Ola kinoMaʻi a me nā kūlana

Beck sarcoidosis: symptoms, Kāohiʻana, kumu a me nā 'ano o ka hana

Ka papa inoa o ka poe mai, i ole e iho mailoko o hiki ma ka kānaka a me na holoholona, a i ku ae ole möakäka hou a hiki i ka hopena o nā kumu,ʻaʻole ka liʻiliʻi loa o ka Beck maʻi. Sarcoidosis - o konaʻikena inoa. Ua Ua diagnosed loa pinepine, i oi aku 150 mai o 100 000 kanaka, akā, ka mea e loli ai kanaka ma kela'āinapuniʻole, ma ka pili ana ia me a ia ia i ka hoʻonohonoho 'kivila i loko o ka'ōnaehana o ka Mea Maluna o ka ICD-10. Kēia mea e hōʻoia 'ia kauka ma kekahi aupuni ia maʻalahi e ho okele ana i ka wehewehena o ka insidious maʻi, mau hooikaika ana e huli hou ohe. A koke loaʻa i ka pāʻoihana akau, ka wā i ke ahonui o ka pono o ke kōkua.

Sarcoidosis - He aha ka keia?

Beck Sarcoidosis mākaukau kaua paha ma ka wā o ka likeʻole kanaka nā loko Emo ole hoomaka e puunaue me ka hoopahaohao oukou pūʻulu o aeee hiki mai o phagocytosis. Ka nodules (granulomas) okumu ia ma kēia kaʻina hana, i ole ai e hoikeia ia iho i loko o kekahi alanui a me ke kumu o kaʻiʻo mea hōʻemi i ola ke kūlana. Granulomas ke hana i loko o kekahi hui, kēia, a me ka naau, maka, puupaa, akepaa, akā, ka hapanui pinepine IIeEeAIEUIeXAIIUE i loko o ka ia maʻiʻaʻai. Fatalities mea pohihihi keia ma ka sarcoidosis, a hoʻopaʻa 'wale i loko o ka nui hoʻonāwaliwaliʻia nā mea maʻi me ka haʻahaʻa e hoʻonele, a i ole, ua malamaia lakou nei,. Kahi o 10% o nā mea maʻi granulomas i hoʻonā 'ia ma luna o lākou iho me ka lapaʻauʻia. Ka hapanui o kanaka pilikia mai sarcoidosis, e noi mai ana kekahi lapaau, a nīnau aku i ka pulmonologist, cardiologist, ophthalmologist, neurologist, dermatologist, rheumatologist.

Mōʻaukala o ka Kaka

Sarcoidosis i ho'ākāka 'ia ma mua e Beck (Böck), Pelekāne surgeon, dermatologist J. Hutchinson. 53-makahiki-kahiko ke kanaka a me ka 64-makahiki-luahine, nona ka ili ma na wawae a me na lima, he poni granulomas: I ka makahiki 1877, elua hoʻomanawanui iki mai ia i malama. Ma hope o 12 makahiki, ka Palani kauka Besnier ho'ākāka 'ia ma ka papa o ka maʻi i loko o ka hoomanawanui ka mea i like granuloma o ka ihu. Eia hou, ua hoʻomanawanui i ka grayish-uliuli nani o na pepeiao a me ka manamanalima. Nānā 'ole o Besnier, he Norewai kauka Tsezar Bok hana histological hookolokolo e like granulomas, a haawi mai la ia i ka inoa o "benign ili sarcoidosis." He pū i kekahi 'ia o ka lole poni nodules ke ikeia ma mucous i loko o ka maʻiʻaʻai, a me ka Kuekene kauka Schaumann ho'āʻo e systematizeʻikepili ma keʻano hoikeana o sarcoidosis. E like me ka hopena o ka maʻi i kapaia "Besnier ka maʻi - Böck -. Schaumann" Keia makahiki, a manawa e hiki ke 'imi i kekahi palapala' inikua.

