Ola kinoMaʻi a me nā kūlana

Cretinism - ia .. Symptoms, lapaʻau, Kāohiʻana a me kaʻike,

Cretinism - he maʻi o ka endocrine'ōnaehana, i ua pu ma ua hoʻemi ha awina o ka thyroid gland. He He 'ano like maʻi i IeAUPIIe, IAa IO akaka ma ka kamaliʻi. No laila, ka mea i mua symptoms? Ka mea kue i ka hoʻololi kemikala o thyroid hormones? He loaʻa i kekahi pono ka nohoʻana? Pane i kēia mau nīnau e ia o ka hoihoi ana i na mea he nui heluhelu.

Pōkole 'ike e pili ana i ka' ole a me ka hana ana o ka thyroid

Cretinism - he maʻi i ua pili me kaʻole thyroid hana. No laila, e hoʻomaka ana me ka mea e e pono no ka ike lea i ka mau 'ike e pili ana i ka hana o keia kino.

Thyroid pili ia i na glands o na secretion. Ua mea e pili ana i ka cartilage o ka larynx ninoieo o ka akau, a me ka lobe hema, a me ka isthmus ai pili aku ia lakou. I ka papa kuhikuhiE gland hormones i haawiia thyroxine a me ka triiodothyronine, kona hoʻololi kemikala ia lŘlŘ ina lawa wale dala o ka iodine. Eia kekahi, keia kino produces kekahi'ē aʻe hana waiwai, o ka oi aku calcitonin (ka hōmona kuleana no ka kalipuna pūnao i loko o ke kino).

Thyroid hana, ua hilinaʻi nui ma luna o ka functioning o ka hypothalamic-pituitary'ōnaehana i loko o ka lolo. Ke pituitary gland ke hookuu aku oia thyroid-noho haumāna kahi hōmona, a haʻalele no ka keʻano o ka hanaʻana o ka hoʻololi kemikala o thyroid hormones. A waiwai hua mai la i loko o ka hypothalamus, i ka pāʻana i ka pituitary.

Me ke komo 'ana o ka thyroid hōmona ia lŘlŘ keʻano o ka hanaʻana e like me:

  • pūnao o adipose'aʻaʻa disintegration, hoʻololi kemikala a me ka hālāwai hope o ke kumuʻiʻo nā lātoma;
  • i ke kahua o ka ikehu, i mea e pono ai Muscle a me ko mākou hopohopo kahua;
  • hoonui koko monakō koko pae;
  • Hana ko mākou hopohopo a me ka endocrine'ōnaehana (thyroid hormones loli i ka hana o nā endocrine glands);
  • Amo ana i nā waiwai i keena.

Me ka ka ho'ēmiʻana o ka nui o ka thyroid hōmona e hoʻomōhala ana i ka maʻi i kapaia hypothyroidism. Ma hoʻi, i kēia maʻi ke alakai i ka cretinism, myxedema, a me ka hahaki pinepine ma ka aoao o ka endocrine nenoaiu.

Hypothyroidism a me kona Lolina

I ka mea, ua nui na nenoai o ka Mea Maluna o ka maʻi. Loa pinepine, ae aku na keiki cretinism, e like me ka maʻi ka mea, i ka innate. Ma ka kekahi lima, ka mea hiki ke loaa - ana ma lalo o ka aoao o kekahi mau aʻe.

Ke kaumaha ma muli o ka mea e mau ke ano o na pathology:

  • iniiaiie hypothyroidism, a ua pili i hoʻopōʻino thyroid hana;
  • haumāna ano o ka maʻi e ia lŘlŘ ma luna o ke kāʻei kua o ka malfunction o ka pituitary;
  • Tertiary hypothyroidism, ma a he mea he malfunction i loko o ka rula ma ka aoao o ka hypothalamus;
  • 'aʻe' ana i ka pā lonoaʻili o ka pale umauma hoʻokahi aeee (i loko o kēia kahua o nā hormones i hua mai la i ka lawa na mea, akā, i kēia mau keena e ole ikepili koʻikoʻi).

