Ola kinoLapaau

Dubin-Johnson maʻi pale: hōʻike,ʻike, symptoms a me ka lapaʻau

I loko nō o ka mea i ke kālā no lapaau i i nui ka holomua a me ka maʻi he nui i hou i ka olelo no na nā mea maʻi, kekahi o kēia mau maʻi ua ole i maopopo hoomaopopo. Kekahi o ia mea no ka Dubin-Johnson maʻi pale. Ke? Aaieou,ʻike, a me ka hana ana o keia maʻi poses i ke ola 'Oihana o kekahi hoihoi. E hoomanao i keia ninau i hou au mamuli.

Epaepa huila maʻi pale a me Dubin-Johnson maʻi pale - pohihihi keia hereditary maʻi ake Similar interconnected jaundice.

kumu o ka

Dubin-Johnson maʻi pale no hoi i kekahi inoa: enzimopaticheskaya jaundice akepaʻa. Ua kupu ana ma ka pili ana i ka 'aʻe' ana o ka haawi i loko o ka bile, mai ke akepaʻa keena o ka bilirubin.

He mea hōʻike ia ma ke kino no ka hoopau ana mea poino a pau luku erythrocytes. Panina Manaʻo bilirubin ia lŘlŘ i loko o nāʻaoʻao:

  • mahuahua i ka nui o ka waiwai a pau e hiki mai ma ka bile;
  • dala uuku o ka mimi, e hele.

Dubin-Johnson maʻi pale ia lŘlŘ ka wā o Nyos amo o bilirubin Via ka bile. Kēia mea he loa pohihihi keia maʻi susceptible i oi kanaka ui (ma kahi o 20-30 makahiki). hihia o ka maʻi, mai ka hanau ana i kekahi manawa i hoʻomaka ai. Ka pilikia o ka maʻiʻaʻai ma hope o ka makahiki o ke kanaka 50 makahiki a oi i ka palena haʻahaʻa.

Ke aaiaoe kumu o ka maʻi pale, Dubin-Johnson mea no a hiki i ka'ōewe mutation, komo i loko o ka mea hoʻolilo o bilirubin i loko o ke ake, a hoʻopā'ālua nā polokina.

symptoms

Dubin-Johnson maʻi pale, symptoms o i mea ano o na maʻi e like me, no kekahi laʻana, luhi, a i kona mau hanohano nō hoʻi hiʻona:

  • ʻeha i loko o ka iwi aoao ma kaʻaoʻao'ākau;
  • he piha nele i ka ikaika loa ka makemake;
  • loaʻa paha e hōʻemi iki maneo o kaʻili;
  • hoonee aku i ake;
  • colic, i kekahi manawa kūpono;
  • ka luaʻi;
  • ana wela mahuahua.

Hoike ana i listen ma muli o ke infectious maʻi, loa kino ai a me ka mea naʻau overload. No ka wahine, e hiki aggravation ma hope oʻai ana o contraceptives.

kamepiula pūʻulu

A pae ana o kanaka e e wary o ka maʻi pale?

Ka maʻi Ua hereditary. Inā kaʻohana he mau keiki me keia maʻi, ke mau ma ke kahua o ka hoʻoneʻe o ka hāpai keiki mea pono e hele aku i nā ho'āʻo ma, kekahi i ka mea e pono ai e ho'āʻo ai, a kukakuka pu me ka hoʻomalu. Kēlā mau koi e pili ana no ua mau Leomakana, a me kekahi o na noho male a me kā lākou pili hoahanau i waiho wale aku no Dubin-Johnson maʻi pale.

Ka PalekanaEND_LINK kaʻina

Geographically, ka maʻi i loa a pau mawaena o'Ilana Iudaio. Lākou helu kīnā 70% o ka huina o ke kaupaonaʻana o ka maʻi ana 'o nā mea maʻi.

