Ola kinoMaʻi a me nā kūlana

Adrenal hyperplasia - He aha ka mea? Symptoms a me ka lapaʻau o ka maʻi

Endocrinologists i loko o kā lākou hana ua pinepineʻalo me abnormalities i loko o nā puʻupaʻa. Adrenal hyperplasia - He aha ka mea? Puʻupaʻa - hui kaulua hui, ka adrenal glands i ke aupuni 'pono ma luna o ka glandular palapala. Aia i hana e pono ai na kanaka kino hormones (adrenaline, noradrenaline, glucocorticoids, a me ka wahine). Hyperplasia aʻe nā hormones akau, a ua ukali ia e kekahi mau symptoms.

Adrenal hyperplasia - He aha ka mea?

I ka adrenal hyperplasia aeea'aʻaʻa hui kaulua glands progressively Hoʻonui i ka pono, i ke kino ua nui mahuahua ma ka nui, nae ka mea hoopaa mai ai i kona mau helehelena. Adrenal medullary waiwai ninoieo o a me ka wauke.

I hookuu e loli ai ka adrenal cortex hyperplasia, aia hoʻomōhala ana i kekahi pathological kaʻina. Ke Kula Kaiapuni 'ʻeho pinepine diagnosed i loko o ka medulla.

Ua hoike mai ai ia i ka maʻi ma kekahi mau makahiki i loko o nā wāhine, nā kānaka a me nā keiki.

Congenital adrenal hyperplasia ua loaʻa ma ka lapaau loa pinepine ana. IeAUPIIe, IAa IO ka mea, hāpai he hereditary, akā, hiki no hoi ana i loko o ka helu ana o kekahi adverse wahi lulu ole mawaho aʻe. E like me nā pathology ua 'akomi i loko o nā mea maʻi me Cushing ka maʻi pale (40% o nā hihia) maʻi pale. Kēia maʻi pale ua ana diagnosed ma ka waena a me ka wa elemakule.

Kēia mea pathology hiki ole ke malama ole. I ka hyperplasia ua Nyos? Iecaianoaaiiuo o hormones e pono ai. Ma nā wāhine, ka mea pinepine ke kumu no infertility. He nui na ano o ka maʻi: nodular hyperplasia o ka adrenal gland, nodular, eiei, congenital a me ka micronodular, a me hyperplasia o medial wāwae. Loa pinepine keia maʻi ia lŘlŘ i loko o nā wāhine.

Nā kumu o ka maʻi

Ke kumu no symptoms hou ka wā adrenal hyperplasia i loko o na keiki, na kanaka a me na wahine, e e okoa. Na mea a pau e hilinaʻi ana ma ke 'ano o ka maʻi. Hyperplasia pili ia i kekahi o na? Ueony, ia paha e idiopathic, solteryayuschey, virility.

I ka loaʻa o kaʻeleuʻano hypertensive? Iecaianoaaiiuo o androgens a me mineralocorticoids, e like me ka hana i ka ino ole maʻaʻa puʻuwai moku a me fundus, pinepine hele aku ai i hypertension maʻi pale.

I ka solteryayuschemʻano hyperplasia mahuahua androgen-i? Iecaianoaaiiuo, pela ka mea, he nele o nā hormones i lawe ia e ka adrenal cortex. Comes hyperkalemia a hypoglycemia. Ka pilikia o ia i ke kino o dehydrated, mi kino.

Ka wā virilnoeʻano hyperplasia malu androgen superaktiven. Mawaho genitalia nui mahuahua ma ka nui, he mau huehue, mahuahua kino lauoho, musculature nui hoʻomohala i ka nui mea.

Mua o nā mea a pau pathology hoʻomaka e holomua ma muli i ka māhuahua secretion o steroid hormones. Ke loaa ke ano o ka maʻi i ka helu o ke kī kumu ke kumu ia ala ae la:

  • metabolic kāna hana;
  • ikaika aʻo nui;
  • Cushing ka maʻi;

Congenital adrenal hyperplasia aie i ka mea i hiki i hāpai keiki, i gestation, ooieoeiiaeuiiai loli hoʻomōhala. Kekahi a'ōlelo hoʻohali - ka EYI o ka maʻi ma ka aaiaoe kiʻekiʻe. Makaʻu hoʻonāukiuki i ka hoike ana mai o symptoms o ka maʻi: he malfunction o ka hypothalamus a me ka pituitary abnormalities ma ka aaiaoe pae, he innate kū kaʻawale cortex hui kaulua glands, ili, mai kā lākou poʻe kūpuna.

nodular hyperplasia

Kauka e puʻunaue i ka Holomua o adrenal hyperplasia i loko o kekahi mau hui e like me ka lapaʻau kiʻi, e like me ke 'ano o ka pele.

