Ola kino, Maʻi a me nā kūlana
Dystrophy - o ia ma ka lāʻau lapaʻau? Akepaa, ka naau, cornea, Muscle
Dystrophy - he maʻi i loko i ke kino nā'aʻaʻa ia lŘlŘ i loko o ka poho ole hoʻomāhuahua o ka waiwai i mea ole i ho'ākāka 'ia ma ka maʻamau moku'āina.
Poino i na keena, a intercellular waiwai hiki aku ai i ka mea i ka mai hui, ekolu pohaku e kuleana pili i ponoʻole. Ke kumu o keia maʻi mea trophic kāna hana (moʻo o keʻano o ka hanaʻana i hoomakaukau nui haʻawina o aeee).
kumu o ka
Kēia pathology he nui kekahi mau mea, lalau mai. Ua hiki e hereditary metabolic kāna hana, infectious maʻi, stress a me ka noʻonoʻo 'pilikia, i kuʻu iho e hoʻonele, malfunction o ka gastrointestinal'āpana, ilihuneʻai, i ka hopena maikaʻi' ole o ka likeʻole aʻe, chromosomal a me somatic maʻi.
Ua mea hewa i ka dystrophy - he maʻi ia e loli ai premature wale keiki. Ka hooulu ana o ia i ka maʻi hiki i hooloihi ae i ka hookeai a me ka liki ole o ka carbohydrate-naʻai i loko o kaʻai. Ke kumu o congenital dystrophy i eʻoi'ōpiopio paha, ma ka mea ku ole, kūpuna makuwahine.
symptoms
Ke kaumaha ma muli o ka 'ano a me ka oolea o ka maʻi, he ekolu degere, a i wehewehe aku e kekahi symptoms.
Ka mua degere - ka hoʻomanawanui mea he emi ma ke kino a me ka paona Muscle leo, nā'aʻaʻa e emi laholio, nee'ōnaehana paleʻea nenoaiu, ma laila i ia pilikia a me ka noho.
Lua o ke degere - ku e mai i ke kāʻei kua o ka holumua ai ke kaupaonaʻana lilo i thinner, e hiki nalo subcutaneous'aʻaʻa, i ke kino poino mai ka nele o nā wikamina.
Ekolu degere - ka meaola ua loa depleted, ke kanaka nee hanu a me ka naau aayoaeuiinoe, hoemiia kino mahana a me ke koko,.
Eia hou, nāʻano o ka dystrophy i pu e mau symptoms: ke ahonui nui hauʻoli, oia hoemiia pahaʻaʻohe ikaika loa ka makemake, nee hiamoe, aia no he mau nawaliwali, he mau loli ma ke kino paona, gastrointestinal kāna hana, hoemiia e hoʻonele. Kēia kanaka, aole ia i ike i kona dystrophy symptoms kaʻaoʻaoʻai e i ka luhi a me ka stress.
Mea Maluna
Classify i ka maʻi, e like me ka mau ana hoʻohālike. Penei, e like me ke kumu o ka pathology mea congenital, a loaa, i ka prevalence o ke kaʻina - kūloko a mau, e like me ka hoonohonoho hou aʻe 'manao maopopo i ke kumuʻiʻo, momona, carbohydrate dystrophy. Kaumaha ma muli o kahi o ka kaʻina ua IIeEeAIEUIeXAIIUE, ka maʻi i e ke kelepona hele (parenchymal), extracellular (mesenchymal, stromal-vascular) a me ka hui.
Eia kekahi, noho kaʻawale? Ueo e like me malnutrition, a me ka gipostatura paratrofiya.
Malnutrition - o ka loa e like me ka ano o ka maʻi. He innate, a me ka loaa. Wehewehe aku ma ka nele o ke kino kaumaha i pili i ka ulu ana o ka hoʻomanawanui.
Paratrofii ka wā he mea kekahi i koe o ke kino kau paona ana, i ua kena ae la ma ka malnutrition a me ka pūnao.
Gipostatura hoikeia ma ka ia emi ana o ke kaupaonaʻana, a kiekie i kulike ai me na rula no i kekahi mau makahiki.
congenital dystrophy
Keia ano o ka hopena o ka ili kāna hana o ka pūnao o nā polokina, i ka momona, a me carbohydrates. A waiho ke kino i ke keiki i ka 'aʻole e loaʻa kekahi'ūhū, hoʻomāhuahua ia lŘlŘ ua pau hōʻuluʻulu manaʻo i nā huahana o ka pūnao i loko o nā'aʻaʻa a me nā loko. Nānā 'ole o ka IIeEeAIEUAA kaʻina hana, he mea mau poino i ka Central ko mākou hopohopo'ōnaehana'aʻaʻa, a hiki aku i ka make.
