Pheochromocytoma - He aha ka mea? Pheochromocytoma: symptoms,ʻike, lapaʻau, kiʻi

Ka loa, e hoike aku o ka hanana o hikoko i loko o ke kino o ke kanaka, i benign? He ua lawa kumu no ka pili. A no ka pane ana i ia i ka mea pono e loa e hoʻokēʻai ai, ai ole maka i ka pilikia o complications, piʻi pū me ka nui loa. No keia kumu, ka mea i ano e aʻo i ka walaʻauʻana hoailona o ka helehelena o ka hikoko, o ka oi aku ina mākou e kamailio ana me ka nānā 'ano like pheochromocytoma. Mākou e ole noonoo i ka hopena o ke kuanaʻike ma luna o ka pilikia o ke kanaka laau a me nā 'ano like ki ina hana like. Ke kipa i ke kauka o ka loa ike loea pāʻoihana.

Pheochromocytoma - He aha ka mea?

E e maopopo i kēia manawa e like me kaʻeho mea malignant paha benign ano, haku o chromaffin keena, a paka catecholamines. Ua hiki paka nā biogenic amines a me peptides i nā norepinephrine a me ka dopamine.

Ma ka hapanui o na hihia (90%) o kēia 'ano o kaʻeho e hoʻomōhala ana i loko o ka adrenal medulla,ʻaʻole loa hoʻi kona helehelena paa ma aortic kino, na pelvis, abdominal a thoracic lua. Ka muli o ka pheochromocytoma i loko o ke poo a me ka'ā'ī māhele hiki e wahi ana i ka mahele o ka hewa.

I ka 10% o nā hihia o keia ano keia ano o kaʻeho mea he malignant extraadrenal IIeEeAIEUAA. Pela ka mea, o ka? Iecaianoaaiiie o dopamine. Like no ke kaʻina hana o ka metastasis ma ia pilikia, i kaʻeho keena hāʻule, i hookuu i loko o ka maʻiʻaʻai, akepaa, iwi, nāʻiʻo, a me ka 'āina' lymph aka wahi.

Ke kumu no ka muli a me ka ulu ana

Ua nui ua lohe no i kēia maʻi like pheochromocytoma. He aha ia mea, Eia naʻe,ʻaʻole pau ike. He nui ke kumu ia o ka pilikia ia lŘlŘ i loko o ke kanaka kino, e maopopo. A laila, i kekahi manawa, ka mea e e kaulana i ka ike hulina pane e pili ana i ke kumu o keia manawa. Akā, me ka hopena o nā haʻawina i ua i kekahi hopena a e pili ana i ka aaiaoe ano o ka pheochromocytoma.

Loa pinepine i ka maʻi i loko o ia lŘlŘ kanaka elemakule 25 a hiki i 50 makahiki. Holo nōhie, ua paa i ka hooulu ana o kēia 'ano o kaʻeho ma ka waenakonu-elemakule wahine. Inā mākou e kamailio e pili ana i na keiki, e like me kaʻike, ua oi aku ia i loko o nā keikikāne. Akā, me ka mau, pheochromocytomaʻeho - he kŘpa a ke nānā kŰia.

Pela no ma kahi o 10% o ka huina helu o na pilikia pili i kaʻohana ano. Kēia 'o ia hoʻi i kēiaʻano o kaʻeho ua i hiki mai ma ka liʻiliʻi loa ma kekahi o na makua o ka hoʻomanawanui.

Hoomau ana i ka nana i ka kumu o keia ano keia ano o ka maʻi, e pono ke kūʻai 'ana i kumumanaʻo i ka mea hiki ia i kekahi o na eiiiiiaiou o ka maʻi pale o mau endocrine neoplasia (' ano 2a a me ka 2B). Pheochromocytoma paa i ka 1% o nā mea maʻi diagnosed me diastolic ke koko.

symptomatology

Ma ka like ana o ka hikoko me pheochromocytoma, symptoms, ʻike, a me ka hana i palaka kī 'ike, i ae, e noonoo i ke kumuhana, mai kekahi pana pua. Akā, e hoʻomaka ana me na hoikeana o ka maʻi. Symptomatology Ua like a me ka pinepine nana e like me ka mea pepehi weliweli emi ola pilikia.

Oe E hoʻomaka ana me ka mea i loaʻa i kekahi symptom i mea paa ma na maʻi like pheochromocytoma. Hypertension - kēia mau mea kekahi o na hoikeana o kaʻeho ma ka nīnau. Ua hiki ke lawe wahi i loko o ka hale lio a me ka krizovoe ke ano. I ka wā o kaʻeho e hoʻomōhala ai ma catecholamine hypertensive ka hoʻoponopono ulia, ke koko, piʻi pū hala loa ia. Akā, ma ka mezhkrizovy au BP e noho kūpono kiʻekiʻe paha ia i loko o ka maʻamau laulā. Kākau hihia wā pheochromocytoma aku me ka ikaika kiʻekiʻe puʻe, akā, me ka crises.

