Ola kinoMaʻi a me nā kūlana

Maʻi pale elongate kau QT: hōʻike, hiki kumu a me ka lapaʻau 'ano

Kanaka Health - i ka papa kuhikuhiE ke keʻena o ka mea maʻamau a me ka mea e like ai ke ola. Akā mākou e i mau manao ola. Pilikia e ala mai no kela kumu, a me kā lākou mea nui hiki no hoi e kekahi. No ka laʻana, ka mea, he pono ole anu, aole ia i kanaka ka mea e hopohopo nei i, ka mea i koke ia, a 'aʻole ole i oi aku ka lilo nui nohona ola. Akā, inā pilikia ka haohao ana i ka mea na nā loko, ia mea oi pilikia no ke ola a me ka paʻa impairs mākou maikaʻiʻana.

Nei, he wahi lihi iki o ka poʻe hoʻopiʻi naau pilikia, a o ka hapanui pinepine ia mea maʻi, he pono ole i ka mea oluolu i ka pono a me ka diagnose. Akā, he mau manawa, i ka wa o ka hoʻomanawanui ua 'akomi i lōʻihi QT maʻi pale. Ma lapaau, i kēia manawa o ke 'a loaa ana o ke kanaka, me ka hoomahuahua i loko o ka lōʻihi like' ole o ka ECG wā mawaena Hoʻohana. A me keia maʻi pale ua wahi wale elongation o ka oi ma mua o 55 HI mai ka maʻamau nā loina. Ma ke aha ka wā o ka maʻi e hoʻomōhala ai, indices o haiahū kūmau o ka wā mawaena paha e oi aku mamua o 440 MS.

hoike ana

Ma ka hapanui o na hihia, ke hoʻomanawanui i ka maʻi mea asymptomatic a me ka hoʻoponopono '-hoike ia mea aneane hiki ole i. I mau, hoohaumia i kanaka me kēiaʻike, a me ka repolarization depolarization ma muli o ka loli ma symmetrical innervation o ka naau. Hoʻomaopopo 'mea hiki wale nō i loko o ka papa o ka hoʻokolokolo' ana i, ma ke kumu o ka lako a pan o nāʻano likeʻole. I ka papa kuhikuhiE ololi ka hoʻopukaʻana i kēiaʻano mea uila instability o ka naau Muscle.

People ka poe i he elongate kau QT maʻi pale ma ineffective lapaʻau ai kona wa e kaawale aku hiki hoʻomōhala ventricular fibrillation a ventricular tachycardia. Mau complications ua ikaika nui ae pilikia no na ola o nā mea maʻi, a halihali i ka lilo o ka mea mau moku'āina. Nolaila, ina e manao i ka alo o ka maʻi e koke lawe malama i kou ola, i ole oe e i hewa hopena. Eia hou, na complications o keia maʻi mea he nui. Ka mea hiki ole ke alakai wale i ka malfunction a me ka mea hōʻemi o ka hoʻomanawanui ka mau moku'āina o ke ola, akā, i ona.

ano

Ma lapaau ka mea, ua lōʻihi? Anoee ia haiahū kūmau, a ma luna o nā makahiki o nā kānakaʻepekema kahu ai, e aʻo e pili ana i ka mea hou. I ka maʻi ua maheleia i mau hoailona ia mea,ʻo ia, a me ka loaa congenital lōʻihi QT maʻi pale wā mawaena. Kau mea 'ano o ka hoomanawanui, hiki wale nō noiʻi hana. I ka congenital kāna hana o ka pilikia a me ka ole o ka aaiaoe kivila. A hiki ke kūʻaiʻana ma luna o ka ulu ana o ka maʻi hiki ke loli ma ka likeʻole aʻe.

shape

Kekahi pee no kekahi mau 'ano o ka maʻi.