Ke kaumaha ma muli o ka wahi o ka hahai ana i ke ano o keia maʻi:
Cell (parenchymal) momoma degeneration
Kēia mea he pilikia i ia lŘlŘ ka wā i kekahi pūʻulu o aeee i nā kuleana no ka functioning o ke kino, he mea he metabolic kāna hana. I waena o nā kumumea i hoonaukiuki i ka hooulu ana o ka maʻi hiki ke kaulana hypoxia, maʻiʻaʻai, intoxication (o ka oi aku ka waiʻona), no kou kino a me ka wikamina deficiency.
Kekahi laʻana o ia ka pathology mea degeneration o ke akepaʻa. Ua hoike mai ai ia ia iho i loko o ka hikiʻole o ke akepaʻa keena, e hana i ko lakou mau oihana, e alakai ana i ka hope o ko lākou momoma'aʻaʻa. Kēia hiki i li nui a me ka cirrhosis.
Loa 'ole i huʻi a me kaʻawahia ano o ka maʻi. Ka moku'āina mua o ka kokololio kūpono 'ana, i ka hopena e e ake ole. ʻawahia ake dystrophy o ke kumu necrosis o kona keena.
Dystrophy naau - kekahi laʻana o ka ke kelepona hele momoma degeneration. Ma keia hihia i ka myocardial pōʻino, kona kuleana pili i ua hihia hoʻi. Heart piʻina ma ka nui, o ka myocardium i flabby, melemele, e ala mai ka endocardium holehole mai ai i aie i ka haoʻa palapala moʻopane o ka momona. Momoma degeneration o ka naau o ka hopena o ka hypoxia (oxygen deficiency), nā mea palahēhē e alakai i ka metabolic kāna hana, malnutrition.
Kumuʻiʻo parenchymal degeneration
Ua Ua maheleia i loko o kekahi mau ano:
- hyaline droplet degeneration wehewehe aku ma ka hoʻomāhuahua i loko o nā puʻupaʻa (kekahi manawa poino mai ake a me ka naau) kumuʻiʻo droplets. Kēia ia lŘlŘ ka wā o ka hakuʻala maʻi e like me mau myeloma, glomerulonephritis, amyloidosis. I ka maʻi, ua hunaia, a hiki aku i ka irreversible hopena.
- I hydropic (hydropic) dystrophy i loko o nā loko (akepaa, adrenal, myocardium, ili aeee) ia lŘlŘ huiwaina kumuʻiʻo wai droplets. Me ka oi o ia mau mea i loko o ka halepaahao aicieeaao hoʻonui degeneration (ka Kernel ua hoʻoikaika i ka periphery). I ka like ke ano e aʻe 'ana o ka wai-moana pūnao, hypoproteinemia, edema, infectious maʻi a me intoxications.
- Rogovaya dystrophy wehewehe aku ma ke kahua o ka horny waiwai, kahi e hiki ole ia, a me excessive hoʻomāhuahua o kahi mea e ia i loko o ka maʻamau dala (ʻili, kui). Hoonaukiuki aku i kekahi maʻi e beriberi, ili mā o? Acaeoey, mea hoʻomaʻi nā mea palahēhē, a me ka maʻi li nui.
Nail dystrophy hiki ia i ka hopena o nā mea palahēhē, ili maʻi, malfunctions gastrointestinal, endocrine a Central ko mākou hopohopo kahua. Eia hou, keia pathology ua i kekahi manawa pu e maʻi kekahi o ka mea'ōnaehana mānowai koko a me ka circulatory nenoai.
Nail dystrophy hiki e congenital a loaa. Ma congenital ano o ka maʻi i ia i piha i kaawale ai o, thinning a me ka hanaʻia naʻe o ke kui una honua. Loaa maʻi wehewehe aku ma gradual poe o ke kui papa, kui recess paha whitening. A, i ke kui papa i eʻoi aku convex, me ka transverse a me ka lonikū Groove. Ke kumu no ia o ka maʻi i e eczema, psoriasis, lichen planus, kui trauma.
Cornea degeneration loaʻa paha kekahi mau ano:
- Hyperkeratosis - ka oi o ka keratin ma luna o kaʻili.
- Congenital hyperkeratosis o kaʻili, a ua kapaia ichthyosis. ua uhiia i ke keiki i ka kino me ka manoanoa ili i kohu iʻa unahi.
- leukoplakia - ka maʻi i loko o a mucosal coarsen. Ua loaʻa i ke cervix, esophagus, waha, a no laila, ma luna o. D.
Parenchymal carbohydrate dystrophy
He ka hopena o ka launa ana o glycogen a me glycoproteins aʻe '. 'Aʻe' ana o glycogen pūnao ano o pathologies e like me mimikō paha glycogenosis.
Mamuli no o ka meaʻehaʻeha pūnao o glycoproteins ma aeee ke kumu hoʻomāhuahua mucoids a me mucins (mucus substance). D. kēia ka hana i loko o maʻi e like me rhinitis, gastritis, bronchitis, a no laila, ma luna o.
