers i loko o ka'ōpū. No ka mea, o ka mea liilii, moku thrombosis mucosa kino haalele i kona ia'ku i Helicobacter pylori.
  • Koko clots. Lākou mau kumu i wehewehe ia e hoʻomāhuahua mau ana i ke koko (viscosity) a me ka loli ma ka vascular pā pōhaku. E like me ka rula, e like me ke kahua hele aku ai i ka hoʻohuikau 'o ke koko holo ma ka lalo lala, cerebral a me ka coronary moku.
  • Pain i loko o nā wāwae.
  • Kaumaha kahe ana ke koko mai ka nui aʻe ana.

lapaʻau '

Kuhikuhi i ke kauka 'ohi i ka piha' inikua mōʻaukala. He hiki ke noi aku i ka helu o ka clarifying nīnau: ka wā eʻikeʻia discomfort / breathlessness / ola discomfort, etc. It mea hoʻomalu i nui, e hooholo i ke alo o ka maʻi maʻi, inoʻano, hiki kino me kaʻawahia waiwai ...

A laila, he physical ninaninau. Ke hoʻomalu e hoʻoholo i ka waihoʻoluʻu o ka ili. By palpation a me ka 'enehana hou hōʻike i hoonee aku spleen paha akepaʻa.

No ka hōʻoiaʻiʻo nō o ka maʻi he OAXA koko e ho'āʻo ai i hoonohoia. Inā ka hoʻomanawanui i kēia pathology, i ka hoao ana i nā hualoaʻa e like penei:

  • Mahuahua i ka helu o ka ula koko keena.
  • Ke kiekie kiko'î hematocrit (pakeneka o kaʻulaʻula koko aeee).
  • High hemoglobin kiko'î.
  • Low pae o ka erythropoietin. Kēia hōmona He kuleana no ka stimulation o ka iwi lolo i loko o ka? Iecaianoaaiiie o houʻulaʻula koko keena.

ʻike, kekahi hoʻohuʻu ka lolo biopsy a me ka aspirate. Ka mua mana o ke ao komo aiʻai ana o ke kinowai hapa o ka lolo, a me ka biopsy - paa constituent.

polycythemia maʻi hookupaa iho la ia e ho'āʻo ai i ka'ōewe mutation.

He aha e e hana?

Loa lanakila i ka maʻi e like me polycythemia oiaio, ia mea i hiki. Ia mea ke kumu o ka Inc ua hoʻomōhala wale nō ma luna o hoemi i ka lapaʻau hoikeana a me ka hoemi thrombotic complications.

Nā mea maʻi i kuhikuhi ia bloodletting. Kēia kaʻina hana hoʻohuʻu i ka pio ana o ka uuku nui o ke koko (mai ka 200 a hiki i kahi o 400 ml) me ka curative ka manao. He mea pono no ke normalization o ka laupaʻi kiko'î o ke koko a me ka ho'ēmi i kona (viscosity).

Nā mea maʻi i ana i koi ' "Aspirin" i mea e emi i ka pilikia o ka ulu acee? Iuo oeiia o thrombotic complications.

Chemotherapy ua hoʻohana 'ia e malama maʻamau hematocrit, ka wā he mea kaumaha ka ohane, a mahuahua thrombocytosis.

Iwi ka lolo transplantation ua hana i loko o kēia maʻi ka loa pohihihi keia, mai ka pathology i loko o ka hihia o ka pono lapaʻau mea ole lethal.

It E e hoʻomaopopo i ka mau lapaʻau regimen i loko o kēlā me kēia hihia i koho pākahi. Ka luna-i ho'ākāka 'ia Inc mea no informational hana wale. Ua UaʻAʻole pono e ho'āʻo i ka Makuakane me keia maʻi.

hiki complications

Ka maʻi Ua nui lawa, no laila mai i hoʻohemahema wale kona nohoʻana. I ole ia, ka mea, ua mahuahua ka likelihood o kaʻawaʻawa loa complications. O nā nā kēia:

  • Koko clots. Kumu o pathological kaʻina i e pee ma ka hoʻoulu koko (viscosity), mahuahua i ka helu o kaʻulaʻula koko keena, a me platelets.
  • Urolithiasis a me ka gout.
  • Kahe ana ke koko, a hiki ma hope o nīnūnēʻoki lāʻau lapaʻau kaʻina hana. E like me ka rula, e like me ka pilikiaʻalo ma hope o ka niho pōʻalo.

Outlook

Vakeza maʻi - he ke nānā maʻi. Symptoms e ana i loko o nā kahua o ka hoʻonaʻauao kakahiaka o kona ulu ana, e e kauoha no ka koke ninaninau, a hahai-i Inc. I ka wa e kaawale aku o ka pono lapaʻau, ina i ole diagnosed i ka maʻi i loko o ka 'eleu kūpono, make ia lŘlŘ. I ka papa kuhikuhiE kumu o ka make pinepine hana vascular complications a hou 'ana i ka maʻi i loko o ka maʻi leukemia. Eia naʻe, kupono lapaau a me ka kānana adherence i nā koi mai i ke kauka ke me ka nui loa nae i ke ola o ka hoʻomanawanui (15-20 makahiki).

E manaolana aku kakou i ka 'ike a pau i hoakaka ia ma ka pauku makemake e maoli pono ia oe. E hoʻokaʻaʻike ola!

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