Ola kinoMaʻi a me nā kūlana

Maʻi demyelinating polyneuropathy: hōʻike, ano, kumu, symptoms a me ka lapaʻau

Demyelinating polyneuropathy - loa maʻi i ka pu ma ka li nui o ke aʻalolo kumu a me ka holo loa ia'na o ka myelin wahī. Me ka pono a me ka 'eleu hana o ka lapaau ana i ka maʻi hiki ke eliminated e pale loa hopena. He nolaila, nui i ka ike i ka papa kuhikuhiE kumu a me symptoms o ka maʻi, i ka manawa e ike i ke kauka.

He aha ka maʻi? Overview

Koke ia mea kumukuai 'ana i kumumanaʻo i ka maʻi mea pohihihi keia - 100 tausani kanaka 1-2 wale e ae mai i ka like maʻi. He nui prone i keia maʻi makua kane, eia nae i keʻalo me ia i kaʻike, na wahine a me na kamalii. E like me ka rula, demyelinating polyneuropathy pu ia e kekahi symmetrical lesion o ke aʻalolo aʻa, kūpono ai i loko o ka ulu nawaliwali o ka distal a me ka proximalʻaoʻao nāʻiʻo. Ma ke ala, he pinepine, i ka maʻi ua pili i Guillain-Barre maʻi pale. A hiki i kēia lā ka mea, he mea ike ole ia, ina paha maʻi hoʻoʻino demyelinating polyneuropathy, he kaawale maʻi 'ole kekahi' ano o ka hua symptoms.

I ka papa kuhikuhiE kumu o ka maʻi

Eia naʻe, i nā kumu a me nāʻano papa hana o ka? Acaeoey o ka maʻi a hiki i ka lā ua,ʻaʻole iʻikeʻia a hiki i ka hopena. Aka hoi, ua hōʻike loa-manawa haʻawina i hoʻoʻino demyelinating polyneuropathy - he autoimmune maʻi. No nā kumu, nā'ōnaehana paleʻea nenoaia hoʻomaka e loaa i ke kino ka mau keena like haole, kūpono ma ka hana kekahi lāʻau lapaʻau kino. Ma keia hihia, mau antigens hoouka nā aʻalolo aa'aʻaʻa, e kauoha ana i ka make ana o ka myelin wahi, ma o na la li nui. Alaila, na nä olonä lilo lākou walaʻauʻana waiwai, e hiki aku ai i ka hoʻohuikau 'o ka innervation o nāʻiʻo a me kekahi mau nā loko.

Ma keia hihia, like me ka aneane kekahi'ē aʻe autoimmune mai, aia no he aaiaoe hooilina. Eia hou, ma laila nō i ka helu o nā kumumea i ke hoololi i ka'ōnaehana paleʻea nenoaiu. Mau nā metabolic a me ka hormonal ka hoʻohuikau ', loa kino ai a me ka mea naʻau stress, trauma, ikaika stress, loa maʻi, maʻiʻaʻai o ke kino, vaccinations,ʻoki kino.

Demyelinating polyneuropathy: Mea Maluna

Ma ke kālā no lapaau, loaʻa nō kekahi mau ano o ka Mea Maluna o ka maʻi. No ka laʻana, ke kaumaha ma muli o ka hihia, kaʻawale allergic, traumatic, hoʻoʻino,ʻawahia, a me kekahi mau ano e ae o ka maʻi. E like me ka Pathomorphology ke hoomaopopo iho demyelinating a axonal polyneuropathyʻano.

Mākou E hoi kamailio e pili ana i ke ano o ka maʻi.

  • Huʻi demyelinating polyneuropathy e hoʻomōhala ana i koke - ka sensory a me ka Hawaii kāna hana hoʻomōhala no kekahi mau lā a me ka pule.
  • Ma subacute ano o ka maʻi ua ole e ulu ana i hoʻomaka koke, akā, kŘpa a koke - mai i kekahi mau pule i eono mahina.
  • Maʻi polyneuropathy ua noʻonoʻo i ka noho pilikia loa, no ka mea, hiki hoʻomōhala hunaia. Holomua o ka maʻi hiki hope no kekahi mau makahiki.

I ka papa kuhikuhiE symptoms o ka maʻi

Ka lapaʻau kiʻi i loko o ia mau maʻi hilinaʻi nui ma luna o na mea he nui aʻe, me ka palapala o ka maʻi, a me ke kumu o kona ulu ana, maikai ahonui, a me kona mau makahiki. Demyelinating polyneuropathy, i hookuu i ke kakahiaka nui kahua o ka hoʻonaʻauao ua pu ma ka Muscle nawaliwali, a me kekahi mau sensory haunaele. No ka laʻana, e hoomanawanui i kekahi manawa, ohumu o ka hoemi pā lonoaʻili i loko o na lala, e aa ana ka waiʻona ma a me ka tingling. No ka mea huʻi ano o ka maʻi wehewehe aku ma ke ano o ka ikaika girdling eha. Akā, i ka wā e hele mai i ka maʻi e make ai o ke aʻalolo aʻa, ka eha hiki ole paha eʻoi aku haʻi, a me kahi e loa.

