Ola kinoMaʻi a me nā kūlana

Fused wawae: 'ehaʻeha ka a me ka iapaau ana

No ke aha la kekahi mau keiki i fused manamana hanau ai? He aha ke ano o keia pathology, a ina paha oe e pakele no ia? Pane i kēia mau mea a me nā nīnau e pili ana i na deviations i hoike ia oe e aʻo mai i kēia 'atikala lako.

General 'ike e pili ana i ka pathology

Fused manamana - he congenital haʻahaʻa lala ulu. Kēia haiahū kūmau Ua wehewehe aku ma ka helehelena a piha kuʻi nukeliu o elua a oi manamanalima. I ka 'inikua hana, fused nā manamana wāwae i ka kūikawā inoa - syndactyly.

Me keia maʻi i loko o kānaka i ia i kuʻi nukeliu o ka poe ino a me ka underdeveloped manamana, a pono ke kino. Ke no o ka syndactyly mea iaea ooieoeiiaeuiiai a me ka mea hoʻonani mā o ka lalo lala.

Ke kao keiki me ka haiahū kūmau e mau e, kukakuka ae la i ka geneticist a me ka orthopedic surgeon. E hoʻonoho i ke 'ano o ka syndactyly, e halihaliia oia iwaho X-Ray o ka wāwae. Iapaau ana o keia kina ua hana wale ma keʻoki kino. Ma keia hihia, ua hoʻokaʻawaleʻia a me ka ea, a kina panina wā loa nō hoʻohana 'ia ka fused manamana elua.

kekahi mau 'ikepili helu

Syndactyly i kapaia'āno'ē kūpono 'ana o ka manamana lima, a mea i ka hopena o ka naha ana o ka pono o ke kaawale ana. Nō kāu, keia ia lŘlŘ i ka embryonic wā.

Fused na manamana wawae o kekahi keiki pēpē loaʻa me ke alapine (frequency) o 1 a hiki i 3000. Ua pono e kaulana ia syndactyly mea e pili ana i ka hapalua o nā mea a pau congenital anomalies. Oia wawae pathology paha e kekahi he kūʻokoʻa deflection, a ua hui ia me nā mā (e laʻa me, manamanalima hypoplasia, polydactyly a me ka polifalangiey, ectrodactyly, brachydactyly, brachioradialis synostosis, splitting o brushes, ulnar a kahahānai clubhand, a no laila, ma luna o.).

Kahi o 60% o nā keiki poe i loaa i ka fused manamana (Hawaii photo kina hōʻike i loko o kēia 'atikala), e pili congenital abnormalities ma ka musculoskeletal'ōnaehana (e like, pseudarthrosis, clubfoot,'āno'ē wawahi mea hoʻonoho, etc.).

kumu o ke kina

No ke aha la e na keiki hoʻomōhala ia he Hope, e like fused nā manamana wāwae? Nā kumu o kēia haiahū kūmau hiki e okoa. Poe akamai i manaʻo i loko o 20% o ka hihia i kēia mea ma muli o ke hereditary aʻe. Ma nā'ōlelo, a pau i ka hewa o ka autosomal Hoʻohaku kumu o ka'āina hoʻoili.

Inā he ohana mōʻaukala o ka syndactyly ua nalowale, ka mea pono ke ea i ka 'aʻe' ana o differentiation a me ke kahua o ka lalo lala o ka fetus ana i embryogenesis. IeAUPIIe, IAa IO kēia ka hana i ka wā ma laila mea i ka hopena o nā adverse aʻe.

A kina? Acaeoey oo?

No ke aha la mau wāwae fused manamana, a pehea e wehewehe ia ka lala ulu? unborn kamaiki wāwae uku pila ia lŘlŘ ma ka hebedoma 5th o intrauterine? acaeoey. Ka mea, ua i kēia manawa i loko o ka fetus e hoʻomōhala physiological syndactyly.

I ka wa e kaawale aku o ke kina mua i loko o ka hebedoma 7th o na manamana lima i hana ai. Keia mea aie a hiki i ka ulu o ka manamana lima kukuna e, na mea i ka hooulu ana o interdigital hakahaka. Inā ka ka ho'ēmiʻana o ka interdigital paia wawahiia, alaila, o ka phalanx ua i hookaawale, i mea, he mea syndactyly.

Hiki kumu'āno'ē ulu

Fused manamana, i ke keiki ke hana i kaʻawahia 'ole ma ke kino o ka wahine hapai. Ma ka hapanui o na hihia keia ia lŘlŘ i lawe ka lapaʻauʻia, kanakaʻona mau nā mea inu, e like me lakou malaila kālaikaiaola, hiʻona aoao, X-Ray irradiation a infectious maʻi (e laʻa me, maʻi palū, syphilis, tuberculosis, etc.).