  • Latent palapala. Ua Ua wehewehe aku ma ka maʻamau wā mawaena nā hoailona i ka hookolokolo, a me ka mea mua hoouka o syncope mea he makeʻana.
  • Malama bouts o syncope, akā, i ka wā mawaena QT ua i ÿö i ka manawa o ka nana.
  • Elongation kaʻawale wā mawaena, a ua ole lewa i loko o ka mōʻaukala.
  • Syncope ana me ka elongation inideka QT, e oi aku ka uku o 440 MS, a ma luna.

kumu

He nui aʻe hiki ke loli i ka hooulu ana o keia maʻi. No ka laʻana, ka mea i hoʻomaka e hoʻomōhala ma muli o ka maʻi hereditary me maʻi pale P-U. Ma keia hihia loa pinepine i ka poho o ka ike paka i ke kāʻili 'ana nae e alakai ai i ka ulu ana o ka maʻi. Nō hoʻi, E-P-A maʻi pale, ina o ka hoʻomanawanui i ka congenital pepeiao kuli. He aha ka ke kumu o ia i kekahi me ka hui pu ana o symptoms, a pehea ia triggers ke kūpono 'ana o ka maʻi, ua loaʻa mai ka noiʻi ai mamao nele. Nō hoʻi,'ōewe mutation hiki i ke kūpono 'ana o ka maʻi. 'O kēia ka papa kuhikuhiE kumu o congenital maʻi, akā, i loko o kekahi hihia ia mea,ʻaʻole koke mai, a me he kanaka makua, ma hope o pilikia stress. I hookuu ia o ka pilikia a me ka hoʻololi kemikala o nā polokina ma ka paʻakai, a potasiuma kaha i kumumea i hoonaukiuki elongate QT wā mawaena maʻi pale. Ke kumu i moe i loko o kaʻaoʻao ole o kekahi mau laau. Hapanui hoʻoweliweli, ua ikaika antibiotics i ka hoʻomanawanui hiki ke lawe i ka hana 'ē aʻe ka maʻi.

Hiki i maʻi ai metabolicʻai e ho'ēmi i calories i loko o kaʻai. Depletion o ke kino i loko o kēia mau wahi, i hiki ke ke lewa ole wale i loko o ka naʻau. Nolaila, e like me kaʻai mea maikaʻi, e negotiate me ke kauka, a mālama ma lalo o kona hooponopono. Attrition ke alakai i complications o kekahi mau mea'ōnaehana mānowai koko maʻi e like me coronary naʻau maʻi a mitral kiwikā prolapse. Maʻi pale kekahi manawa e hoʻomōhala ana i ka manawa i CNS pathologies a me vascular dystonia a me ka 'ē aʻe kāna hana o ka autonomic ko mākou hopohopo nenoaiu.

symptoms

Aia i kekahi hana mana e hōʻike ana i ke ahonui o ka noho lōʻihi QT maʻi pale. Symptoms o kēia maʻi nā:

  • Loss o ka ike paka i ka loihi mai kekahi mau minuke i ka hapaha o ka hora. Ma kekahi mau hihia, he pepehi hiki hope mai i ka iwakālua minuke.
  • Convulsions ma ka synoptic olelo e like epilepsy ma ka nānā aku, akā, na keʻano o ka hanaʻana i kāhea ia i loaʻokoʻa.
  • Koke nawaliwali ma ke kino, me he poeleele hoi o na maka.
  • Palpitations a hiki i ka wa e kaawale aku o ke kino ai 'ole mea naʻau stress.
  • Umaumaʻeha o kekahi ano, hoʻomau ka wa hookeai Kal, e like me pū ia maʻule hou ihola nō paha pōniuniu, a numbness i loko o na lima a me na wawae.

lapaʻau '

Loa pinepine, lōʻihi QT maʻi pale, i loko o nā mamo o ka oi aku,ʻaʻohe symptoms. Ma keia kulana, i ka hoʻomanawanui i haha loa ola a me ka make koke. Nolaila, ina he kanaka mea ma pilikia o ka maʻi, e pono e mau hookolokolo aku la ia ia e kekahi kauka, e alii ai maluna o mai i ka manawa kūpono o ka ulu i ka maʻi. E diagnose i ka maʻi, ke kālā no lapaʻau hoʻohana mau ki ina hana like.

Inā he mea e hoʻohuoiʻia i ke ahonui a me ka lōʻihi QT maʻi pale ola pilikia maopopo hōʻike i kēia, i ka electrocardiogram - o ka mea nui study i Hōʻike maʻi. Ma ia ia i loko o ke kaua, ke hui pu ia lakou, e hoike aku lakou i na hoailona o ventricular tachycardia, Eʻoi mai ana i loko o ventricular fibrillation. Kēia papa hana o ka iniiaiie ano o ka maʻi i loko o ka paa.

