Ola kinoMaʻi a me nā kūlana

Subleukemic myelosis - ka benign Lolina o ka maʻi leukemia

Subleukemic myelosis mea kekahi o ka pae ana o kali maʻi leukemia, ma ke kumu o ka maʻi i ka pathological loli precursor keena myelocyte. Ka poʻe me kaʻole maturation o hematopoietic keena ma keia maʻi kaʻina? Ac? Kū'ē fibro-sclerotic lesions i loko o ka iwi o ka iwi me ka concomitant mīkini'opihia o ka iwi lolo a me ka proliferative loli ma ka spleen a me ka akepaʻa. I mea no ke aha la subleukemic myelosis haawiia i like myeloproliferative leukemia.

Kumu myelofibrosis a me Lolina o ka maʻi

Ma ka hapanui o na hihia, ka maʻi i loko o ia lŘlŘ e hoomanawanui i ka poe i 50 makahiki a 'oi, no laila, he kekahi waiwai pili ana i ka aaiaoe malfunction o nukelea mea kumu a hiki keena, autoimmune kāna hana, mea hoʻomaʻi nā mea palahēhē. Morphological kūpapakū i mieloza hoʻololi a pau ekolu germ hematopoiesis - granulocytic, megakaryocytic a me ka erythroid. He mai ai i ke oolea o kēia mau kāna hana, a hilinaʻi nui no ka maʻi a me ka prognosis.

Ma ka hapanui o na hihia subleukemic myelosis loaaʻano benign, a me he mea he pololei mea hoʻopili ma waena o hoʻomanawanui makahiki i ka manawa o ka hoouka kaua ana o ka maʻi a me ka prognosis - ke kaikaina i ka hoʻomanawanui mea, ke paʻakikī i ka mea myelofibrosis ia lŘlŘ. I ka maʻi ke kahua o ka maʻi, i hiki ulu hope 5-15, a he 20 makahiki ma hope o ka ka loaʻaʻana o nā symptoms mua, nā mea maʻi i hoʻohanuʻana hoʻoponopono ulia. A laila, i ka maʻi i ma luna o nā hiʻona o huʻi leukemia: he nui helu o ka nouʻana mai eʻikeʻia i loko o kaʻike ākea koko. Symptoms o ia ka ulu ana o ka maʻi i ke kuni, na hoailona o ka intoxication, anemic a me ka hemorrhagic maʻi pale. Ua Ua pinepine mahuahua spleen a me ka akepaʻa. Ma kekahi nā mea maʻi, o hiki mai kokololio Holomua o ka maʻi me ka kakahiaka nānā aku ana i ka maʻi pale o ke kahe ana ke koko, a me ka hoʻomanawanui ka anemizatsiey.

Ka lapaʻau kiʻi subleukemic mieloza

Loa pinepine nā mea maʻi e pili ana i olelo ia mau nawaliwali, ehaeha ma ka abdomen, a maoli he me ka hele, a oi loa aku hoi ma hope oʻai (ia mea ku pono i ka nui mahuahua ma ka spleen a me ka ake). Aia mau hoopii o ka headache,ʻeha i loko o ka iwi, a me ka spine. Loa kākaʻikahi, i loko o ka maʻi ke kahua o ka maʻi, i ka hoʻomanawanui i hoʻomōhala loa sensory ka haunaele. Ke kauka Pono e pono hookaawale ia myelosis funicular - he pathological ano o ka ua'emi'ōnaehana i ia lŘlŘ ka wā kekahi megaloblastic anaemia. Keia ano pinepine ia lŘlŘ ma ka anaemia, a ia lŘlŘ i loko o nā mea maʻi me ka lawaʻai ana o ka wikamina B12 i loko o ke kino.

Eia kekahi, thrombosis pinepine i hoʻomaka ai, a lilo ia i ke kumu o ka mahuahua helu o platelets maʻike ākea koko i mau, a me krovi.Poslednee coagulation kāna hana i ke kauoha ae la ia e kekahi morphological immaturity a hiki loa aku i ka nui loa o platelets. Ma neia hope aku, thrombocytosis hele aku ai i ke kūpono 'ana o ke splenomegaly, akā, i loko o ka spleen e hoomaka ana e uhai ia platelets ole wale akā, i ka ula koko keena, i kumu no ka hooulu ana o ka anemia.

Ka loiloi polokalamu a me ka lapaʻau koho no nā mea maʻi

ʻike, "subleukemic myelosis" E e kau mai ma luna o ke kumu o ka lapaʻau koko e ho'āʻo ai, a me ka hopena o ka sternal puncture a iliac trepanobiopsy. Loli i loko o ke koko ho'āʻo mea pili 'ole-kekahi a wale ma luna o ka' ike o ka mahuahua a emi ma ka helu o ke koko keena, a hoʻololi i kā lākou mau pakenekaʻaʻole hiki ke diagnosed "subleukemic myelosis".

Lapaau ana i ka maʻi mea i kalele iho ma luna o ka moku'āina o ka iwi ka lolo, a me ka loaʻa 'ole iwi abnormalities. Ma kekahi mau hihia, nui hōʻeuʻeu kilo o ka hoomanawanui, akā, i ke koke i holopono nō myelofibrosis e ia i ka hookohu o ka chemotherapy ai '.

I ka maʻi ke kahua o ka maʻi i loko o kekahi manawa, pono e undergo pāhawewe Inc, papakaukau hookohu o ka chemotherapy no huʻi myeloid leukemia lapaʻau polokalamu, ana o ka spleen - akā, i loko o kēlā me kēia hihia o ka maʻi lapaau i ka hoʻomanawanui, e koho i kekahi palapala hōʻoia no hematologist.

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