Cerebromedullary malformation maʻi pale

Arnold-Chiari maʻi pale mea he nui congenital anomaly o ke poo o ke kanaka lolo. Kona o Mānoa, ke moe i loko o ka disparity ma waena o ka nui o ka posterior fossa o ka puniu wale no, a me na mea e ae ma keia wahi o ka lolo hale. Ua hiki aku ai i kāna hahaiʻaihue tonsils cerebellum a me ka lolo anei i. Ke alapine (frequency) o kēia mau anomalies mea 4-8 hihia no kela 95-100 tausani. Man.

Currently, ka pathogenesis o ka maʻi i maopopo. Presumably, eia ekolu pathogenic aʻe he hoʻonui i kēia kāna hana:

1. congenital, hereditary neuropathy;
2. traumatic eha auka-auka-occipital a me ka Grill hapa ramp like me ka hopena o ka hanau trauma;
3. CSF hydrodynamic puupuu e kū'ē i ka paia o ka spinal kaula Canal, Aia i loko o ka waena.

eha 'ano o nā anomalies i ua anao? aou i loko o ka 1891 Arnold Chiari, e hoʻohana i kēia Mea Maluna a hiki i ka keia lā.

Arnold-Chiari maʻi paleʻano mea moʻolelo holoi posterior fossa puniu wale no, a puni nā hale i loko o ka spinal Canal mea nui haʻahaʻa ma mua o ka nui o ka foramen magnum. Ma ka lua o kaʻano o ka anomaly Ua noho caudal dislocation o ka medulla oblongata, na nā wahi haʻahaʻa o ka ilo, a me ka IV ventricle, a he pinepine hoʻomōhala hydrocephalus. Arnold-Chiari maʻi pale nei i ke kolu oʻano ka loa pohihihi keia, no ka mea, ua wehewehe aku ma ka lohi loa offset a pau i ka lolo nā hale o ka posterior fossa. I ka ha oʻano ua poe e cerebellar hypoplasia. Ke ha a me ke kolu o ke ano o anomalies i loko o ka hapanui hoopii, incompatible me ke ola.

I ka 80% o ka hoopii, Arnold-Chiari maʻi pale ua diagnosed me ka syringomyelia - pathology o spinalʻaha wehewehe aku ma ka ulu ana o cysts o ka spinalʻaha, a i hanaʻia ma ka moʻolelo holoi posterior fossa mīkini'opihia o ka puniu wale no, a me ka cervical māhele o ka spinal kaula. Ke alo aku o kēia mau cysts hiki aku ai i ke kūpono 'ana o ka holumua ai myelopathy.

Arnold-Chiari maʻi pale: Symptoms

Ka lapaʻau kiʻi o ka maʻi ua wehewehe aku ma ka kēia symptoms:

• eha ma ka ai a me ka occipital mau mea, i ka wā kūpono he kiheʻana a me ka puʻu;
• ua hakumakuma i ka mahana a me ka eha pā lonoaʻili, e like me ka luna lala Muscle ikaika;
• lala spasticity;
• pōniuniu, maʻule hou ihola nō, naueue wale no hoi, ano hoomainoino ma ka huli anaʻe i ko oukou mau poo, ua hoʻemi pilikia makapō acuity a me ka mea e like ai o ka hihiʻo.

I, ua hanahana loa manawa symptoms align i kēia mau pōkole-makahiki cessation o ka ha (apnea), ka mea hoʻonāwaliwali maoli nō o ka pharyngeal reflex a me ka kokololio, involuntary ka neʻe 'ana o na maka.

Ma kekahi mau hihia, Arnold Chiari anomaly hiki ole i kekahi symptoms, a ua loaʻa loa ma ka paha ma PalekanaEND_LINK kaʻina hana. ʻike, o ka mea maʻi ua lawe mai ka hoʻohana 'ana MR kiʻi, a Me tomography me ekolu-dimensional? Aeiino? Oeoey o ka cervical vertebrae, a me occipital iwi.

Arnold-Chiari maʻi pale: iapaau ana

Ia lapaau hilinaʻi nui ma luna o ka hoʻomanawanui, a me ka oolea o ka maʻi. Ma kēia mau iniiaiie symptoms like headache a me nā 'ano o ka eha, kou kauka i waiho aku eha ka lapaʻauʻia a me ka pololei, ponopono-UPS. Kekahi e hoomanawanui i hoike no ke kokua i ka wa e lawe Anati-hoʻoʻino ai 'e hiki ole ai paha hoi e hookaulua ka hana.

Loa pinepine, lapaʻau, kauka makemake e pana aku au i abnormalities surgically. Ke hana mea e hooki aku i ka Holomua o ka loli o ke spine a me ka lolo 'ole a me ka noaaeeecaoee o symptoms. I ka lawe ana mai i ka holomuaʻoki lāʻau lapaʻau vmeschatelstva me ka nui loa emi puʻe ma ka spinal kaula a me ka cerebellum, e like me ka hou ana CSF outflow. He mea likeʻole i kūpono o ka hana e hilinaʻi ana ma ka hydrocephalus. Ka awelika lōʻihi like 'ole o kaʻoki kino o kekahi, a me ka hapalua no, elua no hora, i ka loaa au i elima a hiki i nā lāʻehiku.