Aia ka hoi kekahi ao e hōʻike he elongated wā mawaena maʻi pale QT. Ua Ua lawe mai i ka lā. No laila, ka mea, ua kapaia o ECG ka mālamaʻana. Ka like apono 'e koho i ka hoʻomanawanui i ka cardiac haʻawina i kēia wā. I kona kino, hoopili uuku ka manaʻo i ka mooolelo o ka hoike ana o ka naau, a ma hope o kona wehe 'ana, he akamai hana i deciphering ka hoʻopaʻa' ikepili kūlana kiʻekiʻe. Ka mea, ae oe e ike ai i ko ke hoomanawanui i ka wi bradycardiaʻoʻoleʻa, ina paha na loli o ka morphology o ka T nalu, i pono like, ina paha he mea he 'aʻe' ana i ka keʻano o ka hanaʻana o myocardial repolarization a ventricular premature kui iho oe a.

lapaʻau

Inā ka hoʻomanawanui i ua hōʻike 'loa QT maʻi pale, lapaʻau e e hulina, a kūpono, no ka mea, ka mea wale ala, e pale aku i ke kūpono' ana o nā complications i mea pilikia loa i ka ola, a hiki i ka lawe lethal hoʻokūkū.

lāʻau Inc

Ka maʻi hiki ke hoola iho la hoʻohana antiarrhythmic ai '. Pono i koho 'inikua papa e ole wale hoʻopau i nā symptoms o keia maʻi, akā, no hoi no ka hou wā e stabilize i ka mea'ōnaehana mānowai koko nenoaiu. 'O kēia kekahi o nā kiʻina hana, e hoola i ka congenital maʻi pale o elongated wā mawaena QT LQTS.

ʻoki lāʻau lapaʻau lapaʻau

Inā ke hoʻomanawanui i ka pilikia o ka pilikia a hiki i ke ola ma muli o ke arrhythmias i loko o kēia maʻi, mākaukau Paipai 'e kanu pūʻia i ka pacemaker. Kona 'oihana ka mea e normalize i ke alapine (frequency) o contractions o ka naau Muscle. Hoikehonua, lapaau Ua ulu he kūikawā manaʻo, a hoʻoholo i ka pathological haiahū kūmau o ka naau. Ka maʻi hiki ke kauoha mai ka waho. Ma hoʻokō ', no ka mea hoike, i ka mea e ole pane. Akā, inā i ka lāʻau ikiʻai wale nō e kaʻikaʻiʻia e ka pathological ano, ka mea normalizes ke kino hana.

Ana ma na maʻi like elongated QT wā mawaena maʻi pale, noonoo ole a me ka maluhia kupono. Pacemaker ua paa i ka hema o ka pectoralis nui Muscle. Mai ka mea, i nā uila aʻa lolo e surgeons hoʻopaʻa ma ka makemake wahi, ana nō ia ma ka subclavian aa koko. Ke i hoʻomākaukauʻia hiki e like ma ka programmer. Me ka mea e hiki ke hoʻololi i ka mea kiko'î o stimulation o ka naau, ke kaumaha ma muli o ka 'ano o ka hoʻomanawanui. LIKE, e hana kēlā manawa, i ka wa o ka hana ana o ka naau Muscle, e hele aku ma kēlāʻaoʻao o ka hoakaka kiko'î.

ka hopena

Ka maʻi mea i manawa e hiki i ka diagnose no ka mea, he kākaʻikahi hoike mai ai ia hōʻike. Akā, i ka mea ia manawa i ka hoʻoweliweli 'ana i ka hoʻomanawanui ka ola ka nui loa. Nolaila, ina he mea hiki kekahi hōʻemi iki pilikia o kona hanana, e e paa mau ana manaʻo, a kukakuka pu me ka poe akamai. Inā i kaʻike, ua hookupaa iho la ia, e pono e hulina a me ka piha hana o keia maʻi, no ka mea, hiki ke alakai i ka make.

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