Ola kino, Maʻi a me nā kūlana
Epidermal necrolysisʻawahia: symptoms, kumu, photo
Ka Uluwehi O Ke dermatological maʻi i hiki e ola-na olelo hooweliweli au, mai i hoʻomaka ai loa pinepine. Eia naʻe, ka mea e. Kekahi o kēia mau mea i manaoia e eʻawahia epidermal necrolysis. Kēia pathology He He pohihihi keia maʻi o ka ili i ke alakai i ka make.
He aha ka pathology?
ʻawahia epidermal necrolysis - he nui allergic pathology, i nā hualoaʻa ma ka poe o ka papakaukau, ahu iho o ka ili. He laila, e make, a ua waiho olohelohe ia i ke kino a hiki i ka intoxication ikaika. Me ka palapala hōʻoia no lapaʻau i ka poʻe kānaka hoʻokahi kānāwai sepsis a me ka make.
Bullous make o ka hou 'a i ke koiia mai e ole wale i kaʻili, akā, i mucous membranes. Ka maʻi Ua loa insidious. Ka mea e pepehi iho at ia e hiki maloko mucous membranes, a pinepine hiki aku ai i gastric kahe ana ke koko, naehana hanu ole, a hana paha a me nā 'aʻe' ana o ka meaola.
Pinepine e hoʻomōhala ana iʻawahia epidermal necrolysis ma hope o ka hoʻohana 'ana o kekahi mau ai'. Naʻe, i nā kumu i ia 'ē aʻe. Ka muli a me ka papa o ka maʻi mea kokoke ole ke kilokilo.
kumu o ka
Ka loa e like me ka kumu o ka maʻi o ka hoʻohana 'ana o kekahi mau' ano o ka ai '.
- Sulfonamides.
- Macrolides 'Erythromycin. "
- Penicillin ai '.
- Anticonvulsant: "lamotrigine", "carbamazepine", "Phenobarbital".
- Quinolones "Trovafloxacin".
- Protivovspalitelnye nonsteroidal ai ': "Indomethacin" "Ibuprofen," "piroxicam".
Ka mea hiki wale mai ka loa haʻahaʻa a me ka mea wale 1 ina no 1 miliona kanaka no ka makahiki. Pinepine e loli ai na wahine. Age mea i nui, e like me ka hapanui o nā hihia pathology ua malama ma hope o 55 makahiki.
Ma waho aʻeo i lalau i ka ai 'i ka muli necrolysis hiki lilo iho mailoko me ka staph maʻiʻaʻai.
Hiʻona o ka hooulu ana mai o ka maʻi
Epidermal necrolysisʻawahia Hawaiʻi koke lawa. Ina o ka maʻi i ka'ōnaehana paleʻea'ōnaehana hiki ole pono hoʻomaopopo a neutralize i kaʻawahia waiwai, i loko o kēia hihia o ka 'inikua lāʻau. An allergic naoh ka loa ikaika.
Ma keia hihia, i ka'ōnaehana paleʻea'ōnaehana pepehi i kaʻili, no ka mea, e hoomanao ia i ka'āina'ē kino. Penei rula hooponopono o ka hoʻopöʻino 'ia o nā polokina ua Nyos. Ka ili hoʻomaka e loaa toxins e alakai i ka nui intoxication. Inā manawa 'aʻole i hoʻomaka lapaau, i ke kanaka e make.
? Ueo a me IIeEeAIEUAA
ʻawahia epidermal necrolysis (symptoms o ka maʻi, ke i kūkākūkā mua) hiki ke hoʻolaha like penei:
- Idiopathic. Ua lŘlŘ kū kaʻawale, a me kona mea hiki ole ke hookupaaia.
- Kena ae la ma ka aoao o kekahi ai '.
- Ala aʻela ma lalo o ka aoao o ka staph maʻiʻaʻai. Kēiaʻano o ka pathology ua diagnosedʻano nui i loko o nā keiki. Ma keia hihia, i ka manawa kūpono o ka make ua hoʻokoe '.
- Hui a me nā maʻi.
Nā lesions Hiki ke 'akomi i ma ia wahi: na lākou kīkala, poohiwi, umauma, abdomen a me ka hope, ku una mucosa.
symptomatology o ka maʻi
ʻawahia epidermal necrolysis (Lyell ka maʻi pale) ua nō kāu wehewehe aku ma ka kēia symptoms:
- Huina kino 'aʻe' ana i hoike mai ai ia ia iho i loko o ka lilo o ka ikaika loa ka makemake, headache, mahuahua ka basal mahana. Pinepine ua hoonuiia ka hoailona o ka pathology makewai.