International Mea Maluna

Ke ICD-10'ōnaehana sarcoidosis Beck hoʻolaha like kolu-ka papa maʻi. Kēia 'o ia hoʻi i loko o kona etiology komoʻole e hoʻonele. E like me ia i ka International Catalog kivila häʻawi mai ai i kēia maʻi D 86. Sarcoidosis granulomas ho'ākāka 'ia mai a ke kino i ka penei helu:

  • ma ka ia maʻiʻaʻai - D86.0;
  • i loko o ka lymph aka wahi - D86.1;
  • nā ma ka akemāmā, a ma ka lymph aka wahi - D86.2;
  • ʻili - D86.3;
  • unspecified pathogenesis - D86.9.

Inā sarcoidosis diagnosed nā maʻi, i ka helu ana, ua like penei:

  • pu ma iridocyclitis a anterior uveitis - D86.8 + H22.1 *;
  • lōlō o cranial nā aʻalolo - D86.8 + G53.2 *;
  • ka wā arthropathy - D86.8 + M14,8 *;
  • myocarditis - D86.8 + I41,8 *;
  • ma ka myositis - D86.8 + M63.3 *.

Na Mea Maluna o ke 'ano o ka pele

Sarcoidosis Boeck ke hana i ka ekolu 'ano apau loa.

1. maʻi. Ma nā mea maʻi i Ua he mau mea hōʻemi o ke ola, unreasoning nawaliwali, make o ka hoʻolimalima i nona iho.

2. huʻi. Kēia palapala Ua wehewehe aku ma ka ulia wela Jump, E hoomahuahua auanei lymph aka wahi, haanou ana o ka lala ami.

3. Subacute. Aia He He nalu-me ke kuni, mau moderately.

Līkaia no kekahi hana refractory (lapaʻau hiki ole e).

Mea Maluna ma ka oolea

Ho'ākāka 'ia ma ka maʻi ua differentiated ka ekolu degere o ka oolea:

Mua. Ke hoomanawanui Ua hoʻoākea lymph aka wahi umauma (bronchopulmonary, tracheobronchial, paratracheal, bifurcation).

Lua. Sarcoidosis Boeck ka papahelu 2 wehewehe aku i loko o ia e loaʻa ai ka interstitial hoʻoʻino foci i loko o ka ia maʻiʻaʻai.

Ekolu. Ikeia fibrosis (fibrosis) o ka akemāmā'aʻaʻa, e ole ho'ākea i ka intrathoracic aka wahi, akā, hana emphysema. I mai la lakou, pu me foci o ka fibrosis hana nui conglomerates omo. E hoomanawanui i ohumu o ka umauma eha, ilihune ikaika loa ka makemake, ua hanahana loa ka luhi, nawaliwali, maloo cough, pokole o ka hanu,ʻeha i loko o na ami.

Aia He He Mea Maluna, a e hōʻike ana elima kahua o ka hoʻonaʻauao o ka sarcoidosis:

  • 'Aʻohe. I ka maʻi i hoomaka ai, akā, no ka pahu X-Ray hōʻike i kekahi mea.
  • Mua. Intrasternal lymph aka wahi hoʻomaka e ulu.
  • Lua. Lymph aka wahi e hoonee aku, i loko o ka akemāmā'aʻaʻa hoʻomaka e hōʻike granulomas.
  • Ekolu. I akemāmā'aʻaʻa loli ana.
  • Ha. Pulmonary fibrosis.

etiology

Sarcoidosis Beck ICD 10th hou pili i ka maʻi pili iʻole e hoʻonele i ka hopena o ka hoʻokolokolo 'ana i mau hoike i ke kūlana o HLA (kanaka leukocyte antigens) i loko o keʻano o ka granulomas. Ke'ī mai, o ka loci i loaʻa i ka hoʻopale 'ana e ku e ia sarcoidosis paha, ma ka mea ku ole, ka mea, triggers i ka aoao o ka hoike ana mai o ka pōʻino i ka lolo, mau maka a me ka' ē aʻe nā loko.

Maopopo hookupaa i sarcoidosis oia hoi ole lele. I ka nui, e hoike i keia ano maʻi mākaukau kaua paha ma waena o nā lālāʻohana aliʻi, aole ia e noho aliʻi mai kona hereditary EYI.