Nodular adrenal hyperplasia. Kēia palapala i hereditary. Ka hapanui pinepine diagnosed i loko o ka poʻeʻelemākule, ua ano hoomainoino me ka manawa. I ka hoʻokō 'ʻike, hoike mai i kekahi ano hiʻona - ma ka wauke o adrenal nodules hana. Ka mea hiki e mau (lobed 'ole), a he hoʻokahi, mai ka 4-5 knm. Aey? Acaeoey? Cushing ka maʻi pale. Ke pathology mea ma muli o ka ikaika stimulation o adrenocorticotropic hōmona, ua synthesized ma ka pituitary gland. Ke kumu nui hiʻona o nodular hyperplasia me Cushing ka maʻi pale nā:

  • headache;
  • "Makika" mua o ka maka;
  • convulsions;
  • pōniuniu;
  • mau malaise;
  • ke kaupaona i waiwai ai kuhikuhi (o ka opu,'ā'ī, maka);
  • mahuahua ikaika loa ka makemake;
  • kikoo hoailona ma luna o kaʻili;
  • huehue;
  • hirsutism (i loko o na wahine);
  • ilihune e noho;
  • hyperpigmentation;
  • kiʻekiʻe ke koko;
  • pinepine fractures;
  • kaumaha.

eiei? hyperplasia

Ma keia palapala o ka prostate hyperplasia i ole hoʻololi i kona kinona, ka mea ulu o gradual. Akā, i ka manawa hookahi a lakou kuahene nodules. E kuhikuhi i keʻano o ka maʻi, he pilikia. Ma ka maʻamau iaoiaeii o diagnosing ka ultrasound ole hopena. e loaʻa ai i ka loli o ke kino wale ma MRI ole HI. Pinepine hoʻomōhala hapalua ano, a ana ka wā o nā kēia symptoms: adrenal hyperplasia i loko o nā wāhine pinepine hiki aku ai i ka mahuahua ma ke kino lauoho, hoikeia mai panic ho'āhewa wale, hypertension, obesity. Ma kekahi mau mea he mea poino glomerular a me ka hoʻomōhalaʻeluaʻaoʻao hyperplasia.

Ke pathology o idiopathic aldosteronism ua ma muli o ka mea ulu ma ka aldosterone secretion. I ka hyperplasia glomerular ciia hōʻike i nā kēia symptoms: hypertension, convulsions, Muscle nawaliwali, i kaupalena 'o ka neʻe, oolea mai i ka lōlō, ka makewai, mahuahua mimi auaiaea, nighttime urination. Kekahi mea ku ei ke kumu no ka hoomahuahua i loko o ke koko potasiuma, acidosis. Hoʻonuiʻia ke koko, ua malama mau.

Nodular a congenital ano

Nodular palapala ana progresses i loko o nā keiki a me nā adolescents. Ua hiki ke hoike mai ia ia iho, no ka paewaewa ole adrenal hana no i ka overdose o glucocorticoids. Key hiʻona o nodular shape: ole momona hoʻokomo kālā, Muscle atrophy, pigmentation o kaʻili, symptoms o mimikō, nā aʻalolo pōʻino a me ka mea'ōnaehana mānowai koko, osteoporosis. Inā keiki symptoms o ka maʻi i 'akomi i ka manawa, lawe mai i ka hormonal lapaʻau, ka prognosis e maikaʻi. Hyperplasia o ka hema adrenal gland - He aha ka mea? Ma keia hihia, hyperplasia mea,ʻaʻole e kaukaʻi ma o ka hana o hormones. I ka kupu hikoko oi aku ma mua o 3 knm hana ua koi 'ia. Laparoscopy ua hoʻohana 'ia paha e like me Fedorov papa hana lyumbotomicheskim komo i ka peritoneum ma kaʻaoʻao hema.

Congenital adrenal hyperplasia (VDKN) ua diagnosed oi pinepine ma mua o nā? Ueo. I keiki i loaʻa ma ke alapine (frequency) o 1 a hiki i 12 tausani. Ma keia ano, i ke keiki kekahi 'metabolic a me ka nānā aku. Aia i ekolu papa kuhikuhi ano o ka (ole-panina, hemahema hoi panina, virility a me ka solteryayuschaya.

Ka loa, he pono ole palapala i solteryayuschaya. Hoike aku i kaikamahine ia me wahahee germofroditizm, keikikane pouli ili a puni o ka scrotum, penis piʻina ma ka nui. No nā mea maʻi wehewehe aku ma ka haahaa ulu a me symptoms e like me drowsiness, nausea, lethargy, haʻahaʻa ke koko, dehydration, ilihune kona'ōpū. pono e hana ia ka maʻi a me nā lā mua o ko lakou ola, a hiki i ka make.

