Ola kino, Maʻi a me nā kūlana
Ke etiology o sarcoidosis a me nā mea maʻi i hookahuli ai i ka maʻi pale Lefgrena
Lefgrena maʻi pale - he symmetrical hilar aka wahi bronchopulmonary lymphatic'ōnaehana ma nāʻaoʻaoʻelua. Maʻi pu ma ka ili hoikeana (erythema nodosum), kiʻekiʻe kuni, a me ka arthralgia. Mau symptoms i ano o ka sarcoidosis.
I ka wā o ka maʻi e loli ai i kekahi mau nā loko - maʻiʻaʻai, spleen, lymph aka wahi. Lefgrena maʻi pale sarcoidosis i ho'īli a me ka mea i ka lele maʻi. Not ia e hookahuli ai i ka oncologic maʻi keʻano o ka hanaʻana a me ka tuberculosis.
lapaʻau kiʻi
Sarcoidosis Ua pio ka polokalamu loa he lōʻihi manawa i ke nānā maʻi, akā, i keia la i ke kulana i loli, pathology hohola i ka uku kokololio a puni ka honua. Wahi a ka 'ikepili helu, oi ma mua o kekahi mea'ē aʻe, e ae aku i ka maʻi pale Lefgrena wahine mai ka 20 a hiki i 40 makahiki, akā, i ka maʻi ke hele mai i kekahi kanaka.
Ua hiki ke hana me ka symptoms, progressively 'ole i loko o ka huʻi palapala. Asymptomatic? Aaieou ana 'akomi i ka wale i kāohi fluorography ninaninau. Ka loa, he pono ole ka he gradual Holomua o ka maʻi, a no ka mea kēia mau hoailona:
- dyspnea ma exertion;
- he hoopaa hoi ache i loko o ka pahu;
- ʻeha ma waena o ka uha mua kōmi 'ana ;
- maloo cough;
- haʻahaʻa-papa kuni ;
- luhi a me ka nawaliwali;
- excessive sweating;
- kahe o ka ikaika loa ka makemake;
- oleloʻeha ma ka lalo hoʻi.
Huʻi no ka sarcoidosis kapa maʻi pale Lefgrena, ka mea, ua pu ma ka hooulu ana i ka mahana e 38-39 ° C, hui eha, ili lesions i loko o ka palapala o ka erythema, umaumaʻeha a me ka pokole o ka hanu. HeʻAʻole uncommon ma ka huʻi iloko o piha hou ana me ka hoʻohana 'ana o ke kanaka' inikua lapaʻau a me nā uao ai '.
Ke etiology o ka maʻi
A hiki i ka hopena o ka lapaau ike kumu o keia maʻi, e hoʻoneʻe 'ia paha e hoonaukiuki ia ia ma ka kēia mau kumumea e hoʻomōhala:
- maʻiʻaʻai, Mycobacterium tuberculosis, hepatitis C;
- adverse mawaho aʻe, ana mea hiki ke hooheheeia lepo;
- e uwahi ana, i mea ole ke kumu pono, akā, nui complicates i ka papa o ka mea maʻi;
- nā kūpuna mai.
Kāohiʻana o ka sarcoidosis
Maʻi maʻi pale Lefgrena nui, e hooki aku i ka uiki e, e oia i ke ola. Pono manawa e ninaninau nā loko o ka pahu i loko o 2 makahiki. Lālau aʻela ia i loko o no o ka mea i ua ole i ike i ka etiology o ka maʻi a hiki i ka hopena, i ka hua mua o ka kāohi 'ana i ka e ulu. Poe akamai i paipai aku, e pale aku Hoʻokaʻaʻike me ka mea hiki ke hooheheeia ka lepo a me ka foci o ka maʻiʻaʻai.
Lefgrena maʻi pale sarcoidosis akomi i kēia mau extrapulmonary IIeEeAIEUAA kaʻina - hoʻolilo i ka subcutaneous'aʻaʻa,ʻili a me kaʻike ākea lymph aka wahi. Aia ka he mahuahua cervical, subclavian, axillary a me inguinal aka wahi. Ma kekahi mau hihia, o ka loli lymph aka wahi o ka abdomen.
Iwi a me ka Central ko mākou hopohopo'ōnaehana e loli nui emi pinepine, akā, he paʻakikī no ka maʻi ana. Sarcoidosis o ka naau ia lŘlŘ i loko o 20-30% o ka hihia i asymptomatic. e hoemiia hemaʻaoʻao o ka naau ma ka buke, i ka akau ventricle, piʻi pū.
I keia hookolokolo ana a me ka hana i haawiia mai kuu manawa e hilinai aku ma luna o ka maikaʻi hoʻokūkū. Ma kekahi hihia, ma laila nā loli i loko o akemāmā'aʻaʻa, a ho'ōla hiki aku ai i kīnā o ke kino.
Lefgrena maʻi pale huʻi sarcoidosisʻano
Pinepine pioloke me ka sarcoidosis, tuberculosis no ka mea, o aʻo Kīwala'ō o symptoms. Kēia pono i ka hoʻokolokolo pono ninaninau, no ka mea, na kumu a me kekahi Inc. I ole hihia hiki ole ke komo i loko o ka hoʻoponopono lapaʻau, pela e lawe ai 'manao no nā mea maʻi me ka tuberculosis, ka mea hiki ke alakai i ka make.
Lefgrena maʻi pale (he Classic hoʻohālike) - kēia mea, i ka wa o ka hoʻomanawanui i ka mau ana mea kupono helu. Aia nā loli i ka ili. E hele mai:
- papules a me plaques;
- Chilblains lupus;
- keloid scars;
- infiltrates;
- erythema nodosum;
- SKD a CKD sarcoid Beck;
- mau anuanu aka wahi i loko o ka subcutaneous'aʻaʻa.
lapaʻau '
Ka loiloi 'ana o nā mea maʻi Lefgrena maʻi pale mea e hana X-Ray. E like me ke ano hoohanohano a hana ka hoʻohana 'ana Me tomography. Hoʻomaka biochemical a me ke koko helu.
Ka pilikia o ka lapaʻau mea e uhi i ka hoʻoʻino kaʻina. Ka loa efficientʻaoʻao o ka hoʻohana 'ana o corticosteroids no eono mahina. Inā ka mea, e loli ai ka nui nā loko ua koi 'ia glucocorticosteroid hōmona Inc.
Hoʻomaka koke e holumua ai papa ua malamaia lakou nei, me ka pōkole papa o intravenous hooponopono o Anati-hoʻoʻino ai '. Ma na wahi a ka powerless Inc, ua hana plasmapheresis (koko hoʻomaʻemaʻe). Ma ka loa ke kahua akemāmā maʻi koi hui, transplants. Papa o ka maʻi a me ka lapaʻau hoʻokūkū pili kēia 'ano, akā,ʻaʻole e pono, e hoʻomaka i ke kaʻina hana.
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