Paha keia mea a pau i mea loa kekahi e pili ana i ka etiology o ka maʻi. Definitive pane i ka nīnau e loli ai i ka ulu ana o ka maʻi, aka. ʻepekema paipai i kamepiula kumumea hiki e:

  • infectious paha fungal maʻiʻaʻai;
  • pollen;
  • nā palapala Nine Inch kinoea, a ma ka ohu;
  • no kou kino;
  • hewa kālaikaiaola.

epidemiology

Ināʻaʻole i i kaʻoi loa kukuluia kumu o ka sarcoidosis Beck, i ka epidemiology o ka maʻi ua ike pono. No laila, ka mea, ua hoao ia keia maʻi e loli ai kanaka o nā makahiki, e like me na keiki opiopio, akā, oi pinepine ka mea, ua malama i loko o nā mea maʻi elemakule 20-40 makahiki, a me na wahine i oi prone ia ia. KŘpa lāhui kekahi mai kekahi oko ao. Sarcoidosis kākaʻikahi maʻi kanaka i loko o ka Middle Hikina a me Iapana, a ma India ka mea, ua diagnosed i loko o 150 o 100 000. Ma ka'ākau hapa o 'Eulopa, 40 kanaka e maʻi mai 100 000 ma ka hema loa o na huahelu i iki kiʻekiʻe. Ma Australia Beck maʻi ua diagnosed i ka 92 no 100 000 i loko o ka United States i waena oʻApelika Waena Americans huahelu mea 40-64 hihia, a iwaena o maikai-ua kēnā kanaka e maʻi e 10-14 hihia no 100 000 poʻe e noho ana.

Ka mea, oia kahaha ko oukou naau i ka paka e ae mai oe, mai sarcoidosis emi pinepine ia ma mua o ka poe i aʻole 'oe i kēia maʻa.

symptomatology

Sarcoidosis ma ke kakahiaka nui kahua o ka hoʻonaʻauao pinepineʻaʻohe symptoms. IeAUPIIe, IAa IO kanaka i ole i maopopo ia mea, i kēia maʻi. Keia ua loa maopopo na hoailona o ka maʻi e malama a hiki i 3 degere, ka wā ma laila hele mai ka ai-kapaia akemāmā a me mediastinal ano o Boeck ka sarcoid. Ma keia hihia, i ka hapanui o nā mea maʻi i hiki mai symptoms:

  • kahe o ka ikaika loa ka makemake;
  • apathy, lethargy;
  • luhi (hoʻomaopopo, mai ka manawa o ka hoala mai la);
  • wela;
  • Muscle eha;
  • lilo o ke kino ke kaupaonaʻana;
  • cough i ua ole ia me ka antitussive ai '.

Oia hoopii i pinepine ana e huʻe 'ʻike, o ke "anu" a me ka "ARI", akā, i ka Holomua o sarcoidosis lilo ia protracted cough, hemoptysis ikea mai ai ma luna o ka ili i ka ikeia e hiki granulomas. I ka wā e hiki mai,ʻaʻohe hana i e hoʻohuli ai i nā maka, ake, naau, a me nā loko. Symptomatology ma kēlā me kēia palapala, he ano hiʻona. No ka laʻana, 'ano i loko o sarcoidosis D86.8 + H22.1 * hihiʻo deteriorates, i wela ai lihilihi, akaka lua maka. A hiki aku oeʻano D86.8 + I41,8 * hōʻike i na hoailona o ka naau e hemahema, pokole o ka hanu, arrhythmia. Ka wā e kikokiko i D86.3 ikea ma ka ili erythema nodosum. Ka mea, e hoohalike ai i ka poʻe noʻonoʻoʻole. Iʻa maka, forearms, Main.

lapaʻau '

Sarcoidosis Beck i symptoms like me symptoms o'ē aʻe ka maʻi. I mea e pono differentiate ia, i ke ahonui koi hookolokolo a me ka kuka ana i na mea he nui kauka ololi holoʻokoʻa a me ka helu o nā ho'āʻo ma, e hookaawale ia:

  • tuberculosis;
  • berylliosis (ikeia ma ka hui 'ana me beryllium);
  • ka rumatika;
  • lymphoma (malignant neoplasm o lymph wahi);
  • allergic reactions i kekahi mea;
  • fungal nā mea palahēhē.