Pinepine na kumu o ka hanau ana o ke keiki me ka syndactyly koe unclear.

Fused manamana - ka mea, ua pinepine malama hewa i loko o ka 'ole o ka chromosomal a aaiaoe syndromes.

Ma ke ala, ua nui kākaʻikahi i loaʻa i loko o kānaka lilo syndactyly. Nō kāu, e like me ka pathology aicieeaao ma hope o wāwae'ā (thermal ole Nine Inch).

Fused na manamana wawae - a 'o ia hoʻi kēia pathology?

He nui nā kanaka i 'Imi ke nânâ i pohihihi, ka mea, ua manaoio aku no lakou i keia pathology? Acaeoey? Ole pono. Ua Ua manaoio aku i kēiaʻano o ka mutation ka diabolō. Ua, fused manamanalima mea nō reminiscent o ka maiuu.

Eia naʻe, kauka i aku nei au ia mea malihini a me ka weliweli i loko o ia i ka wāwae mea e ulu ana. He mea pono i ka anomaly lala, mai i mea nō oluolu e pakele ana, o ka oi aku ma na kahua o ka hoʻonaʻauao kakahiaka o ke keiki ka ola.

Nolaila, mai hopohopo nui ina oe e fused nā manamana wāwae. He aha ke ano o ia 'O ia hoʻi, e hiki ke olelo wale i ke kauka,ʻaʻole he diabolō ipo lepili.

Mea Maluna o ka mā

Ma orthopedics syndactyly o Kuisa: e like me ka loa, i ke 'ano o ka ulana, e like me ka moku'āina o ka manamanalima.

Currently ike okoa ia:

  • iwi shape (wā iwi SPIKE ia lŘlŘ);
  • pahee'aʻaʻa palapala (kekahi manawa membranous a me ka ili).

kina Mea Maluna lōʻihi hilinaʻi nui ma ka helu a me ka lōʻihi o phalanges fused ulana.

E pili ana i ka moku'āina o fused manamana, ka syndactyly hiki e eiiieaena a me ka poe noonoo ole. Ma ka hope neo he mea he kuʻi nukeliu o ka maʻamau manamana lima, a me ka mea mua - me abnormalities o ka iwi, hui, tendon a ligament i hoʻomākaukauʻia.

aaiaoe ano

Syndactyly hoʻolaha a aaiaoe ano:

  • Ka muaʻano - zigodaktiliya. Ka helehelena a piha kuʻi nukeliu (membranous) 2nd a me ka 3rd manamananui. No hoi i alii iho la oia mai'ē aʻe webbed manamanalima.
  • Ka lua oʻano - sinpolidaktiliya. Kuʻi nukeliu o ka 4th a me ka 5th nā manamana wāwae me ka a pāpālua hoʻi o ka 5th. No keia pathology ua wehewehe aku ma: i ka 'aʻe' ana o ke kanaahoʻili kapuwaʻi a me hypoplasia o ka waena phalanx.
  • Ke kolu o kaʻano. ʻeluaʻaoʻao piha syndactyly o ka 4th a me ka 5th manamanalima. Ma keia hihia, i ka wāwae ua i loli.
  • Ka haʻano - syndactyly wehe. Fullʻeluaʻaoʻao cutaneous syndactyly lima. I ka Ia manawa, aole he holo ana me keia poho.
  • I ka lima o kaʻano. Merge metatarsal a metacarpal iwi. Ma ka lima mea oi, he pono ole 3-4 kuʻi nukeliu o manamana, a me nā wāwae - 2 a me 3.

kina symptoms

I ka syndactyly o nā wāwae i loko o ke keiki ua loa pinepine malama kuʻi nukeliu o ka 2nd a me ka 3rd nā manamana. Ma ka Ia undivided phalanx hiki e kekahi underdeveloped a ulu maʻamau. Ma kekahi mau hihia, he mea he emi ma ka helu o ka manamana lima, no ka mea, o ko lākou amniotic amputation.

Haʻalele keiki me syndactyly i loko o nā lima o nā keiki a me syndactyly o na wawae hoʻomōhala loa maʻamau. Ka mea, i ole pilikia me ka manaʻo o kekahi laulā huahelu o ka hana. Ma keia iaea ooieoeiiaeuiiai deficiency o ka wāwae, aole ia i hamper kā lākou mau haʻawina, e like me ka pono i aneane loa e hoʻohaiki ana i ke koho ana o ka wā e hiki mai oihana.

Pehea e diagnose?

Pehea e diagnose fused manamana (he hoailona ia ia kina, ua ho'ākāka 'ia ma luna pono)? Syndactyly ia akulla neonatologist koke ma hope o ka hānauʻana o ke keiki. Hou kilo o ke keiki ua lawe pediatric orthopedics aʻoki kino. E hookaawale ia chromosomal a me ka'ōewe abnormalities hiki e pili ana, a me ka geneticist.

