Amyloidosis - He aha ka mea? Amyloidosis: mea, lalau mai, symptoms, lapaʻau,ʻike,

Amyloidosis - He aha ka mea? He He maʻi o ke kumuʻiʻo pūnao ma i ke kahua a me ka palapala moʻopane i loko o kekahi mau nā'aʻaʻa a me nā loko o kekahi mau 'kumuʻiʻo-polysaccharide substance - amyloid.

Ka hooulu ana o ka maʻi

Ulu ka amyloidosis (mea ia mea - mākou i ike mua) ma ka 'aʻe' ana o kumuʻiʻo hoʻololi kemikala i loko o ka reticuloendothelial nenoaiu. ʻO wai koko mea he hoʻomāhuahua o'āno'ē nā polokina. Mau nā polokina meaʻano nui ka hoʻoponopono 'antigens, a i ka allergy like me ke kahua o ka autoantibodies.

A laila, i kēia mau nā mea'aʻaʻa i na antigens, a pane koke grubodispersionnye nā polokina precipitate. Mai ke kahua o ka amyloid. Keia mea ua waiho ma luna o ka moku paia a me kekahi mau nā loko. Ke kiʻekiʻe o loaa, amyloid hele aku ai i ka make ana o ke kino.

Ano o ka amyloidosis. kumu

He nui na ano o ka amyloidosis. Nā kumu o ka maʻi mea pololei e kaukaʻi ma ka 'ano o ka amyloidosis. He aha ka mea? Mea Maluna ua lawe mai e like me ke kumu o kumuʻiʻo, a iloko o ka amyloid fibrils. Aia ma lalo mau manao o ka maʻi.

1. Helu amyloidosis (AL-amyloidosis). Ka wā kona hooulu ana i ka wai koko ikea'āno'ē immunoglobulin malamalama kaula hao, i mea hiki ke noho i mau nā'aʻaʻa o ke kino. Pela no hoʻololi i wai koko keena o mau myeloma, Waldenström ka macroglobulinemia, monoclonal hypergammaglobulinemia.
2. Secondary amyloidosis (AA-amyloidosis). Ma keia hihia, he mea excessive hoʻokuʻu o ke akepaʻa kumuʻiʻo Alpha-globulin. He huʻi pae kumuʻiʻo i ua synthesized i ka maʻi li nui. He mea hiki i ka maʻi likeʻole, e like me rheumatoid arthritis, malaria, bronchiectasis, osteomyelitis, maʻi lēpera, tuberculosis.
3. Family amyloidosis (AF-amyloidosis). He He hereditary maʻi me ka autosomal recessive hooilina. Ua ua i kapa Kaiwaenahonua kuni intermittent paha paroxysmal poliserozita ohana. Kāheaʻia i kēia maʻi ho'āhewa wale o ke kuni, ka hanana o abdominal eha, ili rashes, arthritis, a me ka pleurisy.
4. Ke dialysis amyloidosis (Ah-amyloidosis). Ua ua pili i ka mea i ke kumuʻiʻo Hoʻokolohua-2 microglobulin MHC i ola kanaka ua hoolilo o ma nā puʻupaʻa, a me ka mea, ua 'aʻole i wae ma ka hemodialysis, a no laila, o kona hoʻomāhuahua i loko o ke kino.
5. AE-amyloidosis. Ua ua ulu kekahi ano o ka maʻi 'aʻai, e like me thyroid.
6. Senile amyloidosis.

symptoms

A hiki i kaʻike, o "Amyloidosis" symptoms hilinaʻi ma ka IIeEeAIEUAA o hoʻokomo kālā. Me ka make o ka gastrointestinal'āpana hiki e malama hoonee aku elelo, hoʻopōʻino moni 'ia hana, constipation paha diarrhea. Aia paha eʻeho-amyloid hoʻokomo kālā i loko o ka naʻau liʻiliʻi a me ka'ōpū.

amyloidosis o ka naʻau liʻiliʻi pu ma ka manao o ka ehaeha a me ka discomfort i e mehana abdominal eha. Inā luku aku la ma na pancreas, haawi i ka ia symptoms me ka pancreatitis nei. Inā ake eha malama i kona mea ulu, nausea, belching, ka luaʻi, ke kāʻili 'ana, jaundice.

Amyloidosis naehana ikeia like penei:

• paa ka leo i ka leo;
• symptoms o bronchitis;
• pulmonaryʻeho amyloidosis.

ʻO kēia symptoms kānāwai i loko o amyloidosis o ka'emi'ōnaehana:

• tingling paha e aa ana ka waiʻona ma ka lala, numbness (ʻike ākea polyneuropathy);
• headache, pōniuniu;
• sphincter kāna hana (urinary incontinence, fecal).

Amyloidosis - He aha ia mea, kona kumu a me nā symptoms mākou i nānā '. Ano, ua nana i ana i ka maʻi ua diagnosed a me ka hakakā o lapaau nei.

lapaʻau '

Ma ia he maʻi like amyloidosis,ʻike, ka luna '. I hoonoho ia ma ke keʻena hoʻokolohua a me ka lako e noiʻi.

