Helu sclerosing cholangitis: Symptoms,ʻike, a me ka iapaau ana

Sclerosing cholangitis - he maʻi o ke akepaʻa bile ducts ma i kā lākou mau pā pōhaku maʻi li nui huli no. I ka hopena o kona kumu i keʻano o ka hanaʻana sclerosis, m. E. hope me ka me ka makaʻu no'aʻaʻa. Kēia pathologyʻAʻohe causal pilina me nā ake maʻi, akā, pinepine hele aku ai i ke ano o ka complications mai keia kino. I kēia lā i ka 'atikala, mākou e ke kumu ulu sclerosing cholangitis hoomaopopo. Symptoms a me ka lapaau ana i ka maʻi, e e imua no hoi i kou noonoo.

anatomical pili

Bile mea nui i ke keʻena o ka digestive kaʻina. Ua ua komo i loko o ka hālāwai hope o nā bipi kūpaluʻia, maoli i ka ha awina o pancreatic nā'ūhū a stimulates peristalsis. Bile noke paka ake keena - hepatocytes. No ka lā, e like me ka hopena o ko lākou mālama nui hana ua loaa ia ma kahi o 1 hano o ka wai. Ma hope o ia, i ka bile komo ka bladder, a me ka duodenum.

Outflow secretion i hoʻonohonoho 'ia ma kūikawā ducts. E like me ka mea, e hele mai i loko o intrahepatic a me ka extrahepatic ke kaumaha ma muli o ka wahi. E like me ka hopena o stagnant keʻano o ka hanaʻana, anal o pathogens a me nā kumu, nā ducts i lilo i wela ai. I ka Ia manawa kamailio e pili ana i ka hooulu ana o na maʻi like cholangitis. Pathological kaʻina mau mea he okoa etiology. No laila, ka mea, ua noho kaʻawale i kēia? Ueony:ʻawahia, mea koʻohune, helminthic, sclerosing. Hope i ka loa pohihihi, akā, ua wehewehe aku ma ka loa.

Sclerosing cholangitis maheleia i loko o nā 'ano apau loa: iniiaiie a me nā haumāna. Kēlā me kēia no ia ua wehewehe aku ma kekahi mau 'kau o symptoms a me ka papa. Ma ka hihia mua ia o ia hoʻi, he maʻi maʻi i ka pu ma ka congestion o ka bile , aʻaʻole purulent li nui ducts, i ko lakou make mau loa a me ka hope ma connective'aʻaʻa. Secondary palapala pathology e hoʻomōhala ana i lalo o ka hana o kaʻawahia waiwai. Ma pohihihi keia hoopii, kona hanana ua kena ae la ia e lawa koko lako. Ma kēia 'atikala e kālele ana mākou i loko o oi au mamuli o ka iniiaiie Lolina o ka maʻi.

Pōkole Description o ka maʻi

Helu sclerosing cholangitis ua hoʻolaha like pohihihi keia pathologies o ka biliary nenoaiu. E like me ka mea ana helu ikepili, ka mea, ua diagnosed i loko o kekahi i eha kanaka no 100 tausani heluna. ʻano papa hana o ka? Acaeoey o ka maʻi ho'ēmi i kā keʻano o ka li nui i loko o ka liʻiliʻi hepatic ducts. Pela ka mea, he poe paakiki, o ia. I nā 'ano a me ka ino kaha ma i bile kahe ana i loko o ka Oe. Stagnant keʻano o ka hanaʻana pili i ka intercellular makahiki o ke akepaʻa, kūpono ma ka cirrhosis.

A hiki i ka pau ana o ka hope kenekulia ka mea, ua hiki i ka diagnose i ka maʻi ma hope oʻoki kino a autopsy wale. Mahalo i ke kūpono 'ana o ke lapaau i keia maʻi hiki ke' akomi i nui mamua. A hiki i ka nui loa susceptible ia mea e na kanaka kahiko, 25 a hiki i 40 makahiki. Mau palena i loa conditional, no ka mea, i ka maʻi hiki e asymptomatic no ka lōʻihi manawa. I kekahi manawa, na symptoms o ka li nui kuhihewa no autoimmune maʻi, ulcerative colitis a me cystic fibrosis.

Nā kumu o ka cholangitis

Ke mau kumu o ka maʻi i IKE OLE IA. Kauka kaʻawale pae o nā kumumea e hoomahuahua i ka likelihood o kona hanana. I waena o ia mea:

• aaiaoe predisposition;
• Mea hoʻomaʻi ha awina i loko o ke kino;
• propensity i autoimmune illnesses;
• waiū i kaʻawahia waiwai.

I waena o kēia mau kumumea ua haawiia makakoho aaiaoe maomeka. Tangible ike maopopo ana i keia mea, he mau haʻawina lehulehu o ka maʻi i waena o ka 'ohana.

lapaʻau kiʻi

Ma ka maʻi no na makahiki i e asymptomatic a me ka mehana symptoms. Nā mea maʻi pinepine hiki ole ke olelo pono ia ka meaʻikeʻia e hoike ana i sclerosing cholangitis symptoms. Pathology ua ana 'akomi i ka iho e ike i kekahi kauka e pili ana i ola pilikia' ē aʻe. I ka manawa o kaʻike, hoikeia mai i ka hoailona mua o ka maʻi - mahuahua holo 'awelika o hepatic nā'ūhū.

