Ola kinoMaʻi a me nā kūlana

Aortoarteriit nonspecific: Symptoms a me ka lapaʻau Nā Papahana

Currently, aia nō he nui helu o ka maʻi i mea e loli i likeʻole nā loko, a kino nenoai. Akā, i waena o lākou aia no kekahi poe makemake, e koho i kekahi wahine. Ma kēia 'atikala, loaa kaʻike mākou i kekahi o kēia mau maʻi - o aortoarteriit nonspecific, a pinepine poino mai o ka wahine ke keka, a me ka opiopio makua. Ka loa mau diagnosed maʻi i loko o hawaiian'āina. E ka nana aku i kona kumu, symptoms, a me ka poʻe kūkākūkā, ina he mea hiki, e Makuakane me keia pathology.

Ke ae pā o ka maʻi

Nonspecific aortoarteriit mea he rheumatic maʻi i loko o a he mea lilo loko ili o arteries a me ko lakou mau lala. Inā ka hoʻoʻino kaʻina progresses, ka vascular pā ai hanaʻia naʻe, ala apuupuu Muscle, ahu iho hoʻomaka e wāwahi ai, a UAIAaIN e connective'aʻaʻa, a me ke koko moku hou granulomas oia hoi o ka nui halepaahao.

E like me ka hopena o ia keʻano o ka hanaʻana moku koko e hoÿonui ai a me ka bulge e hoʻomōhala ana i ka aneurysm. Inā i ke kaʻina hana 'Aʻole i pau, a laila ka mea welau a ka a maloo aku o na laholio olona, o ala apuupuu Muscle'aʻaʻa. Hoʻomaka e ae aku i ka nā loko, a nā'aʻaʻa aie i ka hihia hoʻi ke koko pele. Ma ka hoʻonohonoho 'oihana o ka Mea Maluna o ka maʻi, kēlā maʻi i kona iho kivila, i ke koe nonspecific aortoarteriit. ICD M31.4 i hookoia aku la ia ia i ka code (aortic e pio maʻi pale).

Nā kumu o ka maʻi

No laila, hiki, na kumu e hoonaukiuki i ka hooulu ana o keia maʻi, a i ole, ua hoʻokūpaʻa. Ka hapanui o noiʻi ka poe i komo i loko o kēia pukana, mea o ka manao ana ia mea i ka hope kūlana ma keia pâʻani 'o ia ma nā mea palahēhē, na mea e alakai i ka immunodeficiency Hawaii. Oia ka manao i hana ma muli o ia ka mea e ole-ilepili aortoarteriit pinepine pili i loohia, a i ka nānā 'ana ma luna o kāna hana'ōnaehana paleʻea.

Currently, aia no he pūʻulu o nā kānakaʻepekema, ka poe i hāliu mai i ko i ka pono imua i ke kumumanaʻo o autoimmune maʻi? Acaeoey. Maopopo no ia mea ka ka loaʻaʻana o nā mea maʻi me ka wai koko antiaortalnyh nā mea'aʻaʻa.

Mākou ke i aku nei au i keʻano papa hana o autoimmune maʻi hiki ke hookupaa iho la ia, akā, ina paha ia mea iniiaiie, a mea i pane i ka hoʻoʻino kaʻina - e olelo ai mamao paʻakikī.

Mea Maluna o ka maʻi

Aortoarteriit nonspecific hiki e keʻano kaumaha ma muli o ka maikaʻiʻole ia ma 'āpana.

  1. Ka muaʻano - ma keia hihia pepehi wale aortic e pio mai a me ka mea uuku lālā i ana mai ia.
  2. Ma ka lua o ka type i hoʻohuli ai i nā artery i loko o ka thoracic a me ka abdominal.
  3. Ke kolu oʻano - loli aortic e pio mai me ka thoracic a me ka abdominal.
  4. Ha, ua wehewehe aku ma lesions o ka pulmonary artery.

No ka mea noaia paha hoʻomōhala nonspecific aortoarteriit (Takayasu ka maʻi), kīnā o ke kino Hoʻoweliweli 'o ia maʻi loa pinepine. No ina diagnosed Hawaiʻi moku.

symptomatology o ka maʻi

Aortoarteriit nonspecific symptoms mea okoa, e hilinaʻi nui ma luna o ke kino o ka mea maʻi. Takayasu maʻi paha e maʻi a me ka huʻi pae.