Extracellular (mesenchymal) dystrophy
Ua hoʻomōhala ana i loko o ka stroma (ma muli oia hoi o connective'aʻaʻa) kino. Ma keia hihia, ke kaʻina komo ai ka holoʻokoʻa'aʻaʻa a me ke koko moku. An kumu paha e retinal dystrophy. I ka maʻi i e kekahi congenital a loaa. Ma kānaka, ua hoʻemi pilikia makapō acuity, ia mea paakiki e ho okele i loko o ka pouli. Ma ke kahua hope o ka maʻi mea retinal poe maka a me pigmentalnaya dystrophy. Pinepine 'ole i loko o ke kaʻina hana, a me ka cornea.
corneal dystrophy wehewehe aku ma kona opacity, ua hoʻemi pilikia makapō acuity a me ka pā lonoaʻili. Ua hiki e hereditary a loaa. Ka maʻi progresses hoʻomaka koke, hoʻopio aku i nā maka, no laila ia mea mea nui 'eleuʻike.
Symptoms, a e hoʻolohe - keia kaʻeha a me ka haole kino ka waiʻona ma loko o ka maka, redness o ka maka, lua maka, makau o ka malamalama, ua hoʻemi hihio.
Secondary corneal dystrophy aicieeaao like me kaʻilihune o ka trauma. Ua hiki no hoi e ku pono i ka wikamina deficiency, hoolilo collagen maʻi, congenital glaucoma.
Muscular dystrophy - he ana i ua wehewehe aku e holumua ai Muscle nawaliwali, a me ka degeneration. Ka loa, he pono ole mau ano.
Duchenne muscular dystrophy
ʻano nui ia lŘlŘ i loko o nā keiki. Ma keia maʻi he mea he mahuahua bipi nāʻiʻo aie i ka momona hoʻomāhuahua a me ka hoʻonuiʻana o connective'aʻaʻa. Ka maʻi mea, ua hanahana loa, a ua ulu koke, i 12 makahiki ma ka hoʻomanawanui haalele i ka hiki e neʻe puni. Mau kanaka e ola hou ma mua o ka iwakālua o ka makahiki.
Steinert ka maʻi
He loa, he pono ole i loko o nā mākua. Ka maʻi hiki e ili, eia kahi mea akaka ma kekahi mau makahiki. Mawaena o ka mea mua symptoms i ke kaulana myotonia (ma hope o ke kua a na nāʻiʻo hoʻonānea loa lohi) a me ka nawaliwali o ka lehalehu t nāʻiʻo. E holumua ai degeneration o na nāʻiʻo mālie, e loli ai ka malimali nāʻiʻo a me ka naau Muscle.
I ka mesenchymal kumuʻiʻo dystrophy hiki hoomanawanui akepaa, hakuʻala, spleen a me adrenal glands o ke kanaka. Mua kanaka i Nyos i ka naau a me ka lolo.
Stromal vascular momoma degeneration - kēia hanana ola nodular hoʻokomo kālā ma luna o kanaka lala (e laʻa me, dercum maʻi). Ka maʻi hiki e kūloko a me ka mau, e hoʻonāukiuki aku i ka hoʻomāhuahua o ka waiwai, a me ko lakou poho.
Ka hopena o ka mesenchymal carbohydrate dystrophy hiki e edema, haanou ana paha e hoopalupalu ana o na ami, iwi a me cartilage o ke kanaka.
Lapaau a me ka Kāohi
Ma hope o 'oe i ka kiko'īʻike, ia mea e pono ke kakau iho koke ana i ka iapaau ana o keia maʻi ke kaumaha ma muli kona' ano a me ka oolea. Koho na nā kaʻa mokulele o ka iapaau ana, e kōkua i ka poʻe akamai, akā, no kekahi ano o ka dystrophy Pono e hooponopono kupono malama no ka poe mai, e hoʻopau i nā kumumea a i hoʻonāukiuki complications.
Ma waho aʻeo ia e mālama nei i walaʻauʻana lapaʻau mea i pono, e malama i ka? Eia o ka lā, a ua pili i ka ikaikaʻai, wahi a hiki i ke kauka, koi hou lewa, hydrotherapy, hoʻokō '.
No ka mea Kāohiʻana o kēia maʻi no lākou iho ola e e pono ua hoʻonānā, a hiki i hiki ke hoʻopau i nā hopena maikaʻi aʻe i hiki ke kāhea degeneration o kekahi ano keia ano.
Hoʻoikaika i ka ka'ōnaehana paleʻea'ōnaehana, e ai i ka naauao a me ka 'O ke kaulike, hookoikoi a me ka pale aku stress - keia, e ia i ka momona Kāohi mea,ʻaʻole wale nō kēia, akā, nui loa na maʻi.
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