E like me ka maʻi progresses, a me ka lapaʻau kiʻi hou. I waena o kona papa kuhikuhiE symptoms o ka eia pono e kahiāuli.

• luhi, ikaika sleepiness;
• ilihune ikaika loa ka makemake;
• yellowing o ka mucous membranes a me kaʻili;
• e hoohaunaele ana i ka mahana e subfebrile nā loina;
• achingʻeha ma ka akau subcostal wahi, hiki aku i ka ai a me ka'ūhā mua;
• maneo;
• mau xanthomas;
• discomfort ma ka hema maluna quadrant, mai ana i ka hoʻonui o ka spleen;
• hoʻokāʻoi pigmentation o ka ili.

I kekahi manawa, iniiaiie sclerosing cholangitis pu me hoʻoʻino na naau oʻu maʻi. Mau nā ulcerative colitis, Crohn ka maʻi.

ki ina hana like o kaʻike,

Inā e manao i ka maʻi e koke imi kōkua mai i kekahi kauka. Ka ninaninau ana i ka hoʻomanawanui hoʻomaka me ka hoʻopaʻa 'ana o kona mōʻaukala, a me ka hoopii iniiaiie symptoms. Ma hope iho o ia, ke hoomau aku i ka physical ninaninau. Ke hoomanawanui i e scratches ma luna o kaʻili, loa jaundice. Palpation ua ana i ka mahuahua ana o ke akepaʻa a me ka spleen.

I mea e hōʻoia i ka ka muaʻike, a hoouna aku la no ka hou ninaninau i ka hoʻomanawanui. Ua nā nā kēia mau hana:

• koko ho'āʻo (ma ka oi o nā hoailona o leukocytes a me ESR Hōʻike li nui);
• Abdominal ultrasound;
• elastography ake (e leie aku i ka manaʻo kino elasticity);
• retrograde cholangiopancreatography (radiography hoʻohana Akä naÿe);
• koko biochemistry (i loko o iniiaiie sclerosing cholangitis malama excessive ake nā'ūhū);
• MRI;
• Ake biopsy (i kēia hana o ka noiʻi kōkua e kuhikuhi i mau mea o ka fibrosis).

Kēia mau kiʻina hana ae i ke anamanaʻo e hōʻoia i ka iniiaiie sclerosing cholangitis. ʻike, no ka maʻi i kōkua ho oholo i ka oolea o ke pathological kaʻina. I huina, he eha:

1. Portal. Ua Ua wehewehe aku ma keʻano o ke puffiness a me hepatic fibrosis ducts.
2. Periportal. Symptoms o ke kahua mua i complemented e ka oi haʻi fibrosis a me ka luku aku keʻano o ka hanaʻana ducts.
3. Septal. Ma keia kahua o ka maʻi he mea loiloi mua hoailona o ka cirrhosis.
4. Cirrhotic. Wehewehe aku ma ka piha-fledged kūpono 'ana o biliary cirrhosis.

Ma muli o ka hopena o ka luna 'nana ke kauka prescribes Inc.

lapaʻau Nā Kūlana

Inc i loko o kēia maʻi ua nona ma hopu ana i ka hoʻoʻino kaʻina hana, i ka loaa o ka bile pele a me ka detoxification o ke kino. No keia hopena, ka makeʻe kulana a me ka operative ano o ka lapaʻau ia i loko o kēia lāʻau lapaʻau. Ma ka hihia mua o ia hoʻi, ka lapaʻauʻia a me ka adherence i ka ikaikaʻai. ʻoki kino ua hōʻike ma ka loa hoopii, ka wā makeʻe kulana kanaka ke aloha. Koho ana o kekahi mau ano o ka lapaʻau mea i ai i ka kauka.

I ka hoʻohana 'ana ai'

Ke kaumaha ma muli o ka oolea o ka maʻi, ka mea hiki ke hāʻawi i ka moe koena, a hoʻokoe i kekahi hookoikoi. Inā he hoomanawanui ua hopohopo i ka nui eha, oia hoakaka antispasmodics ( "No-Spa", "Spasmobru").

E pau ana i ka hoʻoʻino kaʻina kōkua i ke kēia mau ai ':

1. Immunosuppressants ( "Azathioprine"). Ka mea, inhibit i ka ha awina o ka'ōnaehana paleʻea nenoaiu.
2. Antifibrogennye 'o ia hoʻi. Lākou ka papa kuhikuhi 'ana ua nona ma ka hoʻopau o ka fibrosis, a me ka Kāohiʻana o ko lākou hou? Acaeoey.
3. Glucocorticosteroid hōmona ( "Prednisolone"). Ka mea, kōkua emi li nui.