Ka huʻi pae o ka maʻi ua hoikeia aku ai e na kēia symptoms:

  • General luhi.
  • Ma hoʻokō ', eha i loko o nāʻiʻo a me ka ami.
  • Eia kahi mea akaka haemorrhagic wikiwiki.
  • Ulu ka erythema nodosum.
  • Hoʻonui i ka palena o ka naau.
  • Eia kahi mea akaka systolic a me kēlā wā i kēia wā diastolic'ōhumu aku ai.
  • Pohihihi keia hihia o abdominal eha.
  • Inā mākou e lawe mai keʻena hoʻokolohua ho'āʻo ma, ka mea, hoike lōpū anaemia, i ke alo o ka C-kū'ē kumuʻiʻo.

Muli o kona kulana pinepine, i ka hoike ana o ia mau symptoms misdiagnosed - "rheumatoid arthritis", "TB" a me "sepsis." Kēia, Eia naʻe, i loko o ia lŘlŘ 95% o ka hihia.

I ka holomua o ka maʻi ke kahua o ka maʻi

Inā na kuʻina mua o ka maʻi mai e lawe ka hoʻokō ana i ka ho'ōla ia, pathology koke i maʻi. Symptomatology mea ua okoa mai ia i loko o ka huʻi pae:

  • Kokoke ka mea,ʻaʻoheʻai ma ka kekahi lima, a kekahi manawa elua.
  • Nā mea maʻi pinepine ohumu o kaʻeha ma nāʻaoʻao, i me ka mahuahua haawe wale listen.
  • Hands lilo nawaliwali, paʻakikī no ka poʻe e paa mea.
  • Pinepine i kaʻona, a i ka hopena i loko o ka poho o ka ike paka i.
  • Ka wā e kipa i ka ophthalmologist ia akulla loli ma ka fundus.
  • Mai ke kaʻina hana 'ole ka pinepine o ka coronary arteries, ka mea hiki ke malama ischemic ho'āhewa wale.
  • Me ka make o ka abdominal aorta hoʻomaka e hana eha iaʻi hakuʻala.
  • Neurological kāna hana i hoikeia like hihia hoʻi noonoo ana a me ka hoomanao ana, hoemiia ka hana nona iho.
  • Inā ka optic nā aʻalolo ua iʻa, alaila, poino ka hihio, papalua hihiʻo akaka, e e makapo i loko o kekahi maka.
  • Ke komo ana o ka pulmonary artery alakai ana i ka hooulu ana o ka pokole o ka hanu,ʻeha i loko o ka pahu.
  • E ae aku ami o na lima.
  • I ka hoomaka nonspecific aortoarteriit propagation kaʻina hana me ka papa kuhikuhiE arteries, a IeAUPIIe, IAa IO hiki aku ai i mahuahua ke koko, no ka ai i ka hou ana o na moku koko.

Maʻamau, ka huʻi pae o ka maʻi i maʻi no 6-8 makahiki. Nā mea maʻi e e wary ina ka mea, e mau loa ma ka nawaliwali, headache,ʻeha i loko o ka papa o na arteries nui, hihia hoʻi ōhumu a iaiyoe. Oe Pono e undergo i piha ka ninaninau i ka mea e hookupaa nui ae i ka pololeiʻike.

ʻike,

Inā he mea i hoʻohuoiʻia no ole-kekahi aortoarteriit, i kakahiaka nuiʻike, ka mea nui. Kēia maʻi Ua ike na kauka, ina he mea na kēia symptoms:

  • Inā he mea he nuiʻokoʻa i loko o ke koko, i loko o kekahi mau lima.
  • Lāʻau ikiʻai wale loa nāwaliwali, ai ole detectable.
  • Aia ka intermittent claudication.
  • I ka wa e hoolohe ana i ka leo ike i loko o ka aorta.
  • Ka hookolokolo ana hōʻike artery hou.
  • Insufficiency o ka aortic kiwikā.
  • Paakiki mahuahua ana i loko o ka puʻuwai.
  • ESR ua hoomahuahua ia no kekahi kumu.