- Pain a discomfort i loko o ka mucous membranes. Eia naʻe, kā lākou mau pā lonoaʻili ua me ka nui loa mahuahua. No ka laʻana, oiai e ai ana i ka hoʻomanawanui Kahalaopuna eha ka wā moni 'ia.
- Ka hanana aʻulaʻula wahi lilelile, rashes a me blisters ma luna o kaʻili a me ka mucous membranes. Ma ka hapanui o na hihia ia e loli ai ma kahi o 30% o ke kino, aole hoi ia i ia mea nui.
- Exfoliation o na epidermis. Ma keia hihia, i kaʻili hoʻomaka e emi a hiki ma lalo o nawaliwali nano. Inā ka hoʻohuli ai i nā 'āpana o ka ili, e wehe i ke kahe ana ke koko ka eha, e hōʻike ma lalo iho.
- ʻaʻa puʻuwai insufficiency.
- Infectious kaʻina. Ka mea i kaʻili hiki ole Launch pono a me kanaka e hoʻopale ai mai ka waiū a hiki i pathogens. Ke kulana home 'ole i ka hopena i sepsis.
- Ma nā kahua o ka hoʻonaʻauao ma hope o ka maʻi ke kiai dehydration, tachycardia a me ka hypotension.
- Pain i loko o nā nāʻiʻo.
- Kuni, a me ka cough.
- Anorexia.
- Nausea a me ka luaʻi.
E i no i mucosal lesions hana oi koke ma mua o ka ili kāna hana. A laila, a laila ike ia ua ike pono no ina na kahua o ka hoʻonaʻauao loiloi mua oʻawahia epidermal necrolysis, he Hawaii photo no i mea ole no ka nawaliwali-naʻau, iki kekahi '.
lapaʻau 'Hiʻona
Inā 'oe i kekahi e hoʻohuoiʻia o kaʻawahia epidermal necrolysis, oe e nīnau i kou kauka koke. He pono e ka palena pauʻike, a me ka loa hoʻokolokolo pono, a me kēia mau:
- Fixation nāna hoopii. Noonoo ana ua hōʻailonaʻia ai i kēlā poʻe noʻonoʻoʻole,ʻeha ka waiʻona ma ke.
- Kaʻohiʻana hoʻomanawanui mōʻaukala. I ua, pono e loaʻa mai i ke kauka, ina loaa ia ia kekahi allergies e hoʻonui ai i ka hooulu ana o ka ia i ka luna 'naoh. He kupono e huli mai paha like pilikia ma ka hoʻomanawanui ka hoahanau.
- Mawaho ninaninau o ka hoʻomanawanui. Ma keia hihia, he dermatologist ua kokoke mai noonoo ana i ka ili kala like 'ole, i ke alo o lesions a me blisters ma ka mucousʻili lahilahi. Ke hoomanawanui i pane koke i kā lākou 'ia mea,ʻaʻole he kūpono.
- Ka Ikepili o ka nui o ke koko. He e i ka manawa e ike ai i ko ke kiekie pae o keʻokeʻo koko keena, Ua loaʻaʻiliahi koko keena, hoʻonui o ka erythrocyte sedimentation. Inā mau mea kiko'î e hele ma kela aoao o ka mea maʻamau palena, ke kahua Hōʻike i ke alo o ka li nui.
- Biochemical Ka Ikepili o ke koko. Inā like me ka hopena he mea he kiʻekiʻe kiʻekiʻe o ka bilirubin ka loa ka nui a me ka nui o ke kumuʻiʻo, i ka hoʻomanawanui i e pilikia me ka hakuʻala kuleana pili i.
- Urinalysis. Kēia noiʻi ua i pono e hooholo hakuʻala kuleana pili i. Inā he mea koko, alaila, ia mea he global e hopohopo nei i loko o ka mimi.
- Ana i ka ha awina o ka naau, ke koko, kiko'î.
ʻike, mea i pono e maopopo ma waena oʻawahia epidermal necrolysis nā maʻi: pemphigus, heʻulaʻula kuni, erythema, bullous impetigo, lichen planus.
