Ola kino, Maʻi a me nā kūlana
Goodpasture ka maʻi pale: mea, lalau mai, Symptoms a me ka lapaʻau Nā Papahana
Goodpasture ka maʻi pale - he pohihihi keia autoimmune maʻi i ka pu ma ka hanauna o ka atypical nā mea'aʻaʻa e hoouka aku i ke keena o ka maʻiʻaʻai a me nā puʻupaʻa. Similar maʻi puleʻAmelika, e loli ai i na kanaka ma waena o nā makahiki o ka 12 a me ka 35 o kona mau makahiki. Ua Ua manaoio aku i kekahi mau hoʻomanawanui iki mai i ka aaiaoe propensity no ia i ka haunaele.
Goodpasture ka maʻi pale: na kumu o ka maʻi
O na papa, ke kanaka hoʻomanawanui i ka aaiaoe predisposition i ka maʻi. Aka hoi, eia nā kumumea i kāhea i autoimmune NaI.
Me ka hooulu ana o ka maʻi i ka'ōnaehana paleʻea'ōnaehana produces nā mea'aʻaʻa e hoouka mai i ka basalʻili lahilahi o na capillaries o pulmonary alveoli, a me kaʻaʻa puʻuwai tubules. E like me ka hopena o kēia kaʻina ua loli a ua moku hoʻi iaʻu capillaries, ma o na la kūloko ma kahe ana ke koko, a pili symptoms.
No ka mea manawa mua ia i ka maʻi, ua hoʻopaʻa 'ia ma 1919. Akā, i kēia lā ka mea, uaʻikeʻoleʻia ua mea triggers ka'ōnaehana paleʻea pane. Ua Ua manaoio ia Goodpasture ka maʻi pale ua pili me ka infectious maʻi. I kekahi manawa, i ka ho'ā hope o ka maʻi, kena ae la ia e kekahi Nine Inch, a hoomake iho no hoi. Ua hoʻopaʻa pepa paʻi kiʻi mau hihia ma i ka maʻi pale hoomaka ae la e hoʻomōhala ma hope o ka lalau ka lapaʻauʻia.
Goodpasture ka maʻi pale: symptoms
Nō kāu, o ka mua symptoms o ka naehana nenoaiu. Ke hoomanawanui complains o ka umauma eha, pinepine cough a me ka pokole o ka hanu ma exertion. E like me ka hemoptysis hoomaka me ke kūpono 'ana o ka maʻi. ʻO ia maʻiʻaʻai ke lohe i ka wai a maloo maʻi o. Ke hoomanawanui i 'ike mau luhi a me ka drowsiness. I kekahi manawa, he mea ka hana keaka kaumaha poho no a hiki i ka emi ana ma ka Muscle nuipa a. Kue i ka mahaloia manaoio, na capillaries ma na maka i ole loli ana e ka maʻi.
No ka mea, he nunui uuku hemorrhage, ka mea e hiki mai ana symptom - ia ka maʻi anaemia, a anaemia. Inā e huli i ka hoomanawanui, ka mea hiki ke ike i kona ili, he lenalena. Aia ka cyanosis o ka mucous membranes. Ma kekahi mau hihia, haanou ana o ka maka hōʻike. Ka wela ua nui mahuahua.
Hoailona o ka maʻi i loko o nā puʻupaʻa hōʻike iki ma hope. Oe e hai i ke koho ana o ka uuku nui o ke koko i loko o ka mimi. ʻaʻa puʻuwai ole progresses hoʻomaka koke, a ua ukali ia e kona mau symptoms.
Goodpasture ka maʻi pale: PalekanaEND_LINK ki ina hana like
I mea e hana i kaʻike,, ke kauka pono akahele nana i ka hoʻomanawanui, e ike i ka hopena a me ka ECG ho'āʻo ma. I mau, hiki ke ike Ka Ikepili o ke koko hao deficiency anaemia , a mahuahua leukocyte helu, mahuahua ESR. Urinalysis huai ae mimi ma ka nui dala o ka kumuʻiʻo a me kaʻulaʻula koko keena. Oe E maopopo leʻa noiʻi ana i ka sputum, e like me ka mea ua i loaʻa ula koko keena. E e pono keia mau mea a me ka spirography e kōkua huai ae aʻe 'ana o ka mawaho ka hanu. Hāʻawi aku no hoi ECG study o ke koko kinoea, m-kukuna a me ka biopsy o ka poino'aʻaʻa, aʻo ka mea e hiki ke kau i ka definitiveʻike.
Goodpasture ka maʻi pale: ohe.
I mea, o ka prognosis no e like me nā mea maʻi, ua noho lakou malaila. A me ka mea nui wale nō 'aneʻi - ka manawa e diagnose i ka maʻi, a hoʻomaka hana koke.
Eia naʻe, i ho'ākāka 'ai' no ka mea maʻi e 'ike'. Akā, ka mea kaulana i loko o ka hapanui hoopii, kūpono Inc maʻi pale hope subsides loko 6-9 mahina. Inā 'oe e hooki i ka hooulu ana o kaʻaʻa puʻuwai a me ka pulmonary mai, i ka hoʻomanawanui ke ola. Nō kāu, kauka i hoakaka ia i ka helu o ka loaa ana corticosteroids. Plasmapheresis ua hana, ina he pono - ke koko transfusions , a hiki hakuʻala transplantation. I mea e hooki aku i ka ulu ana o ka anaemia a me ka hao deficiency māʻona i hoakaka ia kūpono lapaʻauʻia. Akā, i kekahi manawa, ma ka loa loa hihia, he koko transfusion ua koi 'ia no ka hoʻopau o ka anemia.
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