Ma ka panina palapala mea,ʻaʻole ma luna o symptoms, akā, he mea ka ulu i loko o ka hoʻololi kemikala o keka kāne hormones. Inā ka maʻi ua ole oia, hou pilikia ana i loko o nā wāhine i loko o ka moe a me ka noʻonoʻo '.

Ke ole-panina palapalaʻia i loko o kanaka makua o na wahine a me adolescents. Ke kumu hoopii o ka infertility, menstrual paewaewa, hirsutism a me ka huehue.

Adrenal hyperplasia: mau symptoms

Loa pinepine, na keiki, na kanaka a me na wahine malama holoiia ano o ka maʻi, i ka wa aole mea i haʻi symptoms, ma na hihia a pau ia mea paakiki e diagnose i ka maʻi. Congenital palapala ua ho'ākāka 'ia i loko o nā keiki ma ka makahiki mua a me ka lua o ke ola ia.

I mau, adrenal hyperplasia (mea ia mea, ua wehewehe mua mākou i) i ka i kēia ka papa kuhikuhiE symptoms:

  • lolelua ke koko, (haʻahaʻa a kiʻekiʻe);
  • ka uuku o ka holomua o ka mimikō mellitus;
  • ke kaupaona mea ulu;
  • hoike ana mai o ka osteoporosis;
  • numbness o nāʻiʻo, ko lakou mau hope atrophy;
  • Women i "Luna-e like maka";
  • paʻa hoʻopilikia;
  • ko mākou hopohopo breakdowns;
  • pigmentation;
  • kikoo hoailona ma luna o kaʻili;
  • haunaele ma ka gastrointestinal'āpana;
  • hookuu iho no e hoʻonele;
  • nocturnal hookuu o ka mimi;
  • excessive makewai;
  • psychoses;
  • infertility;
  • amenorrhea;
  • Mai kona mau makahiki-kūpono ulu kiʻekiʻe;
  • ka emi loa hairline i loko o ke kino māhele'āina;
  • hirsutism.

Na kanaka a me nā wāhine oko i loko o ka lapaʻau hoailona o ka maʻi.

lapaʻau Nā Kūlana

Ke kumu o ka lapaau mea oiaio ka hormonal Inc. ʻepekema, i ole i hoʻoholo pehea e pono e hana ma ka adrenal hyperplasia. Lapaʻau ua pinepine hui. No ka adolescents i ia mea i normalize olelo o ka haumāna ke keka ano, kaikamahine hōʻike estrogens a me nā keiki - androgens.

Hoʻohana 'ia ma ka lapaau ana o na kēia mau pu o glucocorticoids:

  • cortisone'ākeka;
  • hydrocortisone;
  • dexamethasone;
  • prednisolone.

Iloko o ka lā i ka hoʻomanawanui ke launa i ka 2 a 3 nā māhele o nā hormones (i loko o like dala). ? Aaeno? A 5% monakō koko pāʻoihana. Kaikamahine, e like keiki, ke ola a pau i ia e ka mea hoomakaukau.

No kēlā me kēia hoomanawanui i ke kauka e huli i kekahi hana e hoʻokokoke e hāʻawi aku kona lapaʻau ka hoʻolālā (mea a pau hilinaʻi nui ma luna o kona hoao ana a me kaʻike). Single Inc ma ka iapaau ana o keia mai, aole ia i nei.

Congenital hyperplasia o adrenal cortex loaʻia ma surgeons. Aia mau hihia i na wahine hiki ole ke differentiated like wahine a kane. No kaikamahine ka mea, ua pono ea me ka ole kinona o ka labia. Ua i loko o ka makahiki mua o ke ola hōʻike ia i ka hana, i kekahi manawa (ma loa ana) ka mea, ua lawe mai hope. E i ka hana, a me ka hikoko.

Inā i ke kino i nele i ka paʻakai, i ka hoʻomanawanui e hoonui i ka kela la i keia mahele lāʻau o 1-3 nā huna. E hoonohoia i loko o ia hihia, a me ka mineralocorticoid.

Eiei? Hyperplasia lāʻau Inc aʻole i nui ai. Ua Ua koi i loko o ia mau hihia adrenalectomy. Ineffective lapaau a me ka aldosteroma ia hui me ka eiei? Hyperplasia. Ke kēla Ua noho lakou malaila. Ke kumuhana o ka poʻe uʻi a ka lāʻau Inc, a me ka zona glomerulosaʻeluaʻaoʻao hyperplasia (idiopathic hyperaldosteronism). Ana ma keia hihia - mea he lōʻihi ana.

Ke mainstay o ka lapaʻau IGA - loaa ana spironolactone, ia mea he hoa o ke aldosterone. I ka hoʻokō o ka lāʻau eplerenone. Spironolactone ua pinepine ia ma ka hui pu ana, me ka kalipuna hoa. Inā na symptoms keia arterial hypertension, lapaʻau me ka ACE nā mea kūpale ua pili.