No ka 'ike hou aku e pili ana i hahau ana

Ka mea, i hoohalike, e hoʻolohe i ka mea ana me ia i ka pilikia e like me pheochromocytoma ulia (hypertension) ua pinepine pu ma ka gastrointestinal, mea'ōnaehana mānowai koko, metabolic a me ka neuro-psychiatric kāna hana. Olelo ana e pili ana i ka hooulu ana o ka ia o ka moku'āina, ka mea e e kaulana ia mea, ua wehewehe aku ma ka kēia symptoms: headache, tremor, uunu nui, restlessness, haikea ili, ka luaʻi, cramps a me sweating. Aia paha ia i ka 'aʻe' ana o pāpana, tachycardia a me ka naau eha.

I ka diagnosed me ka pheochromocytoma, hypertensive ulia e hoʻonāukiuki ka luaʻi, nausea a me ka maloo waha. Akā, i kēia mau hoʻololi i loko o ke ahonui o ka moku'āina o ke ola kino ua e mau loa ana me kaupalena '. Me ka hikoko pinepine hoʻololi moku'āina o ke koko. Mākou e kamaʻilio e pili ana i na complications me lymphocytosis, hyperglycemia, leukocytosis, a me ka eosinophilia.

Crease hiki i ka hope, mai kekahi mau minuke i ka hola a oi. A hiki i keia moku'āina ano o kona unexpected shutdown. Emi i loko o ke koko, i ia lŘlŘ hoʻomaka koke, no laila, ua hiki malaila i ka pilikia o ka hypotension. E like me ka hoʻonāukiukiʻana symptoms ia aʻe paha e hoʻokō ', e hali ana mai hohonu palpation o ka abdomen, pono o ka waiʻona, a ai', hypothermia a overheating,ʻoi ka neʻe 'ana,' ehaʻeha o ka haunaele a me ka 'ē aʻe.

ka oi aku ho'āhewa wale

Kāʻili 'kamaʻilioʻana i ka i kaʻokoʻa alapine (frequency). Ka mea hiki ke manao 10 a hiki i 15 manawa i ka lā paha i kekahi manawa, i ka mahina. Inā ka hoouka kaua o ka loa ka hoʻoponopono ulia ma ka pheochromocytoma, a laila ka mea i pono, e kamailio e pili ana i ka mea maoli pilikia o ka hahauʻana, kahe ana ke koko i loko o ka retina,ʻaʻa puʻuwai e hemahema, myocardial infarction, dissecting aneurysm o ka aorta, pulmonary edema, a me kekahi poe e ae, ka loa loa complication o keia kulana mea he catecholamine kŰia hoike mai ai ia ia iho ma ka uncontrollable hemodynamics. Mākou e kamaʻilio e pili ana i hoʻololi hypo- a me ka hypertension, me indiscriminate ma ka ano, aʻaʻole hiki ke ee a.

No laila, pheochromocytoma - He aha ka mea? E noonoo pono i kona hoike ana, e ke uku hoʻolohe i ka hapai na wahine, no ka mea, ka mea, ke ano o kaʻeho hiki masquerade like eclampsia, mālama '-eclampsia a me ka toxaemia. Ke no o ia symptoms i lilo adverse hanau nā haumāna.

Hiki a me ka pilina paʻa kinona o kaʻeho, ma i ke koko, Ua kūpono kiʻekiʻe. Ma keia wahi, pinepine kākau hou i loko o nā puʻupaʻa, ke fundus, a me ka myocardium. Ua mea no hoi e hiki koke loli ma ka naʻau i loko, headache, luhi a me ka irritability. Kekahi o ka 10 nā mea maʻi i mimikō ulu.

Aia i nā maʻi i mea pinepine pili me ka pheochromocytoma. Ua mea e pili ana i Raynaud ka maʻi pale, gallstone maʻi, maʻi pale Cushing, neurofibromatosis, a me kekahi poe e ae. I ka hanana e ulu i ka malignantʻeho,ʻeha i loko o ka opu, he mea metastasis i mamao nā loko, a me ka kokololio kaumaha me keia poho.

I Kekahi Mau lapaʻau hoike ana

Aia hoi he mau hiʻona o ka maʻi, a hiki alakai i kekahi complications. Ua mea e pili ana i ke kēia keʻano o ka hanaʻana.