Lohe nuiʻia nei heʻano o ka maʻi like endemic cretinism - he kŰia i ua malama i waena o nā kupa o ka wahi me ka lawa iodine.

Cretinism: 'ehaʻeha ka

Koke ia mea ke kumukuai i ka i ana ia mea, ua nui aʻe i hiki ke alakai i ka mea maʻi. E like me ua oleloia, cretinism e loli ai i na keiki, ka poe i thyroid hōmona deficiency. A ua ka moku'āina hiki e kekahi congenital a loaa.

No ka kumu o congenital hypothyroidism nā:

  • congenital hypoplasia a kaawale o ka thyroid gland o ke keiki;
  • irradiation o ka hapai wahine a lawe lapaʻauʻia e emi i ka hana o ka gland;
  • thyroid mai i loko o ka makuahine, i hāpai keiki;
  • aaiaoe maʻi, i kūpono i ke kāʻili 'ana i hehi iodine thyroid'aʻaʻa;
  • aaiaoe e hoʻonele i ka maʻi 'aʻai ana i ka pituitary hormones;
  • congenital maʻi e ma loko o ka hypothalamic-pituitary kahua.

I ka huli, loaa ke ano o ka maʻi i kekahi ana ma lalo o ka aoao o kaʻokoʻa aʻe:

  • lawa ka nui o ka iodine i loko o kaʻai o ka hapai wahine a me ke keiki;
  • Hashimoto ka thyroiditis;
  • li nui o ka thyroid gland;
  • trauma aʻoki kino i loko o ka thyroid gland;
  • eha, li nui, a me kaʻoki kino ma o ka lolo, a i pu ma lesions o ka hypothalamic-pituitary (axis);
  • loloʻeho.

'Aʻe' ana i ka halepaahao pā lonoaʻili i hormones, thyroid

Oia ke ano o congenital, a pili i kekahi aaiaoe kāna moʻolelo, kāna hana a me ka chromosomal DNA 'ole. Ma keia maʻi hormones i synthesized i loko o ka maʻamau dala, akā, i ka pale umauma hoʻokahi aeea mea ole ikepili koʻikoʻi ia ia. Ili mai na makua a me kaʻaneʻane untreatable.

Cretinism i na keiki: He aha ka ka pilikia?

I mea, i kēia maʻi o loa ka mea, no ka mea, thyroid hormones i kekahi mea i ka pāʻana i ka hana o ka aneane i ke kino holoʻokoʻa. No laila, i ka hopena e i maʻi?

Cretinism e loli ai i ka ulu ana o ka lolo, ka meheu o ia ia. Ma kekahi, e kū'ē i ke kāʻei kua o ka maʻi he mea he developmental kāna hana o ke aʻalolo olona, e like me ka emi ana ma ka huina helu o neurons a me ke kahua o ka waiwai i inhibit i ka ha awina o ka lolo.

Maoli ai, ke keakea kena ae la ma ka thyroid hormones a me nā haunaele i loko o ke kino, ma ka a pau:

  • ka meheu o ka ulu ana keʻano o ka hanaʻana;
  • Muscle nawaliwali;
  • emi ma ka kumuʻiʻo? iecaianoaaiiuo a me ka mana pili 'o Randy;
  • kanaka haunaele iloko o skeletal ulu ana;
  • hemodyscrasia keʻano o ka hanaʻana;
  • he hoʻonāwaliwaliʻia'ōnaehana paleʻea kahua;
  • malfunction o ka endocrine'ōnaehana, ka oi aku o ka adrenal gland, gonads;
  • he malfunction o nā puʻupaʻa, akepaa, liʻiliʻi,'ōpū;
  • 'aʻe' ana i ka mana o ka ili.

O ka holo ana, ina ua pilikia ai ka haohao ana i loko o kakahiaka kamaliʻi, i ka wa e kaawale aku o ka iapaau ana, he mea ka 'aʻe' ana i ka hana o kaʻaneʻane pau hui, nenoai.