Ke hoʻohana i kēia mau lapaʻauʻia e leie aku e lanakila i ka loiloi mua kahua o ka? Acaeoey o iniiaiie sclerosing cholangitis. Symptoms o ka maʻi pinepine ole ke alakaʻi maʻamau ola no nā mea maʻi. Itchy ili, digestive'āpana pilikia a me ka dyspepsia - a pau kēia mau 'aʻe' i ka hopena maikaʻi ma luna o lākou ola. No ia mea, aiiieieoaeuii hāʻawi symptomatic Inc. Ua nā loaa hepatic ( "Essentiale"), gastric nā'ūhū ( "Creon") a me ka lapaʻauʻia, e hoʻopau maneo. Ai 'i mau wae pākahi, e lawe i ka mooolelo o ka pono lapaʻau kiʻi, a me ka hoʻomanawanui ka kulana.

ʻai Hiʻona

Nā mea maʻi i anao? Aou ia mana "papaaina helu 5". Ka wā o kēiaʻai e kaupalena hokii o ka momoma, palai a me spicy mau kiaha. Animal kona kaikea a mea e ahoʻia e puku i ka mea kanu. Eia hou kekahi, ia mea pono e loa hoʻopau mai i kaʻai Hauʻoli La a me ke ono loa, i hua hua a me ka hua, kokoleka, ka waiʻona, ai a me marinades.

Ae ua haawi e hoʻohana wīwī ai / ka iʻa, i kekahi mauʻano o ka berena, porridge ma luna o ka wai. Oe e hoi ai haleʻuwī waiū huahana, ka meli, nulu'Īkalia Nā Kopa nō kai.

A hiki i kaʻike, o "iniiaiie sclerosing cholangitis" lapaau me ka lapaʻauʻia, aʻai haawi i ka maikaʻi hopena wale nō i loko o ka loiloi mua ke kahua. Inā keia manawa ua nalo ana, ka mea, e hoopai auaneiʻoki kino.

ʻoki lāʻau lapaʻau 'uao

Makeʻe kulana therapies hoʻohana 'ia i loko o uncomplicated kinona o pathological kaʻina. ʻO ka 'eleu pili i ke kauka' aʻole e mau haawi aku i ka maikaʻi result i loko o ka hana o hope Inc. I ka iapaau ana me ka ai 'aʻole e alakai i ka normalization o ke ano a' aʻole e hoʻihoʻi maʻamau pono o ka bile, ma laila iʻoki lāʻau lapaʻau 'uao.

I kēia lā kauka makemake endoscopic hana. Ka mea, paipai ana a pau manipulations ma incisions liʻiliʻi i loko o kaʻili. Eia naʻe, e like ke kaʻina hana i loko o ka hapanui o na hihia e haawi aku i ka pōkole-kau kanawai, a ua fraught i complications. I hoʻomaka hoʻonui dilatation a me ka stenting ducts. Iloko o ke kaʻina hana, ke kahuna lapaau Hoʻonui i ka pono o nā kaha o kūikawā nā paukūʻolokaʻa a me nā pūʻulu i ka hei, pale ia mai ka hou. Inā he mea ia e hemo aku sclerosing cholangitis, ake transplant lapaʻau 'o ia hoʻi.

hiki complications

I ka maʻi ua wehewehe aku ma ke kali pele. Ua pane ai poorly i Inc, a me ka nui o systemic hoike ana aggravates wale nō ke kaʻina. Mawaena o ka loa, he pono ole complications ona oia no na kēia:

1. Komo Nā hypertension. Kēia pathology ua pu ma ka mahuahua ma ka puʻe i loko o ka hepatic koko. Kona papa kuhikuhiE hoike ana ua noʻonoʻo ascites.
2. Cholestasis maʻi pale. E kū'ē i ka backdrop o ka poe paakiki, o ka bile ducts i nā taper i loko o kā lākou mau kea-hihia. Kēia wehewehe i ke ano o ka jaundice a me ka pruritus. E like me ka Holomua o ka maʻi lumen narrows nui a me ka oi. Steatorrhea i, i ua pu ma osteoporosis.
3. Mea koʻohune sclerosing cholangitis akepaʻa.
4. Maʻi pancreatitis.
5. Holangiokartsionoma (ʻeho bile ducts).
6. Cholelithiasis.

Oia complications ana i loko o ka 3-4 kahua o ka pathological kaʻina.

I ka olelo wanana a me ka Kāohi ana

Helu sclerosing cholangitis ua hoʻolaha like lohi i holopono nō maʻi. Kona hopena ma ka hapanui o na hihia mea maʻi ake ole. Ālai 'worsen ka prognosis mua makahiki o ka hoomanawanui, imua o concomitant pathologies o ka naʻau liʻiliʻi, ka hanana o complications. Nō kāu, a me ka helehelena o ka loiloi mua na hoailona o ka pau mua o ka kahua hope kŰlń ao mai ka 7 a hiki i 12 makahiki.

Ua mea hiki ke pale aku i ka iniiaiie sclerosing cholangitis? Reviews o nā kauka e olelo aku ia ma muli o ka lawa ole study o kekahi Kāohiʻana o ka maʻi i ole, ua ulu.