• Children diagnosed me ka pheochromocytoma i loko o ka hapanui o na hihia e hoʻomōhala ana i hypertension. A hapaha o ka hoʻomanawanui iki mai ma kekahi kakahiaka nui elemakule Ua paʻa polydipsia, polyuria, a me ke kāʻili 'ana. Kekahi complication e hiki i pheochromocytoma i keiki - he slowdown i loko o ka ulu. Eia hoʻi, ka mea, ua ma he kakahiaka nui makahiki me kaʻike,ʻo ia ia iho i manao ai i ka ikaika kaumaha poho, sweating, nausea a me ka luaʻi, pilikia makapō ka haunaele, a me ka vasomotor haunaele.
• Women me ka pheochromocytoma e 'ike mea hōʻemi o ke ola ma muli o ia i ka iʻa. Hapai wahine paha e ka Mohai o eclampsia a me ka mālama '-eclampsia.
• Ma na wahi a kaʻeho ua aia e hiki mai ana ma ka paia o ka bladder, urination i e pili me ke kāʻili 'ana. Aia mea no hoi he pilikia o painless hematuria, mahuahua ke koko, headache, nausea a me palpitations.

ki ina hana like o kaʻike,

I mea e kuhikuhi i ke ano o ka hoʻomanawanui me kēia maʻi e like me pheochromocytoma, moku'āina Ka Ikepili i ke kino e e hoʻomōhala kuhikuhi ma ka kēia symptoms: mae o ka ili o ka maka, a me ka waiū, mahuahua ke koko, tachycardia, orthostatic hypotension.

Pela ia mea e pono ia e akahele palpation o ka hoao i loko o ka hihia o ka hikoko i loko o ka'ā'ī, a me abdomen. ʻO lalo laina mea i na hana hiki i ka hooulu ana o ka catecholamine hoʻoponopono ulia.

Nō hoʻi, kiʻekiʻe-kbpsʻike, i loko o ia mau hikoko e komo i ka makaikai ana i ka ophthalmologist. Keia ano hiki ke wahi i ka mea i aneane 40% o ka poʻe pilikia mai hypertension, ua 'akomi i hypertensive retinopathy, a me ka loli iki ana oolea.

Aia i biochemical nā koi a no kaʻike, o ka pheochromocytoma, he Hawaii photo no i ae mai, e maopopo i ke koʻikoʻio o ke kulana. No laila mākou e kamaʻilio e pili ana i ka māhuahua pae o catecholamines i loko o ke koko, mimi, ke koko monakō koko a me ka chromogranin-A i loko o ke koko lāʻau lapaʻau. I kekahi manawa mea paha e piliʻikepili ma mahuahua i loko o ka lehulehu o parathyroid hōmona, cortisol, kalipuna, phosphorus, calcitonin, a me nā kumu mua.

Ma lalo o kekahi mau kumu o nā mea maʻi ua lawe mai palena pauʻike, o ka hikoko. Mākou e kamaʻilio e pili ana i maʻi e like me psychosis, neurosis, hypertension, hyperthyroidism, paroxysmal tachycardia, ʻapu kōheoheoʻana a me ka hahaki pinepine i loko o ka CNS.

Ma ka hoomaopopo ana i ke 'ano o kaʻeho, a me ka degere o kona? Acaeoey hiki ke hoʻohana' MRI a me HI, e like me ka hoʻopaʻa 'ana o ka hoʻomanawanui ka cardiac haʻawina. Inā pheochromocytoma ua diagnosed, symptoms,ʻike, a me ka lapaʻau - e, ao ke ano i mea mākaukau pili me ka hikoko o nāʻano likeʻole ia i ka 'eleu ka loaʻaʻana o nā pilikia a me ke ake lapaau i ke ki i ka maikaʻi hope o ka hana me ka hoʻomanawanui.

Pehea e hana

Aia i kekahi mau ano o ka ole ma kaʻeho like malignant a me ka ole i ka hoʻoweliweli '. Ma ka hapanui o hoopii,ʻoki kino e ia i ka loa ka naauao olelo hooholo, ina mea i ike pheochromocytoma. Removal e e oi loa i pili i ka hihia o kaʻeho ma ka adrenal gland.

Akā, hiki mai ai ka hewa aie i ka poe ilihune ke ano o ka naau, ipu koko a me ka kiʻekiʻe ke koko. Komo 'surgeon ka wā e like me ke ano o loa undesirable paha hoi unacceptable. Ua huli mai oi ma luna o ka hopena o ia kaʻeho me pheochromocytoma. ua hoemi i ka lāʻau lapaʻau Inc, IeAUPIIe, IAa IO lawe i kekahi mau lā.