He mea nui i aneane ole ola-hooweliweli Dubin-Johnson maʻi pale. Kumu e hoomanawanui i keʻae i keia. Kauka hookolokolo aku la ia i ke ola expectancy o nā mea maʻi i kēia maʻi, a manao ia ia, aole ia e alakai i ka make.

About 25% o ka hoʻomanawanui iki mai ka mahina eha ma ka hypochondrium akau. Ka 'ole o ke akepaʻa i loli, he mea ole deformation i loko o ka maʻi pale. Akā, i ka mea ia manawa i loko o kona nā'aʻaʻa ikeiaʻeleʻele wahi lilelile, kūpono ai i loko o ke kino hoʻololi kona ano i ka uliuli a me ka pouli eleele. Kēia hiʻona o ka maʻi pale ua kapaia kokoleka? Inoaia nā kuki. Keia kanawai ua loaʻa ma ka hahau metabolites secretion.

I ka maʻi i ka maikaʻi prognosis, e like nae ka mea hiki ke hoʻomau ma ke ola ana o ka hoʻomanawanui.

I ka papaʻaina ma lalo Hōʻike 'o ka' ikepili ma luna o ke kūlana o ka mea na nā loko o nā mea maʻi.

hui, moku'āina
ake like me ka rula, mahuahua
ka laau awaawa, a me ka bladder ducts ole hoʻololi
spleen pinepine hoalaia

lapaʻau '

Dubin-Johnson maʻi pale, ma kaʻike, a i lawe wahi i loko o kekahi mau kahua o ka hoʻonaʻauao, nānā 'ia e kālailai.

  • He OAXA e ultrasound o ka abdomen.
  • General koko a me ka mimi ho'āʻo ma.
  • Ka Ikepili o ke koko a me ka mimi no bilirubin. E like me ka rula, ka mea, uaʻoi aku ko lākou kiʻekiʻe.
  • Eia kekahi laʻana fenobarbetalom.
  • Hōʻailona o ka hepatitis.
  • Laʻana bromsulfaleinova.
  • Coproporphyrin waiwai o nā hoailona ma ka mimi no ka lā.
  • Ka maʻiʻo o na nā'ūhū i loko o ke koko.

Pili kekahi kiʻina hana'ē aʻe o kaʻike,.

inoa hiʻona
PalekanaEND_LINK laparoscopy typical o keia maʻi pale poeleele hoi ake
kui kele ma biopsy loaa ia ia ma ke akepaʻa i ho'ākāka 'pigment gepotatsitah
ke kaʻina hana no intravenous holetsistografii i ke aumoe paha,ʻaʻole lawe mai opacification o ka gallbladder a me kona ducts ma nā mea a pau

Ma ke alo o Dubin-Johnson maʻi pale hoʻomanawanui iki mai i ke kipa i ke kino.

Lapaau a me ka Kāohi

Dubin-Johnson maʻi pale, i lapaʻau 'aʻole ole pū loaa kūikawā hoomakaukau hoi malalo o ko kāohi ana:

  • adherence i ka ikaikaʻai, i ka pono o ka B nā wikamina, ole-preservatives;
  • ka ho'ēmiʻana i loko o stress wahi, i hiki;
  • ka ho'ēmiʻana o physical aayoaeuiinoe;
  • hoole ana o kanakaʻona mau nā mea inu;
  • Ka pololei, ka mālamaʻana o ka bilirubin pae ma luna o ke ola o ka hoʻomanawanui ka ola.

Ua mea i pono, e hoomanao i hāpai keiki i exacerbate i ka maʻi. Ai ', e kōkua hoola i ka maʻi pale Dubin-Johnson, a ianoiyuaa a i ke kino.

Like me, ke ano o ka maʻi o epaepa huila maʻi pale.

pōkole hōʻikeʻano o ka

Epaepa huila maʻi pale no hoi mea he hereditary maʻi e loli ai ke akepaʻa. Undergoes loli ma ka haawi ana i bilirubin,'ūhū oihana koe maʻamau. Mākou ke i aku nei au i ka maʻi o ka Lightweight ano o Dubin-Johnson maʻi pale i ho'ākāka 'ia ma luna. Symptoms no hoi i hoike i kona wahi softer.