Ke hoomanawanui hanaʻia i ke Ka Ikepili:

  • koko (a biochemical);
  • mimi (huina);
  • ECG;
  • bronchoscopy;
  • hoʻopaʻa haʻawina bronchial holoi i ka wai;
  • TB hāpana;
  • X-kukuna (ka mea hiki ke hana ia ma ka huipūʻana me kekahi HI ana i ka ÷ naehana hanu'ōnaehana), e loaa pakahi aku la ia i ka pono i nā hualoaʻa ma ka multislice HI, a, e huai ae granulomatous loli o ka naau i hoakaka ia MRI;
  • taroskopiya (hoʻohana 'ia i loko o ka oi aku pilikia hihia a).

US sarcoidosis Beck hana transesophageal haawi maikaʻi loa i nā hualoaʻa ma ka hookolokolo ana i intrathoracic lymph aka wahi. I ka Ia manawa lawe mai i ka biopsy.

Kekahiʻano o ka anamanaʻo - kaʻimiʻana me ka gallium. Kēia mea hiki ke hooheheeia kamaʻilioʻana i loaa i loko o nā paena o ka li nui. 2 mau lā ma hope o intravenous hooponopono ana o ka waiwai o ka mea hoʻomanawanui scan NineManga.com. Ke keakea oia i gallium hiki ke loaa i loko o kekahi o hoʻoʻino foci, nānā 'ole' ana o ka mea ka mea, i ko ka sarcoidosis 'ole' ē aʻe mai.

Iapaau ana o sarcoidosis Beck

Ka pahuhopu o ka Inc no keia maʻi mea e malama i kaʻoihana o ka loli ana i nā loko. Inā ke hoʻomanawanui i ka maʻiʻaʻai he scars, e pohaku uinihepa, o ia hou.

A hiki aku i ka hopena o nā mea a pau i nā ho'āʻo ma hoʻopaʻa i kaʻike, o "sarcoidosis", ke kauka prescribes steroid. Na ka papa kuhikuhiE huahana - "Prednisolone". I ka papa o ka lapaʻau i ka lōʻihi, i ka 8 mahina. Ma keia hihia, aole e eʻaoʻao ole:

  • haanou ana;
  • kaumaha ka uku;
  • houpo eha;
  • naʻau i loko nā poʻohiwi;
  • hypertension;
  • huehue.

Oiai ka lawe i ka lāʻau loa wikiwiki ka mea, he maikaʻi ia, akā, ma hope e hoʻi discontinuation symptoms o ka maʻi.

Ka luna 'ua hoakaka ia "Pentoxifylline", "Methotrexate" "Chloroquine."

Ua haawiia i ka mea i granulomas i nalo ma luna o lākou iho, e hoomanawanui i ka poe i sarcoidosis Aʻole ole i kekahi discomfort a me ka eha, mai kau mai lapaʻau, akā, i ka pololei, ka mālamaʻana o ko lākou mau ola kino you.

Outlook

Inā heʻike, o "sarcoidosis Beck" ma ke HI scan NineManga.com, umauma X-Ray, biopsy Ka Ikepili, hewa hiki ole ia, akā, oe e i pono i ka manao. Ka maʻi a me ka iapaau ana akau, aole e emi i ka hae o ka poʻe e ola ana, aole ia e pili i ka hiki i ka hana, a me nā wāhine a me ka maʻi ole kekahi pilikia e hanau i ola na keiki.

Complications e ala wale i loko o ka hapa o ka mea e hoomanawanui i ka poe i ole, ua malamaia lakou nei, i loko o ka 'eleu kūpono. Ka mea, e loaʻa:

  • naehana insufficiency;
  • nui hihiʻo hoʻopilikia, a me ka makapo;
  • aggravation o na maʻi.

Kāohiʻana o sarcoidosis aole i hoʻomōhala i ka manawa ku pono i ka maopopo 'ana o kona etiology. Kauka e haawi mau wale koi:

  • malama i ka pololei pololei o ka lā;
  • ka naauao, e ai;
  • mai i hoʻomāʻewaʻewa mai ka waiʻona;
  • ʻaloʻana Hoʻokaʻaʻike me ka pilikia Nine Inch, o ka oi aku A i ka wa o ke kiʻekiʻe volatility, e like me ke kinoea make a me ka lepo.

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