Ka hoʻohana a okoa ai 'i kaʻeho neutralization hoʻohuʻu ia me ke ahonui o, e ia ma ka moe, a me ka lawe hapa-noho kūlana. E lawe mai i ka maʻamau ke koko, kauka i hoakaka ia Alpha-blockers. More ua hōʻike hewa, ka mea, ke ai 'e like me "Tropafen" a me "phenoxybenzamine." Inā ka hoʻomanawanui ua paa hypertensive ka hoʻoponopono ulia, topical hooponopono makemake e "phentolamine" "paʻakai nitroprusside" a me ka 'ē aʻe like ai'. He aha ka mea nui o ka mea i iloko o ka mālama '-iapaau mea pono e hoola i ka hoʻomanawanui mai dehydration.

E ho ohana iʻoki kino

Inā pheochromocytoma Ua 'akomi i, i ka lapaau ma ka scalpel ua wae me ka pili ana i ka mea mau kaʻina kaʻeho. Ka loa, he pono ole i ka hui, transbryushinny, extraperitoneal a me ka transthoracic ki ina hana like.

I ka hanana i ka wahine paha,ʻeho i ike ma hope o ka ninaninau, ka prognosis meʻoki lāʻau lapaʻau lapaʻau e e pono. O ka ihu, malaila e e relapses, akā, e hoike mai ai ia lakou iho wale nō i loko o 13-15% o ka hihia.

Akā, i ka wa e mau hikoko, i ke kulana mea me ka nui loa hou huikau. Ka loa kupono pāʻoihana mea e wehe a pau hikoko, akā, me ka pilikia moe i loko o ka mea ana i ka pahiki o ka holomua hoʻokūkū mea he haʻahaʻa. Ia mea no keia mea, i loko o ka hihia o mau pheochromocytomasʻoki kino ua lawe mai i loko o kekahi mau kahua o ka hoʻonaʻauao. Ma kekahi wahi, i hiki, wale i kaʻeho ua wehe hapa 'ia'.

Like no ka hiʻona o ka hana, i loko o ka papa o kona manaʻo e pili wale nō laparotomy ke kula. Ua wehewehe i kēia kokoke loa i kahi kiʻekiʻe-kamepiula extraadrenalʻeho IIeEeAIEUAA. Ua mea i ke kumukuai o ka ike ana i ka mana o ka hemodynamic (ke koko, a me ka Central venous puʻe) ua paʻa ma ka 'uao.

Ma ka hapanui o na hihia ma hope o wehe pheochromocytoma, ke koko, emi. Inā ia he naoh o ka meaola mea i ike, alaila, he mea na kumu e manao i ka mea o ke kahua o ectopicʻeho'aʻaʻa.

Inā i loaʻa i loko o pheochromocytoma hapai wahine, mua i ka noaaeeecaoee o ke koko,, a laila, hana i ka cesarean pauku, a me abortion, a wale laila, e lawe aku oe i kaʻeho no ia.

I Ina o diagnosing he malignant pheochromocytoma, i i loaa i ka puunaue ana o metastases chemotherapy ( "Dacarbazine" "Vincristine", "Cyclophosphamide").

I mau, ina i 'akomi i kaʻeho ma ka kakahiaka nui ke kahua, a me ka hoʻomanawanui mea alakaʻi mākaukau, no ka lapaʻau, ka mea hiki wale mai i ka lanakila i kēia pilikia i loa kiʻekiʻe.

He aha kumumea hiki ke hoakakaia like triggers

Me ka hooulu ana o ka hikoko i loko o ke kino o mau i ka pilikia o ka hoʻonāukiuki ka hoouka. He nolaila, nui ia e Ike e no laua, a i alakai i ka aggravation o ka moku'āina. He He ninau e pili ana i moe ke keakea ole, i ke kino kulou loli, hyperventilation,ʻolu i na naau oʻu neʻe, physical haawe, ka noʻonoʻo 'excitation a me ka puʻe i ke kahi o IIeEeAIEUIeXAIIUEʻeho. Inā 'oe i diagnosed me pheochromocytoma, e ole e hoʻomau ana i ka waiʻona, pakahi aku la ia i ka waina a me ka pia, e like me kaʻai i ka waiū.

Aia ua, ua hoʻopaʻa pepa paʻi kiʻi i hihia i ka wa a ka ino i hoomaka ai ma hope o ka loaa ana nicotine i, tricyclic antidepressants, phenothiazine nā mea loaʻa a me ka Hoʻokolohua-blockers.

hualoaʻa

Pēlā mākou i ka theme like o "Pheochromocytoma" Ua hoʻi. He aha ka mea, nana aku la makou i ka loa au mamuli. Ua koe e e ka ahuwale Ka Hopena: ka pilikia mea, ua nui e pono ia naka. Ma na hoailona mua e hoohalike ai i ka symptoms o pheochromocytoma, ia mea pono, e nīnau aku i ke kauka, e diagnosed a hoʻomaka lapaau.