I loko nō o ka mea e ia iʻike, ua i ma hope o ka pilikia makapō nana e möakäka hou i ke 'ano o ke kina, e like me ka hooulu ana o ka lapaʻau ka hoʻolālā, ia mea pono e hoʻomaka i ka mahele kila.

Radiography wāwae i loko o nā nā wānana waiwai e leie aku mākaukau i ke kiÿeleo i ka pa apŘ o ka iwi, hui ola, i ka lōʻihi, a me ka alo o ka iwi kuʻi nukeliu. E kuhikuhi i na ano o ke koko a me ka vascular aʻeo ka hoʻolele 'ana i ka manamana lima hana UZDG, reovasography, angiography a me ka pila nui ana wela.

maʻi lapaʻau

Ua loaʻa he laau fused nā manamana wāwae? Ana e hookaawale i ka phalanges - keia mea i ka wale hiki pāʻoihana. Naʻe, ka mea e e hoʻomaopopo i ka meaʻoki lāʻau lapaʻau kaʻina hana ua hoʻohana 'ia ka wā wale syndactyly o ka manamanalima. E pili ana i fused phalanges ana, alaila, o ka hana ua i hōʻike 'ia. Inā interferes ia abnormality me ka maʻamau hele, ua no i lawe mai i ka 'uao.

A pau ka hana e hele ma?

Terms a me ka hana ana iʻoki lāʻau lapaʻau 'uao i paa ma muli o ke' ano a me ke kinona o ke kina. Ke kumu o keia hana mea e hoʻopau i nā mea hoʻonani kina, e like me ka hoʻomaikaʻi i ka hana o ka wawae a me ka lima.

ʻO kaʻoi loa manawa no ka hana - i ka makahiki o ka 4-5 makahiki. Inā ua mālama i ke keiki pēpē syndactyly hopena, ke kākoʻo a ua lawe mai i loko o ka lua o ka hapalua o kona ola. Kēia 'ano ua ālai deformation o kiʻekiʻe manamana a me haoʻa i ka ulu ana o na phalanges.

ʻoki lāʻau lapaʻau hoʻokokoke mai

Iʻoki lāʻau lapaʻau ana ke kēia hoʻokokoke mai i ke hoʻohana:

  • kaawale o conjoined manamana lima me ka ili plasty me kūloko nā'aʻaʻa;
  • membranous kaawale ulana skinless Ka lula ea Ke;
  • fused kaawale manamana lima, a ua complemented ma ka hui hoʻohana o ka ili pakuiia auanei lakou me ka noa autografts a kūloko nā'aʻaʻa;
  • kaawale o conjoined manamana lima, a ua complemented e noa ili pakui polnosloynym a mahae ili pakuiia auanei lakou;
  • multistage 'ākeʻakeʻa a me tendon-Muscle, ili a me ka iwi pakuiia auanei lakou.

Ka postoperative manawa

Ma hope oʻoki kino e immobilize i ka hoʻokaʻawaleʻia manamana lima ma luna o ka lala hoʻokō i ka weheʻia puna splint. ? Aeiiaiaiaaia e komo ai ma ka liʻiliʻi loa 3-4 mahina.

Kahi o 15 mau lā ma hope o ka hana hoʻomaka i ka hoʻomanawanuiʻana ke ola. E hana i kēia, e hoʻohana i ka lomilomi lima a me na wawae, me ka Inc, phonophoresis me Lydasum, uila stimulation o nāʻiʻo o ka manamana lima, ozokerite, paraffin a me ka mud wahī mai.

I ka hopena o ka hana

Nā Papahana hoʻohana 'ia i loko o ke kālā noʻoki kino lapaʻau o syndactyly haawi maikai mea hoʻonani a me ka ooieoeiiaeuiuo hopena. Me ka 'eleu' uao ua pau hoihoi ole wale ka maʻamau 'ole, akā, i ka hana palaki o ka wāwae.

ʻoki kino, e wehe i syndactyly ua holomua ina ka hoʻomanawanuiʻaʻohe puakai scars a kīloi paʻewa deformity o na manamana, me he mea he piha huahelu o ke noi i ka interphalangeal hui (adduction, abduction, mailaila aku a me ka flexion), hoʻopaʻa hoʻi i ka papa (i loko o ka hihia o ka palaki), maikai pā lonoaʻili, a kūlohelohe ano na hakahaka ma waena o ka manamana.

Inā ka iapaau ana o ka syndactyly hoʻoholo,ʻaʻole e lawe mai, ka mea hiki i ka hopena maikaʻi 'ole ma ke ana a me ka ulu ana o ke keiki lala.

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