Ma keʻena hoʻokolohua haʻawina, he nui ka loiloi 'ia o ke koko malama mahuahua i loko o ESR, leukocytes a ua hoʻemi platelet helu. Ke mau Ikepili o ka mimi kumuʻiʻo mea i loaʻa i loko o ka sediment - nā paukūʻolokaʻa, leukocytes a me erythrocytes. I coprogram hoike nui dala o ka pia, a me ka momona Muscle olona. Ma ke koko biochemistry ma lesions o ke akepaʻa hoikeia mai ka loa naʻokoko, bilirubin,'ākilikai phosphatase.

Ma iniiaiie amyloidosis ma ka mimi a me ke koko wai koko hōʻike he kiʻekiʻe ka maʻiʻo o ka amyloid. Ka wā 'aʻole ka haumāna i ke keʻena hoʻokolohua ho'āʻo ma hōʻike hoailona o ka maʻi li nui.

Kekahi hana 'ē aʻe PalekanaEND_LINK ana:

• X-Ray keia hookolokolo ana;
• echocardiography (i loko o ka hihia o ka kēia naʻau hoouka);
• ooieoeiiaeuiuo assays me ka make;
• biopsy kino.

lapaʻau

A i ka maʻi ua lawe mai-hoʻomanawanui lapaau. Amyloidosis, ma a he mea nui keia, e like me maʻiʻaʻa puʻuwai ka hoʻokō 'ole' ole loa naau hoʻokō 'ole' ia i loko o ka haukapila.

Ma iniiaiie amyloidosis initially kohoia ai 'e like me "Chloroquine" "Melphalan" "prednisolone", "Colchicine".

I ka haumāna amyloidosis hana i ka nń ku maʻi, e laʻa me, osteomyelitis, tuberculosis, pleural empyema listen'ōlelo., Pinepine ke kino a pau symptoms o amyloidosis ma hope daimonio.

Inā ka maʻi e hoʻomōhala ana i like me ka hopena o ka hakuʻala hemodialysis, laila, ua hoolilo ia ke hoomanawanui i ka peritoneal dialysis.

Ma ka hihia o ka diarrhea binders hoʻohana laau lapaau, e like me "bismuth subnitrate," a adsorbing hope paha.

Ka mea, e hoi e symptomatic lapaʻau.

• hoomakaukau hoemi puʻe;
• nā wikamina, diuretics;
• wai koko transfusions, etc.

A eia hoi, e hiki ke hoopili aʻoki lāʻau lapaʻau lapaʻau. amyloidosis o ka spleen i hee ma hope o ka wehe 'ana o ka hui,. Ma ka hapanui o na hihia, ua hiki aku i ka hana hou i loko o keʻano o nā mea maʻi, a emi ke kahua o ka amyloid.

ka ai

Amyloidosis pono a eia iʻai. Me ka hooulu ana o ka maʻi hakuʻala maʻi e kali paakaiʻai ana, a me ka kumuʻiʻo ai e like me ka ai, ka iʻa, hua. Inā ulu maʻi naau e hemahema, e ke hoʻokoe 'ia mai i kaʻai o ka paakai, paka a me pickledʻai.

cardiac amyloidosis

Ua maʻi ua i kapa amyloid cardiomyopathy. Me kona hooulu ana o ka amyloid palapala moʻopane ke hana ma ka myocarditis, pericarditis, endocarditis, a ma luna o nā paia o ka aorta a me ka coronary arteries. Ke kumu no keia naau maʻi paha e iniiaiie amyloidosis, nā haumāna a me ka 'ohana. Pinepine amyloidosis o ka naau - ka mea, o ka noho kaʻawaleʻana mai ole, a me ka mea, ua ulu i loko o laua me ka amyloidosis o ke akemāmā, hakuʻala, liʻiliʻi 'ole spleen.

Symptoms o cardiac amyloidosis

Pinepine na symptoms o keia maʻi mea like i hypertrophic cardiomyopathy a coronary naʻau maʻi. Ma ka loiloi mua ke kahua, symptoms i vague. I ka mahina irritability a me ka luhi, kekahi kaupaona lilo, haanou ana o nā'aʻaʻa a me ka pōniuniu.

Kaʻoi mea hōʻemi ana ia lŘlŘ ma hope o kekahi stress a naehana maʻiʻaʻai. Ma hope iho o ia maʻamau ikea naau eha type angina pectoris, arrhythmia, haʻi edema, dyspnea, ake hoʻonui. Ke koko, ua ana i kuʻu iho.

Ka maʻi progresses hoʻomaka koke, a me kona kiʻiona hiʻona o ka ia'ku (ia'ku) i ka Inc. I loa hoopii, hoʻomanawanui iki mai i ka mahina ascites (hoʻomāhuahua o ka loli ma ka abdominal lua) a pericardial effusion. Aie i ka amyloid infiltrates hoʻomōhala sinus bradycardia. Kēia hiki alakai i ka manawa e make.

Outlook

Ma ka naau amyloidosis ilihune prognosis. Congestive naau ole i loko o kēia maʻi progresses steadily a me ka make, Ua imminent. Ma Rusia ka mea,ʻaʻohe hana kūikawā-oaio? A Hana me kēia pukana.