I ka maʻi ke hoike like, mai ka hanau ana a me ka kamaliʻi. Bilirubin i loko o ke koko o ka hoʻomanawanui hiki e noa a me ka nakinakiia. Aia He He Akä naÿe o ka gallbladder.

Epaepa huila maʻi pale ua wehewehe aku ma ka mea i loko o hepatocytes ole maʻiʻo o ka mea eleele pigments. 'Aʻole i loaʻa o ka manao, a uaʻikeʻia me kokoleka? Inoaia nā kuki. Ke kumu o ka maʻi mea iki okoa mai Dubin-Johnson maʻi pale. Ma keia hihia, ke ake hiki ole Makuakane me ke omo o ka bilirubin. E like me ka hopena, hoʻokō 'ole' undigested waiwai hoʻi i loko o ke koko. Ma keia kumu, i loko o ka hoʻomanawanui e hoʻomōhala ana i giperbulemiya. Ano prognosis o ka maʻi.

I ka manawa o kaʻike, lidofreninom akepaa, ka laau awaawa, a me ka bladder ducts i hiki.

maʻi pale symptoms

Na hoailona epaepa huila maʻi pale ka mea i like loa me ka symptoms o ka maʻi pale Dubin-Johnson:

  • Implicitly hoikeia jaundice.
  • I ka manao o ke awaawa i loko o ka waha.
  • Pain i loko o ka hypochondrium akau.
  • A lohe o Dubin-Johnson maʻi pale, ake nā mea maʻi nui ae la ka nui. Ma ka hihia o epaepa huila maʻi pale ua mahuahua wale i loko o kekahi mau hihia.
  • Ke kiekie pae o bilirubin i loko o ke koko.
  • ake kuleana pili i ho'āʻo ai i mea maʻamau.
  • koko e ho'āʻo ai me ka loli.
  • Ke ake bioptome mea i hoʻomāhuahua o pigments.

Prognosis nui maikaʻi, i ka maʻi pale ia lŘlŘ ma na makahiki, i oi aku compromising kanaka ola.

ʻike, no ka maʻi pale

Ka maʻi hiki wale ke kau ma ka hulinaʻike, o ka meaola.

Haʻawina mālama 'ia i loko o ke keʻena hoʻokolohua, e kōkua hoike i hoʻomāhuahua mau ana i ka maʻiʻo o ka bilirubin i loko o ke koko. No ka meaʻike, ka mea, ua nui e ike i ka helu ana o coproporphyrin na i loko o ka mimi.

Ma ka hapanui o nā mea maʻi, i ka maʻi progresses me kekahi symptoms.

Ma ka hihia o kaʻike, a epaepa huila maʻi pale pana aku au i ake keia hookolokolo ana: kona X-Ray a me ka ultrasound. Ma ka Ia Ka Ikepili undergo ka laau awaawa, a me ka bladder ducts.

maʻi Kāohi

General kāohi ana e like penei:

  • ka ho'ēmiʻana o physical aayoaeuiinoe;
  • iapaau ana o ka maʻi pili i epaepa huila maʻi pale;
  • Pale stress a me ka 'ehaʻeha o stress.

Makaʻu o ka mahuahua o ka bilirubin i loko o ke koko

Bilirubin, piʻi pū no ka mea kēia mau kumu:

  • loa stress;
  • unhealthyʻai, iʻai kue;
  • i ka hoʻohana 'ana ai';
  • excessive pono o ka waiʻona.

lapaau ana i ka maʻi

Common ki ina hana like, e hoʻopau i ka maʻi ma laila. Naʻe, ka mea, e hoʻokō i kāohi ana. E like me ka ai 'oe i pono e lawe' o ia hoʻi ia auaiaea bilirubin mai ke kino. Bile Ua pinepine ai 'i hoʻohana.

Koho i ka iapaau ana kūpono e kōkua i ke kauka.

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