Eia hoi, e kōkua diagnose i ke kēia haʻawina:

  1. Biochemical Ka Ikepili o ke koko hōʻike i loko o ka abnormalities koko i mea ano o keia maʻi.
  2. Ultrasound ka ninaninau ana i na moku, e loiloi i ko lakou kulana a me ka uku o ke koko.
  3. Angiography me ka Akä naÿe ka pahu kui huai ae arterial constriction.
  4. Pahu X-Ray mea i hoʻoholo 'o ka wahi o lesions o ka aorta a me ka pulmonary artery.
  5. Echocardiography Loiloi i ka functioning o ka naau.
  6. By electroencephalography hiki huai ae ka haunaele ma cerebral moku koko.

Ke'ōlelo mai, no ka mea maʻi, a me ka poe me nonspecific aortoarteriit, 'inikua mōʻaukala hoʻomaka me ka piha anamanaʻo, i AIM e paʻipaʻiʻike.

palena pauʻike,

He mea nui no kaʻike, e differentiate aortoarteriit congenital anomalies o ka vascular'ōnaehana a me ka thromboembolism. No ka mea hope ua wehewehe aku ma ka huʻi papa o ka hiki ho okumu ana o ke koko clot i loko o ka lua o ka naau Muscle.

An nui hiʻona mea i ka ole-i ho'ākāka 'e loli ai aortoarteriit pae o ka moku, oiai no congenital anomalies e ae mai oe i kekahi mau arteries.

Inā ua ku paa ma kaʻike, renovascular hypertension, ia mea pono i ka hoomanao i ka mea hiki ke hoʻomōhala atherosclerosis a me kaʻaʻa puʻuwai moku. Inā aortoarteriit nonspecific e hoʻomōhala ana iʻano nui i loko o na kaikamahine, atherosclerosis e loli ai mua na kanaka.

Wale i ka piha hookolokolo a me ka palapala hōʻoia no hoʻomalu, e kōkua e i kaʻike, a me ka hoʻomaka ka hoʻokō lapaau.

Lapaʻau syndromes loko pathology

Ua haawiia ia i loko o kēia pathology e loli kekahi mau pauku o ka moku i hoolako i ke koko i ka na nā loko, e mea hiki ke kālā līkaia no kekahi mau lapaʻau syndromes:

  1. deficiency maʻi pale o kaʻike ākea koko pele. I ka Ia manawa, aia no na eha i loko o nā lima me ka manao o ka numbness i loko o ka manamanalima. Inā luku aku la ma ka vertebral arteries, ka eha ma ke kua malaila.
  2. Mea'ōnaehana mānowai koko maʻi pale - ua pili i ka hooulu ana o collateral holo. Hiki diagnose na symptoms o myocarditis, ischemia.
  3. Inā i ka loli ana o aortic e pio mai, i ka ulu cerebrovascular maʻi pale. Hoikeia aku ai e headaches, hoemiia hihio, mai ka pioloke o cerebral holo.
  4. Abdominal maʻi pale ua hoikeia aku ai e kaʻeha i loko o ka abdomen, i mea paroxysmal ma ka ano. Kēia hoike ana mea i uncommon ma lesions o ka abdominal aorta.
  5. Hypertension maʻi pale - akaka like me kaʻilihune o lesions o kaʻaʻa puʻuwai arteries.

Inc

Inā i kaʻike, o "nonspecific aortoarteriit" iapaau ana ua manao ia:

  1. Nui hopena ma luna o ka pulakaumaka o ka li nui, hiki ma ka hoemi ia i ka palena iki.
  2. Kaua aku me ka ischemic complications.
  3. Wehe i na hoikeana o ka hypertension.

He aha ina he kanaka i ke pili-kekahi aortoarteriit? ʻike, lawe mai ho'āʻo ma Komikina'Āina, he hoʻomalu hana - e kūkulu i ka lapaau regimen. Inc paha e like penei:

  • Ka lapaʻauʻia.
  • ʻoki kino.