Ka mua na hoailona o ka maʻi i loko o na keiki

Na wale ala, e huai ae i ka maʻi i loko o nā pēpē i mea he koko hoao no ka hōmona. Cretinism i loko o ka 2-3 mahina o ke ola mua, kokoke 'aʻole i kānāwai. Aka hoi, ke kauka e hai i ka emi ma ka ikaika loa ka makemake, pokole o ka nasal hanu, pinepine digestive pilikia, haʻahaʻa ka naʻau ana a me ka nui fontanelles i loko o ka puniu wale no mea i lōʻihi ulu.

E like me ka ulu ana o ke keiki hiki ke ike, a me ka 'ē aʻe, oi hoʻoponopono symptoms. Ke kamaiki Ua ho onui ana ke kaupaonaʻana lohi akā, nana nepunepu like prone i ka edema. I kekahi manawa, he mea kaumaha nani elelo. Disproportionate poo nui me ke kino ma ke kua o ka ulu ana. ahupapa a mau keiki e e ākea nasal alahaka a me ka ololi mau maka, e like me ka pono me pōkole a me ka mānoanoa'ā'ī. Oe i hai kekahi kāna hana'ē aʻe - i ke keiki mau waiʻona, lethargic, uncommunicative. Me ka elemakule, oe e hai i kali hou aku; o ka noʻonoʻo kūpono 'ana.

Cretinism symptoms i kanaka makua nā mea maʻi

Inā untreated, na symptoms wale e ino me ka elemakule. People pilikia mai cretinism, i loa ano physical hiʻona, e like me pōkole ke kino o Iesu, kino māhele o ka disparity. Ua ua i wehewehe aku e kekahi mau paonioni ana, clumsiness ma muli o ke kino 'ole, clubfoot, hoʻopōʻino ka hoʻoneʻe i mau ami. Aia nō i kūikawā hiʻona, e like me kiʻekiʻe lae, nui lehelehe, kiʻekiʻe cheekbones, mau nei iluna alelo, nei iluna pepeiao.

ʻaneʻane nā mea maʻi a pau me ia i kaʻike, e ae mai oe, mai noʻonoʻo retardation i loli iki degere. Nō hoʻi, ma laila nō keʻano o ka hoolohe, a me ka olelo, i kekahi manawa, i ka mea kuli-mutism. Mai ka hana o ka 'īnea i glands ua hoemi, e mea hiki infertility. Eia hou, i kēia mau kanaka i sluggish, unsociable, apathetic a me koʻu hoomanawanui ana'ku ia mai kekahi ano o ka noʻonoʻo kāna hana.

Hoikehonua, ano o kaʻike,

Inā he mea e hoʻohuoiʻia e koke nīnau aku i ke kauka. Wale nō ke akamai ike ia mea hypothyroidism, symptoms a me ka hana a mākou e kūkā ana i keia la. No ka pololeiʻike, hoopai wale nana endocrinologist lawa.

E hoʻomaka, mālama 'ia ke koko e ho'āʻo ai no ka hōmona pae a me ka thyroid gland. Ma ke ala, kekahi nā mea maʻi e kūkulu i ka ai-kapaia? Aiaiiuie hypothyroidism, no laila, i nā ho'āʻo ma kekahi, hou kekahi manawa ma hope. Ma na mea he nui nā keʻena lāʻau lapaʻau lawe koko mai nā pēpē i no ka Kāohi noiʻi.

Hope no hoi e paa ana ia ultrasound thyroid gland, a no hoi, ina e pono ai, a me Doppler ʻelua papa kaʻimiʻana. Mau ho'āʻo ma e ka mea hiki e hooholo i ka nui o ka prostate, ka loaʻa nui, piʻi pū, nā loli i nā nā'aʻaʻa o ka thyroid gland hikoko, e like me ka moku'āina o ke koko.

Children kekahi hōʻike X-Ray iwi, e like me ka na keiki i ka maʻi, ua lohi skeletal ossification. Inā pono, i ka hoʻomanawanui i ninaninau lapaau a pediatrician, neurologist, orthopedist, psychiatrist - kokua kauka huai ae i ke alo o nā complications, a me ka unuhi i ka lapaau regimen.

