Hemolytic-uremic maʻi pale - He aha ka mea?

Hemolytic uremic maʻi pale o ka symptom, a ua hoikeia mai ma ka palapala o ka hemolytic anaemia, OPN a me ka thrombocytopenia. No ka mea manawa mua i ho'ākāka 'ia i kēia maʻi i ka 1955. E like me ka poe akamai, ma kahi o 70% o ka hihia i kaʻike, i loko o na keiki o ka makahiki mua o ke ola, a me wale i kekahi mau mea i hana 'i hoʻopaʻa i loko o nā mākua. Ma kēia 'atikala e olelo e pili ana i kēia maʻi mākou, a nana no hoi ma pehea e e hanaʻia ke kālā no ano o hemolytic uremic maʻi pale.

koke kumu

Ka hooulu ana o keia maʻi hoʻomalu ma ka keia lā ua pili i kekahi mau aʻe. Kuhikuhi i kēia mea hoʻomaʻi 'anaʻawahia poino capillary endothelium no laila, i kapaʻia glomeruli. ka mea 'ē aʻe lima kumu ma i moe i loko o DIC, a me mechanical poino i erythrocytes. Ua Ua manaoio aku i ka la mahope hiki ke poino i hooholo ma ka capillaries o glomeruli iho, i mea i huli piha me ka fibrin clots.

ka papa kuhikuhiE symptoms

Hemolytic-uremic maʻi pale ia lŘlŘ puleʻAmelika, i na keiki me ka kokololio emi ma ka mimi auaiaea, akā, i loko o ka wa e kaawale aku o ahuwale na hoailona o ka dehydration, a ma luna o ke kāʻei kua o kŘpa maʻamau VEO kiko'î. Inā kekahi kamaiki i ke kuni, a me ka luaʻi,ʻikeʻia loa paha i ka maʻi progresses hoʻomaka koke - ua he cerebral edema. Pinepine, hemolytic uremic maʻi pale ua complemented e haikea-ua kēnā keiki, ma ka pohihihi keia hoopii, a me ka poe liilii, pele.

diagnosing

E hookoiaʻi ka mea iʻike, i hemolytic-uremic maʻi pale, e pono e hele i ka moʻo o ka ho'āʻo ma, a me ke koko piha Ka Ikepili. Wale nō ma hope o ka piha ninaninau o ka hoʻomanawanui ke olelo e pili ana i hou lapaau.

Hoikehonua, ano o ka lapaau

More nei iʻike, make ua loa kiʻekiʻe (80 a hiki i 100%). Eia naʻe,ʻepekema mea mau e imi i ka pāʻoihana a hiki i kēia pilikia. Pela ia i hana i na mea maalea kapaia "ʻimi hoʻopunipuni hakuʻala", mahalo no i ke kulana i hoʻololi radically. I kēia lā, make aneane loa ana (ma waena o elua a me ka umi pakeneka). Ka mea, e ia wale n? I ka hopena maʻi ka loaʻaʻana, e like me ka pono me i loko o ka ulu ana o irreversible keʻano o ka hanaʻana i loko o ka lolo ma muli i kona nani. It E e kaulana i ka ʻike, ka atypical hemolytic uremic maʻi pale, ano laulā, pono, mai 2 a hiki i 9 kau (kela la i keia) ka hoʻohana 'ana i ka "ʻimi hoʻopunipuni hakuʻala". Ma keia dialysis hoʻomalu e malama maʻamau o metabolites, e like me pale lolo nani.

Outlook

Hoikehonua, ano ae keiki e Makuakane me kēia pilikia. Naʻe, i kēia mea hiki wale nō i loko o ka hanana i ka maʻi i loko o 'akomi i kona wā kahua o ka hoʻonaʻauao. I ole ia, i ka likelihood o hoopau ai i ke ola i kekahi mau mea ma lalo. E like me ka poe akamai, i ke kahua i loko o ka wa e kaawale aku o ka maikaʻi pane ma ka aoao o ke kino ma hope 2-3 kau o ka hemodialysis, ke wānana i loa lakou malaila.