E noonoo oe i ka hōʻike a me nā 'ano o kēlā me kēia koho.

lapaʻau me ka ai '

Lapaʻauʻia hoakaka ia aortoarteriit ka wā e noonoo pono i ka oolea o ke ahonui i ka ana a me ke kahe 'ano o ka hoʻoʻino kaʻina. ʻO kēia mau ai 'i hoakaka ia loa pinepine:

  • "Prednisolone" i loko o ka nui o ka 1-2 mg no kilogram o ka hoʻomanawanui kaumaha. Komo ua lawe mai no 1-2 mahina.
  • Inā ka li nui i ka nawaliwali ano, ua hoike mai ka loaa ana aminohinolinovogo ai ', no ka laʻana, "hana Lago" i 0,25 g.
  • XIX. Inc ua muli ma ka? Eaia o "methotrexate". Ke laʻau heluna He 7-10 mg no huinahalike mika kinoʻilikai wahi. ? Eaia - hookahi o ka hebedoma.
  • Kākoʻo konohiki i anticoagulants, cardiac a me ka ai 'i lalo ke koko.

Uluwehi O Inc i kaʻaoʻaoʻelua ano, ina he mea ole hana hou paha, aia no he hiohiona hoʻohuikau o ka lala, lolo, ka mea, ua? Aeiiaiaoaony e akoakoa ai iʻoki lāʻau lapaʻau 'uao.

ʻoki lāʻau lapaʻau lapaʻau

Inā makeʻe kulana nohoʻana mai i ke kōkua, a me ke kahua e wale kiʻiʻino, i e, Kamuela iʻoki lāʻau lapaʻau malama. ʻoki kino kōkua e hoihoi koko i nā loko a me nā'aʻaʻa. Akā, e pono e kaʻikaʻiʻia ma ka manaʻo i ka hoʻoʻino kaʻina E e papani iho la i muaʻoki kino. He nui na ano no kēiaʻano o ka Inc:

  • Endarterectomy. Ua ua hana ia ma ke alo o ka noho kaʻawale segmental occlusion o na arteries, i holo 'ana mai o ka aorta.
  • Agnioplastika lawe mai ina loaʻa nā loli i loko o na moku kanaka o nā puʻupaʻa.
  • Holo alaʻokoʻa pakuiia auanei lakou ua lawe mai ka hoʻohana 'ana i ka kemikala vascular prosthesis. Oia uao mea mana i loko o mau vascular lesions.

Ma hope oʻoki kino hoʻopulapula au mea nui, kaʻaeʻana me kauka koi.

Aʻo no nā mea maʻi

We loaʻa mai i ka mea a ka aortoarteriit nonspecific symptoms a me ka hana i kekahi mea, noonoo iho, akā, i ka hoʻomanawanui mea hoʻomalu i nui, e malama i ke kēia mau lula.

  1. Kēlā me kēia hoomanawanui ë he mähele wale i ka iapaau ana o keia maʻi pono manawa a me ka ana i kona akua o ko nā mea a pau kauka ka hookohu.
  2. He mea pono e hoopili aku i ke ano a me ka laʻau heluna o ka lapaʻauʻia mea i ao aku i ke kauka.
  3. No ka mea, e lawe nui dala o ka ai ', he mea no ka pilikia o nā adverse loa i Inc. E loa kń ia, ia mea pono e undergo regular examinations a me ka hele aku e ho'āʻo ai.
  4. A hiki i ka mea hōʻemi o ka pono, e hai aku i ka hoʻomalu.

Inā e hoopili aku i kēia mau koi, i ka Inc o ka maʻi, e e oi holomua.

Ke prognosis no nā mea maʻi

Eia naʻe, i ka pakele ana i ka politika-kekahi aortoarteritis hiki ole, akā, inā hiki kū i ke kauka mau koi, a pau pono ka 'inikua lapaʻau e kalaia mai ai. Kēia e ae hoʻomanawanui iki mai e komo i loko o ka mau chores, a i haha aku eha.

I ka laulā o ka lapaau hilinaʻi nui ma luna o ka oolea o ka li nui, a me ka alo ana o complications, a me ka mea, ua loli ana ma ka pololei a me ka māmā o kaʻike,. No laila, ma ka hopena o ka Inc ua 'oluʻolu, e mea pono, e huai ae i ka maʻi i loko o kona kakahiaka kahua o ka hoʻonaʻauao.

Special kāohi ana mea i hoakaka ia.

Kekahi maʻi pono i ka hookokoke nui, ka mea wale alahele e loaʻa ai? Ienoai a hoʻolilo i ka maʻi. E malama i kou ola, a kekahi mea loiloi mau - no laila 'oe e huai ae abnormalities ma kekahi kakahiaka nui ke kahua, a e koho ka hoʻokō lapaau.

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