Ma ka hihia o kekahi? Eaia o virilization o ka hoʻoponopono ai 'ana ma kekahi mau manawa. Inā i keʻano o adrenal hyperplasia pili i ka virilizing, e ia i ka hookohu o ka cortisol. Ua hiki ke hoʻohana 'me he intramuscular ka pahu kui. Mahele lāʻau lalau Kauka. No ka mua keiki i hoʻohana prednisolone.

Inā he mea i pono lapaʻau, ka hyperplasia i alakai i ke kūpono 'ana o ka maʻi Kona a Cushing ka maʻi. Hope kuponoʻike lapaʻau e hoʻomaka koke.

ʻike, no ka maʻi

Adrenal hyperplasia - He aha ka mea? Pehea e diagnose i ka maʻi? Nodular a eiei? Hyperplasia akomi i loko o ka papa o vocal a me ka keʻena hoʻokolohua noiʻi. Ka lapaʻau 'puke: ahonui ana, physical ninaninau, clinical ninaninau, radiological ninaninau aʻume mākenēki resonance kiʻi, radionuclide kaʻimiʻana. E like me nā hualoaʻa auhau waiwai, a me ke ano o nā adrenal glands. Radioimmunoassay hana keʻena hoʻokolohua noiʻi. Hooponoponoia ia mea, ma ka mimi a me ke koko cortisol. No ka Loiloi i ka hormonal kūlana haʻahaʻa, ke manao nei-ua hoʻopili immunosorbent mea o loko. I kekahi manawa, he mea pono e hoʻomaka wehena puncture.

E like me ka hopena o kaʻike, ke kauka e huʻe i kaʻike, a me ka waihona o ka iaoiaeii loa pono o ka nohoʻana.

Hyperplasia nā mākua: mea e hana ai?

I hookuu hyperactivity o ka adrenal cortex e diagnosed ma ka wā kamaliʻi, akā, i ka hoailona o ka maʻi ikea i loko o nā mākua. adrenal hyperplasia i loko o na wahine ua wehewehe aku ma ka ulu kiʻekiʻe o pubic lauoho, leo hohonu, huehue, eha ma ka hope o ke poo, nocturnal kāʻili 'ana, ilihune, e ai ana, a mahuahua nui ke koko, adrenal maʻi pale.

Inā e loaʻaʻoe iāʻoe iho i loko o kēia mau symptoms, mai i ho'āʻo i ka diagnose oe ia oe iho. Ma kēia hihia mai i ke kōkua, a me ka poʻe laau. Urgently ka hoʻoponopono 'ana i kauka. He mea pono i ka hormonal lapaau. IeAUPIIe, IAa IO, na wahine me ia iʻike, ua i paipai i ka manaʻo hāpai keiki. Ma na hihia a pau, a hiki ole i ka hanau. I kekahi manawa, i ka pono pāʻoihana a hiki i ka pilikia - ka piha hoʻopau o ka mea maʻi hakuʻala, a pau kona appendages.

Kāohi

He aha ka adrenal hyperplasia - mea oi loa Pono e ike i ka poe Leomakana i? Oaony i ka hanau ana o ke keiki, a ma o ka 'ohana ka mea, (genetically) i na hihia o congenital hyperplasia. Eʻoluʻolu, e hoʻohuli i i geneticists - mākaukau, 'ike' Oihana. No ka mea Kāohiʻana o ka maʻi, e pono e eʻike, o perinatal (i ka manawa o ke keiki ua ka ulu a me ka mea i loko o ka opu o ka makuwahine). Ma ka trimester mua o ka hāpai keiki ua lawe mai chorionic villus mea hōʻikeʻikeʻuʻuku. Ma ka lua o ka hapalua o ke koi 'Ikepili o amniotic loli, a e hooholo i ka nui o hormones.

Koho - IVF. Ma keia hihia, e hiki e i ka mua aaiaoe Ka Ikepili o ka germ keena mua ka mea, i fertilized.

Ma gestation i nā wāhine diagnosed me hyperplasia e ia ma lalo mau hooponopono ana o ke kauka mau kekahi, a pau koi 'ia e ho'āʻo ai. E e hoʻokoe 'ia mai ke ola o nā mea a pau e hikiʻawahia waiwai, a me ka waiwai o ka pāhawewe.

No ka mea Kāohiʻana o adrenal hyperplasia Radio he nui a Mānoa a me ka loiloi e ho'āʻo ai i ka e hana i loko o ke keiki pēpē. No ka mea Ikepili ka mea, e pono ke lawe i ke koko mai ka capillary (he wahi i kohoʻia no ka puncture kuekue wawae kao).

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