Caroli ka maʻi: Symptoms a me ka iapaau ana

Caroli ka maʻi o ka loa luna 'iaea ooieoeiiaeuiiai ka pioloke o ka ake,ʻike, a me ka hana a ke kumu pilikia nui no kauka.

He aha mea he maʻi

Caroli mai - pohihihi keia congenital ake maʻi, kena ae la ma ke anoe o ka bile ducts, Aia maloko o ka kino. Ua Ua wehewehe aku i loko i ka maʻamau kalepa ae la lakou ua Nyos bile stagnation ia lŘlŘ a me kona ka piʻiʻana maʻiʻaʻai. Pinepine i ka maʻi mea, he pono ole i loko o nā kānaka, a me ka mea i hoʻomaka me ka noho 'ana kamaliʻi a adolescence. I ka holomua o ka pathological kaʻina hana hilinaʻi nui ma luna o ka huina a me ka degere o ka poho i na ducts i loko o ke akepaʻa.

ano o ka maʻi

I ka lā, he kuokoa Mea Maluna o Caroli ka maʻi ma ka lapaau ua nalowale. Naʻe, manaʻo huhū keia, ma laila nō nāʻokoʻa ano o ka maʻi. Ka palapala mua ua wehewehe aku i loko o ia ka mea i haki biliary patency, a me ka mea hope kahua o nā pōhaku.

Ka lua o ka palapala pili me ka congenital hepatic fibrosis. Ma keia hihia, aia no he hōʻemi iki? Anoe o na ducts a me ke kahua o ka pohaku, he hiki, nae ka mea, i kekahi manawa ana i loko o nā kuʻina ma hope o ka maʻi.

Pae holomua Lālā paʻa bile ducts paha e pili ana i mau mea o cystic ake, a pela visualized paku paia ai hanaʻia naʻe i loko o cyst lumen.

kumu o ka

Caroli ka maʻi pili i ka maʻi congenital i kupu ma muli i ka autosomal recessive pololei o ka'āina hoʻoili. Inā 'oe i kahi kokoke hoahanau me ka like pathology, ma hope o ka hanau ana o ke keiki koke Pono e hoʻomaka i ka hulina ninaninau, me he mea he nui wale o ka hele ana ma hereditary maʻi.

Ma kekahi mau hihia, i ka maʻi ua i huiʻia nā pathological kāna hana o ke akepaa, a complicates nui i ka iapaau ana.

Ka papa kuhikuhiE symptoms

Caroli ka maʻi symptoms ke hoike mai ai ia lakou iho i loko o ka loa kekahi makahiki i loko o nā keiki a me nā keiki kanaka. He hiki ke lawe i ka papa kuhikuhiE hiʻona o ka maʻi e like me:

• abdominal eha;
• kuni;
• hōʻemi iki yellowness o kaʻili;
• ake hoʻonui ma palpation.

Kaha lapaʻau hoike ana mai o ka maʻi i pinepine me ka hanana o ka li nui hou pili. Holo nōhie Caroli maʻi ua diagnosed i kane keiki. Ma ka exacerbation i Ua heʻoi mahuahua i loko o ka nui o ka bilirubin, a keʻokeʻo koko aeea helu.

ka lawelaweʻana mea

I loko nō o ka mea i na symptoms o ka maʻi lawa i olelo ia, akā, ka mea, o kekahi ano o na mea he nui 'ē aʻe akepaʻa kāna hana. Pololeiʻike, a me ka hooholo i ka hiki Caroli ka maʻi i loko o ka US a me ka manawa HI. Me tomography ua manaoia kekahi o ka loa informative ano o ka hoike, no ka mea, e hiki ke ike pono lawa a pau i ka 'aʻe' ana o na rula. Eia hou kekahi, endoscopic cholangiography i ke koi 'ia no kaʻike,.

Ake hana ho'āʻo ma no ka lōʻihi manawa 'aʻole e hoʻololi i ole, nae, a me ka Holomua o ka maʻi a me ka hooloihi ae i hoʻoʻino kaʻina i loko o ka biochemical Ka Ikepili o ke koko ke huai ae i ka hoailona a pau o ka cholestasis.

