Ola kino, Maʻi a me nā kūlana
Pituitary dwarfism. He aha ka mea?
Dwarfism paha scientifically, pituitary dwarfism, mea he pathology ma a he mea i kali hou aku; o physical ulu a me ka ulu ana, a ua kauoha aku e nele maila hoʻololi kemikala a me ka secretion o ka ulu ana hōmona (iʻikeʻia e like me ka ulu ana hōmona).
Kēia pathology He loa pohihihi keia, ma ka hola 2 mai o 10,000 kanaka pituitary dwarfism ua 'akomi i loko o elua hou, he pono ole i loko o nā keikikāne ma mua i loko o na kaikamahine. Ka ulu ana i loko o nā kānaka ua noʻonoʻo dwarf ina ia mea emi o 130 knm a me na wahine i ka ia - emi o 120cm.
Ka loa, he pono ole, lalau mai i na kēia:
• hanau mā (ma ka utero anterior pituitary hana incorrectly)
• poo eha (mau loaʻa nā nōhie)
• pituitaryʻeho a puni nā hale,
• aaiaoe predisposition,
• syphilis, tuberculosis, sarcoidosis,
• Neʻe like chemotherapy a pāhawewe Inc.
Eia naʻe, oi ma mua o ka hapalua o nā kumu o ka dwarfism a me ke koena o nä.
E like me ka pituitary dwarfism? Acaeoey oo?
Weight a me ke kiekie o na keiki me ka lawa secretion o ka ulu hōmona i hanau i ole oko mai o ka like aiee o ola keiki. ka mua symptoms loa pinepine ana i na keiki, a hiki i ka makahiki o ka 2-3 makahiki: mau keiki mai i hoomaka i ka mālama i me ka maʻamau ulu o ko lākou mau na¯. Ikaika hoemiia ulu ana, a 'aʻole e oi 3.4 knm / makahiki (ma ka uku ana o ka hola 8 knm / MH). I loko nō o ka lohi o ka ulu, ka pololei huliāmahi o ke kino o ke keiki i mālama 'ia.
Eia hou kekahi, pituitary insufficiency i hoikeia aku ai e na kēia mau hiʻona:
• underdevelopment o ka reproductive kahua,
• kaulana underdeveloped muscular kahua,
• hypotension,
• hoemi i ka mämä holo o ka ossification o ka iwi, pepe niho ulu a me ka loli,
• ina he mea heʻeho ma ka pituitary gland a me na wahi a puni o ka lolo, ma ka hou ana i mau symptoms, ka mea e hoʻomōhala ana i oi a me ka blurred hihiʻo.
IeAUPIIe, IAa IO, noʻonoʻo kūpono 'ana i loko o kēia maʻi, mai ae aku, e hoomanawanui i pele i maikai iaiyoe.
.To hoʻokūpaʻa i kaʻike, o "pituitary dwarfism" Ua pono.
• hoao no ka ulu hōmona. Eia hou, oe e pono e ho'āʻo ai i ka hōʻike 'ē aʻe hormones. Paha oe Pono hormonal ho'āʻo ma: mua paa i maopopo kahi kiʻekiʻe o hormones i loko o ke koko, ma hope i ka hoʻomanawanui i ka lāʻau e loli ai i ka rula o ka hōmona, ma hope o kekahi manawa, ua hai i ka Ka Ikepili.
• E holo X-Ray māhele o ka sella a me ka puniu wale no, e hooholo i ka nui o ka pituitary gland. No hoi e möakäka hou e paa ana ia kamepiula aʻume mākenēki resonance kiʻi o ka lolo, i he painless kaʻina hana, e ae oe e ike i ka au mamuli wahi o ka pituitary māhele, a me ka puni lolo'aʻaʻa. Inā he mea mea hōʻemi o ka hihiʻo, ia mea no hoi e pono ai ke nīnau kekahi ophthalmologist.
Pituitary dwarfism lapaau ana ma endocrinologists. Ka walaʻauʻana hana o ka hoihoi hou ana i ka ulu ana hōmona pae i loko o ke kino, he hope Inc: ka hoʻohana 'ana i ka mauʻimi hoʻopunipuni ulu hōmona. E kōkua i ka i ka ho omaulia ana o ka laʻau heluna a me ka hooponopono ana o ka ulu ana hōmona ua manawa papahana i kūikawā peni no ka pahu kui.
Inā kūpono lapaʻau mea he ulu i loko o ka ulu ana i ka mahana maʻamau (8-12 knm / makahiki), mamua i ka lapaʻau, e like me ka rula, eia wale 3-4 knm / makahiki. Ma puberty E e komo i loko o ka iapaau ana regimen anal hormones.
I ka laulā o ka lapaʻau hilinaʻi nui 'ana ma luna o nā kumu o ka maʻi, ka mea, ua kena ae la. Loa pinepine, nā mea maʻi me ka kūpono hana a hiki i ka ulu ana maʻamau, a ke hakuloli i ke kaiapuni.
I kapa i ka poe akamai i ka hoailona mua o ka pituitary insufficiency!
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