Nā Papahana O Ka ana i ka maʻi

Wale kou kauka ike i ka hypothyroidism (symptoms a me ka hana ana o keia maʻi, hiki complications - i kēia mau mea a pau e ke kūkākūkā me ka 'oihana), a wale ia e kōkuaʻoe. No laila, ma kekahi hihia, mai i hoʻohemahema wale i ka'ōlelo aʻo o ka poe akamai i.

E like me ka rula, nā mea maʻi e loaa hope Inc - ka mea, lawe hormonal ai 'i e i ka nele o maoli hormones thyroid. Ma kekahi, ia mea nō ka hoʻokō ua ka lāʻau «L- thyroxine". Eia, i ka iapaau ana regimen i ke komo pu wikamina eiiieaenu, nootropic ai '( "cerebro", "Pyracetam", "Nootropil"), me pono me ka medicament no ka hoʻomaikaʻi i ka mana o ka hoomalu ana a me ka neural nā'aʻaʻa mana ( "Lipotserebrin", "Pantogam", " encephabol ").

An nui ke keʻena o ka lapaʻau mea ponoʻai, a e i lawa dala o ka iodine. Ke kaumaha ma muli o ka ano o ka hoʻomanawanui i pono ai kōkua neurologist paha psychiatrist. I ka wā e hiki mai, ke keiki pono mau undergo i ka 'inikua hookolokolo, a lawe i nā ho'āʻo ma, i ka hopena o i ke kauka ke hoʻomaʻa i ka iapaau ana regimen.

He aha ka ke Outlook no ka hoʻomanawanui iki mai?

Cretinism - He maʻi ka loa pilikia, e like me ka mea hiki i alakai i ka kīnā o ke kino. Aka hoi, ka hapanui pinepine i loko o ka kakahiakaʻike, a me ka pono hana o ka hoomanawanui hikiʻole ke kōkua. Normalization o ka thyroid a me ka pituitary glands hiki aku ai i ka hoʻopau o metabolic kāna hana.

Naʻe, i na hihia a pau, complications hiki ke käpae '. No ka laʻana, ka wā hoʻomaka 'ana ka hopena lolo pōʻino Inc koe. Ae, a me kekahi aaiaoe maʻi i paʻakikī i ke ahiahi symptomatic lapaau.

He nui ka hoʻokō ano o ka Kāohiʻana?

Ua mea waiwai 'ana i kumumanaʻo ia cretinism - he maʻi loa nui, a ma kekahi hihia hiki ole ke AOON. Me ka i ka loaʻaʻana a me ka 'eleu hana hiki e käpae' ia e pono ke kaupaonaʻana complications. Understandably, he nui loa kanaka i hoihoi i loko o ka ninau o ka mea, ua hiki ke pale aku i ka ulu ana o ka maʻi.

Aia nō kekahi ano rula, i poe akamai i waiho aku i ka mālama. No ka laʻana, ma ka wahi, kahi a ka maʻi mea, he pono ole, ua pono e lawe mai nohona ma prophylaxis, i pau e kanaka hoʻoponopono i ka lawa ka maʻiʻo o ka iodine i loko o kaʻai.

No ka mea, cretinism e loli ai i na keiki, kona thyroid hōmona deficiency, ia mea paʻakikī nui, e hoʻolohe i kēia wahi ma ka hoʻolālā kahua o ka hāpai keiki. No ka laʻana, e aʻo aku ai iā mākua no ka ho'āʻo, a hele aku ma kekahi mau ho'āʻo ma no ke alo o ka metabolic kāna hana a me kekahi aaiaoe maʻi. Eia hou, he wahine hapai e akahele kanaka hoʻoponopono i ka nui o ka luku iodine. A ia mea nui ia e mālama nei loiloi 'ho'āʻo ma hope koke iho o ka hanau ana, no ka mea, o ka koke ia ka maʻi ua' akomi i, ka mea i oi aku i ka manawa o ka holomua lapaau ma mua o ka helehelena o ka mea complications.

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