No ka mea, nā mea maʻi i ma pilikia o ka cholangiocarcinoma, e halihaliia oia iwaho o ka hou, a serological loiloi no ke alo o kaʻeho hōʻailona.

Hiʻona o ka lapaʻau

Ma ke alo o Caroli maʻi lapaʻau lula pono e malama me ka 'ole' aʻole, no ka mea, i kēia pathology mea e holumua ai ma ka ano. Lapaau o ia hoʻi, ma ke noi ana o ka laulā-pae antibiotics, a me ursodeoxycholicʻakika aaieieno? You e ole calculus ho okumu.

Eia hou, i ka iapaau ana maupaʻa:

• analgesics;
• litholysis na pohaku;
• biliary nōkahea.

Ma luna o ka piʻiʻana, cholangitis, a me nā complications o ka purulent Inc mea i okoa mai ka iapaau ana o ka mea koʻohune cholangitis. He nui e wehe i ka pus, a laila, ua lawe hoomaemae ana mai o ka bile leki uea, a noi aku la antibiotics e kōkua wehe maʻiʻaʻai.

Ke hana ua hana wale i loko o ka hihia o pinepine exacerbations a ineffective hoʻohana o ka makeʻe kulana 'ana i kūpono. Ka buke o kaʻoki lāʻau lapaʻau 'uao i ĸokoĸa ana nä pane nunui. pohaku wale paha biliary ala hiki ke wehe.

Ma ka hihia o ka loa ikaika? Aiey ala a me biliary bile stagnation, ka surgeon ke alakai i ka wehe 'ana o kekahi lobe o ke akepaʻa. I loa hoopii, hepatic insufficiency ma ke alo a me na hoailona o ka degeneration i loko o ka malignantʻeho, he ake transplant i e paipai mai i kekahi hoahanau pili.

No ka pane pololei, ka hapanui kauka Paipai Noho kekahi akepaʻa transplantation a hiki i ka wa e kaawale aku o ka loa symptoms i loko o nā kuʻina ka loiloi mua o ka maʻi. Pinepine, nae, i ke alo o ka maʻiʻaʻai mea he contraindication e transplantation. nā mea maʻi ola ana ma hope o transplantation me ka congenital fibrosis ana i ua aiiieieoaeuii diagnosed cholangitis i transplantation, Uaʻano haʻahaʻa.

Prognosis o keia maʻi loa ai noho lakou malaila, no ka relapses kānāwai ma luna o kekahi mau makahiki. Eia naʻe, nui kākaʻikahi ia Nā hualoaʻa ma ka make ana o ka hoʻomanawanui.

Caroli maʻi

Caroli maʻi muli o kona kulana pinepine pili me ka congenital hepatic fibrosis, kūpono ma ka Caroli maʻi. Ua o kēia mau pathologies i hana ia e ka kokoke'ālike palapala biliary kāna hana i loko o akepaa'aʻaʻa i ka pae ana o embryonic? Acaeoey. Ka maʻi pale ua ili ma ka hoahanau pili, a me ka hoike abdominal eha, a kahe ana ke koko mai esophageal varices. Neonates paha e kekahi hui malu pu ana o na kumu nui symptoms o congenital hepatic fibrosis, Caroli maʻi a me ka polycystic hakuʻala maʻi.

Kēia maʻi pili i ka congenital bile leki uea cyst,, ia nae mea he pohihihi keia, a ka hapanui i loko o kanaka elemakule ma lalo o 30 makahiki. Ma ka mea mua mau makahiki o ka pathology ia lŘlŘʻaneʻane asymptomatic, like loa me ka anoe o ka bile ducts mai i hoʻonāukiuki stagnation o ka bile, a e hana rula no ka ho okumu ana i na pohaku a me ka piʻiʻana maʻiʻaʻai. Inā hoʻohana pū me nā ae nānā mau hoailona o ka jaundice, e Hōʻike i ke alo o ke cholangitis.

Ua kaulanaʻano nui hema-kapakahi ake pōʻino, akā, e hiki no hoi ia i mau-ala i loko o kekahi mau hihia.

Ma kekahi mau hihia, ke akepaʻa mea, no ka ikaika i ka mea hiki ke aloha ia 'ē nā loko. Nolaila, kekahi o na complications hiki ke noʻonoʻo me ka hanana o kaʻaʻa puʻuwai ole.