Ma paresthesias o nāʻaoʻao hou me ke kaʻina progresses. Ma ka nana oe, e hai i ka emi a me ka wa e kaawale aku o tendon reflexes a me kā lākou piha nalowale. Loa pinepine ka mea, ua ka demyelination kaʻina uhi nā aʻalolo o ka lala, akā, he mea hiki pio'ē aʻe nā aʻalolo. No ka laʻana, kekahi e hoomanawanui i ohumu o numbness o ke elelo, a me ka wahi a puni o ka waha. Loa emi pinepine malama lani paresis. Ma keia wahi, i ka hoʻomanawanui mea hiki ole ke ale wale iho i ka ai a me kou tuha.

Axonal-demyelinating polyneuropathy: Kind a me Symptoms

I ka lukuia'na o axons mea i hookuu, kena ae la ia ma kaʻawahia ia ma luna o ke kino. Axonal ano o ka maʻi ua maheleia i loko o kekahi mau kumu ano:

  • Huʻi polyneuropathy i loko o ka hapanui o na hihia ua kena ae la ia e loa kaʻapu kōheoheo meaola (e laʻa me, he'okesaside o arsenic a me nā pilikia toxins). Symptoms o kāna hana o na ko mākou hopohopo'ōnaehana hōʻike 'ano koke - ma hope o 14-21 lā o ka hoʻomanawanui hiki ke ike paresis o lalo, a me luna lala.
  • Subacute palapala o ka maʻi hiki no ke kena ae la ma kaʻapu kōheoheo, a me ke koʻikoʻi metabolic malfunction. I ka papa kuhikuhiE symptoms ke hoʻomōhala no kekahi mau pule (kekahi manawa, i ka 6 mahina).
  • Maʻi axonal neuropathy e hoʻomōhala ana i lohi, i kekahi manawa i ke kaʻina hana i oi aku mamua o elima makahiki. IeAUPIIe, IAa IO, keia palapala ua pili i ke alo o aaiaoe predisposition, e like me hooloihi ae i intoxication o ka meaola (ʻaʻohe mea, no ka laʻana, i ka maʻi alcoholism).

ki ina hana like o kaʻike,

Wale i ka hoao ana i kauka hiki diagnose "demyelinating polyneuropathy." ʻike, no ka maʻi - he luna 'kaʻina hana, i ka loaʻa o he mau o ka Naauao. E hoʻomaka, e oaeouee? Physical hookolokolo a me ka ohi ana o ka loa piha mōʻaukala. Inā ka hoʻomanawanui i sensorimotor neuropathy mea e hoʻomōhala ai ole emi malalo o elua mahina, a laila ia mea he kumu kūpono no ka hou pololeiʻike.

Ma hope, e like me ka rula, ma lalo o hou hoʻokolokolo 'ana. No ka laʻana, ana o nā aʻalolo conduction māmā holo o impulses a ka Hawaii nā aʻalolo ke ÷ ike i ka ho'ēmiʻana i loko o ka papa kuhikuhiE nā hoailona. A ma ke keʻena hoʻokolohua study o cerebrospinal loli mahuahua pae kumuʻiʻo malama.

He aha lapaʻau e kaumaha ana kēia lapaau?

A Inc e noi mai ana demyelinating polyneuropathy? Lapaʻau ma keia hihia oia o kekahi mau anuu, oia hemo ana o ka li nui, ka suppression o ka'ōnaehana paleʻea'ōnaehana ha awina a me kākoʻo hopena.

Ma exacerbation o ka li nui, a me ka alo o nā mea maʻi ikaika hoakaka hormonal Anati-hoʻoʻino ai ', oia hoi corticosteroids. Ka loa ka hoʻokō ka "Prednisolone" a me kona analogues. Inc hoʻomaka me ka mahele lāʻau kiʻekiʻe, a emi like me ka nalowaleʻana o nā symptoms. Nō kāu, Muscle ikaika Ka hoʻomaka 'ana e hoʻi hou mai ma hope o kekahi mau pule. Akā, e pono ke kūʻai 'ana i kumumanaʻo i lōʻihi-makahiki hoʻohana ana i ka lāʻau' ia ke alakai i ka meaʻaoʻao ole.

Hoʻomanawanui iki mai me ka maʻi maʻi e pinepine paipai i ka plasmapheresis, i haawi maikai hopena, a hiki loaʻa ke kala. No hoi, ka lawelaweia ana hoʻomanawanui iki mai ai 'e hiki inhibit i ka ha awina o ka'ōnaehana paleʻea'ōnaehana - e lawe lākou i nā papa no ka aneane i ka wā e ola ana. Kekahi o nā 'ana i kūpono hou o kēia Inc mea intravenous immunoglobulin.

Ke prognosis no nā mea maʻi me ka polyneuropathy

Ka hope o keia hihia hilinaʻi nui ma luna o ke kino o ka maʻi, ka pono o ka lapaʻau, e like me kekahi o nā 'ano kanaka o ka meaola. No ka laʻana, he kanaka me ka huʻi ano o ka maʻi, a koke ae la i ka pono lapaʻau, e ae mai oe i ka hopena o ka maʻi he nui maʻalahi. A ina he piha koi hiki ke loaʻa maʻaʻole loa hoʻi e mau ana, he nui loa nā mea maʻi e hoʻi i ka maʻamau ola.

Akā, maʻi demyelinating polyneuropathy, a hoʻomōhala i ka lohi, a ma luna o kekahi mau makahiki, ke alakai i ka irreversible poino i ka'emi'ōnaehana, kīnā o ke kino, a like ka make. Ma ke ala, ka maʻi hoi Ka hali 'ʻelemākule e hoʻomanawanui iki mai ka hapanui loa.

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