Hiʻona o ka lapaʻau
Poe e ka maʻi pono a pau e hana. I ole ia, i ka hoʻomanawanui i kakali sepsis a me ka make. Inā ka hoʻomanawanui mea i hiki mai ka luna symptoms, a laila ka mea pono e hoopakele koke i ka haukapila ana. Inā ka maʻi pilikia, Ua hoonoho ia ka luahi ma ka mālama nui mālama, kahi 'inikua kookoo e hōʻike iā ia i kūpono malama.
Ke keʻena ma luna, i loaʻa maʻi, e e sterile, a e hoʻopau i ka manawa kūpono o ka hui 'ē nā mea palahēhē. Pathology iapaau ana komo ana o nā kumumea i triggered i ka maʻi.
Like no ka lāʻau Inc, laila, ma laila e hele mai i ke kōkua o nā corticosteroids a me antihistamines. Eia hou kekahi, ia e ke i hoʻonohonoho 'ia ma ka infusion Inc. Antibiotics Hiki ke hoʻohana wale i loko o ka hanana i ka hoʻomanawanui i ke ka piʻiʻana o ka haumāna maʻiʻaʻai.
pono no hoi e hanaʻawahia epidermal necrolysis (mea ia mea, e ike ano) me ke kōkua o kūloko kumu waiwai, e kōkua e hoihoi maʻamau ili e noho: anesthetics (painkillers), me ka hinu, antiseptics.
Eia hou, oe e pono e hoopili aku ai i na kumu mua o ka Inc:
- Ka mea, e hiki e ke koke ike mai i ke kino o ka lāʻau e ia mamua. Ua ia mea enemas.
- He kupono e lawe ai ', ka hoʻopukaʻana i ka hoihoi hou ia ana o ka maʻamau wai-paakai pūnao, e like me "Regidron".
- Kauka e hoakaka ia na laau no ka ake hoomalu, me ka maikai "Gepabene".
- Loaa ana konohiki e ho'ēmi i ke koko clotting.
He aha complications ke kānāwai?
Inā 'oe i diagnosed me kaʻawahia epidermal necrolysis, complications e komo:
- Ka hooulu ana o ka nui mea koʻohune maʻiʻaʻai.
- Loa dehydration, a hiki i ka hoʻomanawanui i ka make.
- I ka lilo ana o ka nui nui o ka ili. Inā he kanaka haalele i oi ma mua o ka hapalua o na epidermis, e hoomakaukauiaʻi kekahi make.
- Ka maloʻoʻana o kaʻili, i keʻano o ka scars ma luna ona, hoʻololi 'ia ma pigmentation.
- Maʻi ka'aʻaiawāʻana o ka mucous membranes.
Outlook
Inā maikaʻiʻole o ka pathology ia i ka hoʻomaka 'ana i ka manawa, o ka make ana, ke hiki aku i 70%. I ka lilo ana o ka nui loa o ka ili, e hana i ka hoʻomanawanui susceptible loa i nā mea palahēhē.
Manaʻoi hoʻokoe 'hoʻokumu pū Inc eʻaʻole kōkua wale kiʻi pohaku uinihepa, o ka maʻi, akā, e hoʻi i ka manawa e pale aku i na weliweli complications e like me na kahe ana ke koko, pōʻino i ka genitourinary'ōnaehana, i ka hikiʻole, e lawe ai, hakuʻala ole a me ka akepaʻa.
It E e kaulana i na keiki i ka make, mai ka maʻi, ua nui emi ma mua o nā mākua. Inā ka hoʻomanawanui ua hehi 60-makahiki milestone, ia ei loaa ole ia. Eia naʻe, pono lapaʻau hiki ke hoʻoikaika 'ana i kona kulana.
pathology Kāohi
Kekahi inoa no keia pathology likeʻawahia epidermal necrolysis - Lyell ka maʻi pale. Photos o ka maʻi mea maikaʻi,ʻaʻole e nānā impressionable kanaka. Kēia mea he luna 'pathology, i hiki ke käpae' ina e hahai i ke kāohi ana:
- Ka lapaʻauʻia E e lawe wale ina mea i koi 'ia e ke kauka.
- pono i ke hoʻomalu ina e 'ike i kekahi allergic reactions.
- Mea a ka pathology oe i e, e mai lawe hou aku 7 ai 'ka poʻe.
- Hana ole pakiko-staphylococcal a me ka hoʻoʻino ili maʻi.
- Pale hui 'ana me kekahi irritant e hiki i allergies.
Like no ka lapaʻau, laila mea a pau hilinaʻi nui ma luna o nā 'ano o ka meaola, a me ka hoʻomanawanui ka makemake, e hana me ke kue. E hoʻokaʻaʻike ola!
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